The large vestibular aqueduct - case report and review of the literature

Patients with a large vestibular aqueduct (LVA) suffer from a loss of hearing in childhood at an early onset. An acute loss of hearing can be precipitated by minor head trauma. Until now there seems to be no sufficient therapy for stopping the progression of a loss of hearing. It has been shown that...

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Veröffentlicht in:Acta oto-laryngologica 2006-08, Vol.126 (8), p.788-795
Hauptverfasser: Steinbach, Silke, Brockmeier, Steffi-Johanna, Kiefer, >Jan
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container_title Acta oto-laryngologica
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creator Steinbach, Silke
Brockmeier, Steffi-Johanna
Kiefer, >Jan
description Patients with a large vestibular aqueduct (LVA) suffer from a loss of hearing in childhood at an early onset. An acute loss of hearing can be precipitated by minor head trauma. Until now there seems to be no sufficient therapy for stopping the progression of a loss of hearing. It has been shown that a cochlear implantation is a worthwhile procedure if the patient is almost deaf. We report the case of a patient with a bilateral LVA. A loss of hearing was confirmed at the age of 16 months. Exposure to loud noise triggered an acute progression of the hearing loss. At the age of 18 years, LVA was confirmed radiologically, revealing an enlarged endolymphatic duct and sac in MRI scans and an enlarged vestibular aqueduct in the CT scan. We successfully performed a cochlear implant (MED-EL, Combi 40+ flex). Proceeding from this case report, the paper reviews the literature on LVA.
doi_str_mv 10.1080/00016480500527276
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An acute loss of hearing can be precipitated by minor head trauma. Until now there seems to be no sufficient therapy for stopping the progression of a loss of hearing. It has been shown that a cochlear implantation is a worthwhile procedure if the patient is almost deaf. We report the case of a patient with a bilateral LVA. A loss of hearing was confirmed at the age of 16 months. Exposure to loud noise triggered an acute progression of the hearing loss. At the age of 18 years, LVA was confirmed radiologically, revealing an enlarged endolymphatic duct and sac in MRI scans and an enlarged vestibular aqueduct in the CT scan. We successfully performed a cochlear implant (MED-EL, Combi 40+ flex). 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Diseases due to physical agents</subject><subject>inner ear malformation</subject><subject>Large vestibular aqueduct (LVA)</subject><subject>Magnetic Resonance Imaging</subject><subject>Medical sciences</subject><subject>Non tumoral diseases</subject><subject>Otorhinolaryngology. Stomatology</subject><subject>Reference Values</subject><subject>sensorineural hearing loss</subject><subject>Speech Discrimination Tests</subject><subject>Tomography, X-Ray Computed</subject><subject>Traumas. 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Diseases due to physical agents</topic><topic>inner ear malformation</topic><topic>Large vestibular aqueduct (LVA)</topic><topic>Magnetic Resonance Imaging</topic><topic>Medical sciences</topic><topic>Non tumoral diseases</topic><topic>Otorhinolaryngology. Stomatology</topic><topic>Reference Values</topic><topic>sensorineural hearing loss</topic><topic>Speech Discrimination Tests</topic><topic>Tomography, X-Ray Computed</topic><topic>Traumas. 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source MEDLINE; Taylor & Francis Medical Library - CRKN; Taylor & Francis Journals Complete
subjects Adolescent
Adult
Audiometry, Pure-Tone
Biological and medical sciences
Child
Child, Preschool
cochlear implantation
Cochlear Implants
Combined Modality Therapy
Deafness - congenital
Deafness - diagnosis
Deafness - rehabilitation
Ear, auditive nerve, cochleovestibular tract, facial nerve: diseases, semeiology
Endolymphatic Duct - abnormalities
Endolymphatic Duct - pathology
Endolymphatic Sac - abnormalities
Endolymphatic Sac - pathology
Female
Follow-Up Studies
head trauma
Hearing Aids
Humans
Infant
Injuries of the nervous system and the skull. Diseases due to physical agents
inner ear malformation
Large vestibular aqueduct (LVA)
Magnetic Resonance Imaging
Medical sciences
Non tumoral diseases
Otorhinolaryngology. Stomatology
Reference Values
sensorineural hearing loss
Speech Discrimination Tests
Tomography, X-Ray Computed
Traumas. Diseases due to physical agents
Vestibular Aqueduct - abnormalities
Vestibular Aqueduct - pathology
title The large vestibular aqueduct - case report and review of the literature
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