'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient
A female patient just over 20 years of age developed first grade atrioventricular block, and later atrial fibrillation. When she was 41 years old she was diagnosed with Emery-Dreifuss muscular dystrophy (EDMD). A VVIR pacemaker was implanted in 2002, replaced in 2003 with an ICD. Nine months later,...
Gespeichert in:
| Veröffentlicht in: | Europace (London, England) England), 2007-12, Vol.9 (12), p.1158-1160 |
|---|---|
| Hauptverfasser: | , , |
| Format: | Artikel |
| Sprache: | eng |
| Schlagworte: | |
| Online-Zugang: | Volltext bestellen |
| Tags: |
Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
|
| container_end_page | 1160 |
|---|---|
| container_issue | 12 |
| container_start_page | 1158 |
| container_title | Europace (London, England) |
| container_volume | 9 |
| creator | Golzio, Pier Giorgio Chiribiri, Amedeo Gaita, Fiorenzo |
| description | A female patient just over 20 years of age developed first grade atrioventricular block, and later atrial fibrillation. When she was 41 years old she was diagnosed with Emery-Dreifuss muscular dystrophy (EDMD). A VVIR pacemaker was implanted in 2002, replaced in 2003 with an ICD. Nine months later, during febrile illness, the patient experienced three appropriate ICD discharges. No further ICD interventions occurred. The transient course of arrhythmic activity and the possible influence of triggering factors lessen the role of electrophysiologic study to identify risk of sudden death, and suggest that in patients with EDMD requiring pacemaker implantation, an ICD would be more properly indicated. |
| doi_str_mv | 10.1093/europace/eum236 |
| format | Article |
| fullrecord | <record><control><sourceid>proquest_TOX</sourceid><recordid>TN_cdi_proquest_miscellaneous_68551057</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><oup_id>10.1093/europace/eum236</oup_id><sourcerecordid>68551057</sourcerecordid><originalsourceid>FETCH-LOGICAL-c464t-6ba1333fd4d55c33836b09b2cca219b1afa374a7b4eb7a87930cd5f76094abab3</originalsourceid><addsrcrecordid>eNqFkE1LHTEUhkOxVKuu3ZXgQqEwmo_JZLIs9vYDhG50PZwkZzAyMxmTjPT--47cWwQ3rs67eM7Ly0PIGWdXnBl5jUuKMzhcwyhk84EccSVFJZgRB2tmxlSKC3NIPuf8yBjTwqhP5JBr0-hWtEcEL-8n_DujK-gvaV68x4l6hPJA4TkGj57aLQ3jPMBUwA5IHSQf4jOmgqny2AebwjBAiYmGiW5GTNvqe8LQLznTGUrAqZyQjz0MGU_395jc_9jc3fyqbv_8_H3z7bZydVOXqrHApZS9r71STspWNpYZK5wDwY3l0IPUNWhbo9XQaiOZ86rXDTM1WLDymFzseucUnxbMpRtDdrjOmzAuuWtapThTegXP34CPcUnTuq3jphXGMMVW6HoHuRRzTth3cwojpG3HWfeiv_uvv9vpXz--7GsXO6J_5fe-V-DrDojL_G7bP0xGk_k</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>198299050</pqid></control><display><type>article</type><title>'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient</title><source>Oxford Journals Open Access Collection</source><creator>Golzio, Pier Giorgio ; Chiribiri, Amedeo ; Gaita, Fiorenzo</creator><creatorcontrib>Golzio, Pier Giorgio ; Chiribiri, Amedeo ; Gaita, Fiorenzo</creatorcontrib><description>A female patient just over 20 years of age developed first grade atrioventricular block, and later atrial fibrillation. When she was 41 years old she was diagnosed with Emery-Dreifuss muscular dystrophy (EDMD). A VVIR pacemaker was implanted in 2002, replaced in 2003 with an ICD. Nine months later, during febrile illness, the patient experienced three appropriate ICD discharges. No further ICD interventions occurred. The transient course of arrhythmic activity and the possible influence of triggering factors lessen the role of electrophysiologic study to identify risk of sudden death, and suggest that in patients with EDMD requiring pacemaker implantation, an ICD would be more properly indicated.</description><identifier>ISSN: 1099-5129</identifier><identifier>EISSN: 1532-2092</identifier><identifier>DOI: 10.1093/europace/eum236</identifier><identifier>PMID: 17967828</identifier><language>eng</language><publisher>England: Oxford University Press</publisher><subject>Adult ; Atrial Fibrillation - complications ; Atrial Fibrillation - physiopathology ; Atrial Fibrillation - therapy ; Atrioventricular Block - physiopathology ; Death, Sudden - etiology ; Death, Sudden - prevention & control ; Defibrillators, Implantable ; Female ; Humans ; Muscular Dystrophy, Emery-Dreifuss - complications ; Muscular Dystrophy, Emery-Dreifuss - physiopathology ; Tachycardia, Ventricular - complications ; Tachycardia, Ventricular - physiopathology ; Tachycardia, Ventricular - therapy</subject><ispartof>Europace (London, England), 2007-12, Vol.9 (12), p.1158-1160</ispartof><rights>Published on behalf of the European Society of Cardiology. All rights reserved. © The Author 2007. For permissions please email: journals.permissions@oxfordjournals.org 2007</rights><rights>Published on behalf of the European Society of Cardiology. All rights reserved. © The Author 2007. For permissions please email: journals.permissions@oxfordjournals.org</rights><lds50>peer_reviewed</lds50><oa>free_for_read</oa><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c464t-6ba1333fd4d55c33836b09b2cca219b1afa374a7b4eb7a87930cd5f76094abab3</citedby></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,777,781,1599,27905,27906</link.rule.ids><linktorsrc>$$Uhttps://dx.doi.org/10.1093/europace/eum236$$EView_record_in_Oxford_University_Press$$FView_record_in_$$GOxford_University_Press</linktorsrc><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/17967828$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Golzio, Pier Giorgio</creatorcontrib><creatorcontrib>Chiribiri, Amedeo</creatorcontrib><creatorcontrib>Gaita, Fiorenzo</creatorcontrib><title>'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient</title><title>Europace (London, England)</title><addtitle>Europace</addtitle><description>A female patient just over 20 years of age developed first grade atrioventricular block, and later atrial fibrillation. When she was 41 years old she was diagnosed with Emery-Dreifuss muscular dystrophy (EDMD). A VVIR pacemaker was implanted in 2002, replaced in 2003 with an ICD. Nine months later, during febrile illness, the patient experienced three appropriate ICD discharges. No further ICD interventions occurred. The transient course of arrhythmic activity and the possible influence of triggering factors lessen the role of electrophysiologic study to identify risk of sudden death, and suggest that in patients with EDMD requiring pacemaker implantation, an ICD would be more properly indicated.</description><subject>Adult</subject><subject>Atrial Fibrillation - complications</subject><subject>Atrial Fibrillation - physiopathology</subject><subject>Atrial Fibrillation - therapy</subject><subject>Atrioventricular Block - physiopathology</subject><subject>Death, Sudden - etiology</subject><subject>Death, Sudden - prevention & control</subject><subject>Defibrillators, Implantable</subject><subject>Female</subject><subject>Humans</subject><subject>Muscular Dystrophy, Emery-Dreifuss - complications</subject><subject>Muscular Dystrophy, Emery-Dreifuss - physiopathology</subject><subject>Tachycardia, Ventricular - complications</subject><subject>Tachycardia, Ventricular - physiopathology</subject><subject>Tachycardia, Ventricular - therapy</subject><issn>1099-5129</issn><issn>1532-2092</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2007</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqFkE1LHTEUhkOxVKuu3ZXgQqEwmo_JZLIs9vYDhG50PZwkZzAyMxmTjPT--47cWwQ3rs67eM7Ly0PIGWdXnBl5jUuKMzhcwyhk84EccSVFJZgRB2tmxlSKC3NIPuf8yBjTwqhP5JBr0-hWtEcEL-8n_DujK-gvaV68x4l6hPJA4TkGj57aLQ3jPMBUwA5IHSQf4jOmgqny2AebwjBAiYmGiW5GTNvqe8LQLznTGUrAqZyQjz0MGU_395jc_9jc3fyqbv_8_H3z7bZydVOXqrHApZS9r71STspWNpYZK5wDwY3l0IPUNWhbo9XQaiOZ86rXDTM1WLDymFzseucUnxbMpRtDdrjOmzAuuWtapThTegXP34CPcUnTuq3jphXGMMVW6HoHuRRzTth3cwojpG3HWfeiv_uvv9vpXz--7GsXO6J_5fe-V-DrDojL_G7bP0xGk_k</recordid><startdate>20071201</startdate><enddate>20071201</enddate><creator>Golzio, Pier Giorgio</creator><creator>Chiribiri, Amedeo</creator><creator>Gaita, Fiorenzo</creator><general>Oxford University Press</general><general>Oxford Publishing Limited (England)</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7T5</scope><scope>H94</scope><scope>K9.</scope><scope>7X8</scope></search><sort><creationdate>20071201</creationdate><title>'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient</title><author>Golzio, Pier Giorgio ; Chiribiri, Amedeo ; Gaita, Fiorenzo</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c464t-6ba1333fd4d55c33836b09b2cca219b1afa374a7b4eb7a87930cd5f76094abab3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2007</creationdate><topic>Adult</topic><topic>Atrial Fibrillation - complications</topic><topic>Atrial Fibrillation - physiopathology</topic><topic>Atrial Fibrillation - therapy</topic><topic>Atrioventricular Block - physiopathology</topic><topic>Death, Sudden - etiology</topic><topic>Death, Sudden - prevention & control</topic><topic>Defibrillators, Implantable</topic><topic>Female</topic><topic>Humans</topic><topic>Muscular Dystrophy, Emery-Dreifuss - complications</topic><topic>Muscular Dystrophy, Emery-Dreifuss - physiopathology</topic><topic>Tachycardia, Ventricular - complications</topic><topic>Tachycardia, Ventricular - physiopathology</topic><topic>Tachycardia, Ventricular - therapy</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Golzio, Pier Giorgio</creatorcontrib><creatorcontrib>Chiribiri, Amedeo</creatorcontrib><creatorcontrib>Gaita, Fiorenzo</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>Immunology Abstracts</collection><collection>AIDS and Cancer Research Abstracts</collection><collection>ProQuest Health & Medical Complete (Alumni)</collection><collection>MEDLINE - Academic</collection><jtitle>Europace (London, England)</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext_linktorsrc</fulltext></delivery><addata><au>Golzio, Pier Giorgio</au><au>Chiribiri, Amedeo</au><au>Gaita, Fiorenzo</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient</atitle><jtitle>Europace (London, England)</jtitle><addtitle>Europace</addtitle><date>2007-12-01</date><risdate>2007</risdate><volume>9</volume><issue>12</issue><spage>1158</spage><epage>1160</epage><pages>1158-1160</pages><issn>1099-5129</issn><eissn>1532-2092</eissn><abstract>A female patient just over 20 years of age developed first grade atrioventricular block, and later atrial fibrillation. When she was 41 years old she was diagnosed with Emery-Dreifuss muscular dystrophy (EDMD). A VVIR pacemaker was implanted in 2002, replaced in 2003 with an ICD. Nine months later, during febrile illness, the patient experienced three appropriate ICD discharges. No further ICD interventions occurred. The transient course of arrhythmic activity and the possible influence of triggering factors lessen the role of electrophysiologic study to identify risk of sudden death, and suggest that in patients with EDMD requiring pacemaker implantation, an ICD would be more properly indicated.</abstract><cop>England</cop><pub>Oxford University Press</pub><pmid>17967828</pmid><doi>10.1093/europace/eum236</doi><tpages>3</tpages><oa>free_for_read</oa></addata></record> |
| fulltext | fulltext_linktorsrc |
| identifier | ISSN: 1099-5129 |
| ispartof | Europace (London, England), 2007-12, Vol.9 (12), p.1158-1160 |
| issn | 1099-5129 1532-2092 |
| language | eng |
| recordid | cdi_proquest_miscellaneous_68551057 |
| source | Oxford Journals Open Access Collection |
| subjects | Adult Atrial Fibrillation - complications Atrial Fibrillation - physiopathology Atrial Fibrillation - therapy Atrioventricular Block - physiopathology Death, Sudden - etiology Death, Sudden - prevention & control Defibrillators, Implantable Female Humans Muscular Dystrophy, Emery-Dreifuss - complications Muscular Dystrophy, Emery-Dreifuss - physiopathology Tachycardia, Ventricular - complications Tachycardia, Ventricular - physiopathology Tachycardia, Ventricular - therapy |
| title | 'Unexpected' sudden death avoided by implantable cardioverter-defibrillator in Emery-Dreifuss patient |
| url | https://sfx.bib-bvb.de/sfx_tum?ctx_ver=Z39.88-2004&ctx_enc=info:ofi/enc:UTF-8&ctx_tim=2025-01-20T12%3A13%3A34IST&url_ver=Z39.88-2004&url_ctx_fmt=infofi/fmt:kev:mtx:ctx&rfr_id=info:sid/primo.exlibrisgroup.com:primo3-Article-proquest_TOX&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.genre=article&rft.atitle='Unexpected'%20sudden%20death%20avoided%20by%20implantable%20cardioverter-defibrillator%20in%20Emery-Dreifuss%20patient&rft.jtitle=Europace%20(London,%20England)&rft.au=Golzio,%20Pier%20Giorgio&rft.date=2007-12-01&rft.volume=9&rft.issue=12&rft.spage=1158&rft.epage=1160&rft.pages=1158-1160&rft.issn=1099-5129&rft.eissn=1532-2092&rft_id=info:doi/10.1093/europace/eum236&rft_dat=%3Cproquest_TOX%3E68551057%3C/proquest_TOX%3E%3Curl%3E%3C/url%3E&disable_directlink=true&sfx.directlink=off&sfx.report_link=0&rft_id=info:oai/&rft_pqid=198299050&rft_id=info:pmid/17967828&rft_oup_id=10.1093/europace/eum236&rfr_iscdi=true |