A fatal case of peritonitis due to colonic localization of acute myeloid leukemia

Myeloid sarcoma (MS) is an extramedullary localization of immature granulocyte cells that can occur in association with acute myeloid leukemia (AML). Gastrointestinal involvement is relatively common in MS, but exclusive colonic localization is a rare occurrence. Here, we report on a 53-year-old mal...

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Veröffentlicht in:Annals of hematology 2025-01
Hauptverfasser: Buzzatti, Elisa, Botti, Caterina, Presicci, Roberta, Mauro, Cristina, Blasi, Francesca, Paterno, Giovangiacinto, Savino, Luca, Palmieri, Raffaele, Gurnari, Carmelo, Ottone, Tiziana, Mallegni, Flavia, Meddi, Elisa, Moretti, Federico, Tiravanti, Ilaria, Cardillo, Lucia, Mezzanotte, Valeria, Taka, Kristian, De Marchi, Lucrezia, Venditti, Adriano, Villa, Massimo, Del Principe, Maria Ilaria
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container_title Annals of hematology
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creator Buzzatti, Elisa
Botti, Caterina
Presicci, Roberta
Mauro, Cristina
Blasi, Francesca
Paterno, Giovangiacinto
Savino, Luca
Palmieri, Raffaele
Gurnari, Carmelo
Ottone, Tiziana
Mallegni, Flavia
Meddi, Elisa
Moretti, Federico
Tiravanti, Ilaria
Cardillo, Lucia
Mezzanotte, Valeria
Taka, Kristian
De Marchi, Lucrezia
Venditti, Adriano
Villa, Massimo
Del Principe, Maria Ilaria
description Myeloid sarcoma (MS) is an extramedullary localization of immature granulocyte cells that can occur in association with acute myeloid leukemia (AML). Gastrointestinal involvement is relatively common in MS, but exclusive colonic localization is a rare occurrence. Here, we report on a 53-year-old male patient affected by AML developing a severe abdominal pain caused by intestinal perforation requiring surgical intervention. The post-mortem examination revealed an infiltrate consistent with MS. Diagnosis of colonic MS can be difficult due to non-specific symptoms and complicated by the challenges associated with exploring this area. Clinical acumen is crucial to promptly establish adequate management due to the potentially life-threatening nature of this condition.
doi_str_mv 10.1007/s00277-024-06172-2
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title A fatal case of peritonitis due to colonic localization of acute myeloid leukemia
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