Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion
At age 13 years, after 3 years of intermittently being admitted to hospital with weight loss, exacerbations of dyspnoea, and an alpelisib-related thyroiditis, the patient had increasing fatigue and respiratory distress; pulmonary function testing indicated severe restrictive lung disease. A chest x-...
Gespeichert in:
| Veröffentlicht in: | The Lancet (British edition) 2024-11, Vol.404 (10466), p.1989-1990 |
|---|---|
| Hauptverfasser: | , , |
| Format: | Artikel |
| Sprache: | eng |
| Schlagworte: | |
| Online-Zugang: | Volltext |
| Tags: |
Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
|
| container_end_page | 1990 |
|---|---|
| container_issue | 10466 |
| container_start_page | 1989 |
| container_title | The Lancet (British edition) |
| container_volume | 404 |
| creator | Gupta, Mudit Krishnamurthy, Ganesh Smith, Christopher L |
| description | At age 13 years, after 3 years of intermittently being admitted to hospital with weight loss, exacerbations of dyspnoea, and an alpelisib-related thyroiditis, the patient had increasing fatigue and respiratory distress; pulmonary function testing indicated severe restrictive lung disease. A chest x-ray showed mild pulmonary oedema and an increase in the size of the right pleural effusion; repeat dynamic contrast-enhanced magnetic resonance lymphangiography showed extensive pulmonary lymphatic perfusion and a small thoracic duct (figure). Central conducting lymphatic anomaly is a heterogeneous form of a group of disorders, known as complex lymphatic anomalies, that encompasses any condition affecting the thoracic duct and cisterna chyli—the primary structures of the central lymphatic system. |
| doi_str_mv | 10.1016/S0140-6736(24)02355-9 |
| format | Article |
| fullrecord | <record><control><sourceid>proquest_cross</sourceid><recordid>TN_cdi_proquest_miscellaneous_3129221141</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><els_id>S0140673624023559</els_id><sourcerecordid>3128530772</sourcerecordid><originalsourceid>FETCH-LOGICAL-c271t-4cf5f0011fe2e9d62dfab6decbe65ea5884173e88d297212280b1ca5a463b3833</originalsourceid><addsrcrecordid>eNqFkTtvFDEURi0EIkvgJ4As0YRiiJ_zqBBa8ZIiUQQkOstj32EdeezBHgdtnx-ONxsilIbKzfnOvb4fQi8peUsJbc8vCRWkaTvenjHxhjAuZTM8QhsqOtFI0f14jDb3yAl6lvMVIUS0RD5FJ3yQktCOb9DNFsKatMcmBlvM6sJP7PfzstOrM1iHOGu_x7_dusNL8XMMOu3_Aew-L15np7HRJUPGCfKaXPVcA_alyqzLoDNUlcVml2KoqcVDOcyEaSrZxfAcPZm0z_Di7j1F3z9--Lb93Fx8_fRl-_6iMayjayPMJCdCKJ2AwWBbZic9thbMCK0ELfte1D9B31s2dIwy1pORGi21aPnIe85P0dnRu6T4q9RN1eyyAe91gFiy4pQNjFEqaEVfP0CvYkmhbnegeslJ17FKySNlUsw5waSW5OZ6IkWJOtSkbmtShw4UE-q2JjXU3Ks7exlnsPepv71U4N0RgHqOawdJZeMgGLAugVmVje4_I_4Abt6k6Q</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>3128530772</pqid></control><display><type>article</type><title>Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion</title><source>Elsevier ScienceDirect Journals Complete</source><creator>Gupta, Mudit ; Krishnamurthy, Ganesh ; Smith, Christopher L</creator><creatorcontrib>Gupta, Mudit ; Krishnamurthy, Ganesh ; Smith, Christopher L</creatorcontrib><description>At age 13 years, after 3 years of intermittently being admitted to hospital with weight loss, exacerbations of dyspnoea, and an alpelisib-related thyroiditis, the patient had increasing fatigue and respiratory distress; pulmonary function testing indicated severe restrictive lung disease. A chest x-ray showed mild pulmonary oedema and an increase in the size of the right pleural effusion; repeat dynamic contrast-enhanced magnetic resonance lymphangiography showed extensive pulmonary lymphatic perfusion and a small thoracic duct (figure). Central conducting lymphatic anomaly is a heterogeneous form of a group of disorders, known as complex lymphatic anomalies, that encompasses any condition affecting the thoracic duct and cisterna chyli—the primary structures of the central lymphatic system.</description><identifier>ISSN: 0140-6736</identifier><identifier>ISSN: 1474-547X</identifier><identifier>EISSN: 1474-547X</identifier><identifier>DOI: 10.1016/S0140-6736(24)02355-9</identifier><identifier>PMID: 39550173</identifier><language>eng</language><publisher>England: Elsevier Ltd</publisher><subject>Dyspnea ; Edema ; Embolization ; Fatigue tests ; Intervention ; Lung diseases ; Lymphangiography ; Lymphatic system ; Lymphedema ; Magnetic resonance ; Pleural effusion ; Pulmonary functions ; Respiration ; Respiratory function ; Thoracic duct ; Thyroiditis ; Weight loss</subject><ispartof>The Lancet (British edition), 2024-11, Vol.404 (10466), p.1989-1990</ispartof><rights>2024 Elsevier Ltd</rights><rights>2024. Elsevier Ltd</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktohtml>$$Uhttps://dx.doi.org/10.1016/S0140-6736(24)02355-9$$EHTML$$P50$$Gelsevier$$H</linktohtml><link.rule.ids>314,780,784,3550,27924,27925,45995</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/39550173$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Gupta, Mudit</creatorcontrib><creatorcontrib>Krishnamurthy, Ganesh</creatorcontrib><creatorcontrib>Smith, Christopher L</creatorcontrib><title>Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion</title><title>The Lancet (British edition)</title><addtitle>Lancet</addtitle><description>At age 13 years, after 3 years of intermittently being admitted to hospital with weight loss, exacerbations of dyspnoea, and an alpelisib-related thyroiditis, the patient had increasing fatigue and respiratory distress; pulmonary function testing indicated severe restrictive lung disease. A chest x-ray showed mild pulmonary oedema and an increase in the size of the right pleural effusion; repeat dynamic contrast-enhanced magnetic resonance lymphangiography showed extensive pulmonary lymphatic perfusion and a small thoracic duct (figure). Central conducting lymphatic anomaly is a heterogeneous form of a group of disorders, known as complex lymphatic anomalies, that encompasses any condition affecting the thoracic duct and cisterna chyli—the primary structures of the central lymphatic system.</description><subject>Dyspnea</subject><subject>Edema</subject><subject>Embolization</subject><subject>Fatigue tests</subject><subject>Intervention</subject><subject>Lung diseases</subject><subject>Lymphangiography</subject><subject>Lymphatic system</subject><subject>Lymphedema</subject><subject>Magnetic resonance</subject><subject>Pleural effusion</subject><subject>Pulmonary functions</subject><subject>Respiration</subject><subject>Respiratory function</subject><subject>Thoracic duct</subject><subject>Thyroiditis</subject><subject>Weight loss</subject><issn>0140-6736</issn><issn>1474-547X</issn><issn>1474-547X</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2024</creationdate><recordtype>article</recordtype><recordid>eNqFkTtvFDEURi0EIkvgJ4As0YRiiJ_zqBBa8ZIiUQQkOstj32EdeezBHgdtnx-ONxsilIbKzfnOvb4fQi8peUsJbc8vCRWkaTvenjHxhjAuZTM8QhsqOtFI0f14jDb3yAl6lvMVIUS0RD5FJ3yQktCOb9DNFsKatMcmBlvM6sJP7PfzstOrM1iHOGu_x7_dusNL8XMMOu3_Aew-L15np7HRJUPGCfKaXPVcA_alyqzLoDNUlcVml2KoqcVDOcyEaSrZxfAcPZm0z_Di7j1F3z9--Lb93Fx8_fRl-_6iMayjayPMJCdCKJ2AwWBbZic9thbMCK0ELfte1D9B31s2dIwy1pORGi21aPnIe85P0dnRu6T4q9RN1eyyAe91gFiy4pQNjFEqaEVfP0CvYkmhbnegeslJ17FKySNlUsw5waSW5OZ6IkWJOtSkbmtShw4UE-q2JjXU3Ks7exlnsPepv71U4N0RgHqOawdJZeMgGLAugVmVje4_I_4Abt6k6Q</recordid><startdate>20241116</startdate><enddate>20241116</enddate><creator>Gupta, Mudit</creator><creator>Krishnamurthy, Ganesh</creator><creator>Smith, Christopher L</creator><general>Elsevier Ltd</general><general>Elsevier Limited</general><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7QL</scope><scope>7QP</scope><scope>7TK</scope><scope>7U7</scope><scope>7U9</scope><scope>ASE</scope><scope>C1K</scope><scope>FPQ</scope><scope>H94</scope><scope>K6X</scope><scope>K9.</scope><scope>KB~</scope><scope>M7N</scope><scope>NAPCQ</scope><scope>7X8</scope></search><sort><creationdate>20241116</creationdate><title>Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion</title><author>Gupta, Mudit ; Krishnamurthy, Ganesh ; Smith, Christopher L</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c271t-4cf5f0011fe2e9d62dfab6decbe65ea5884173e88d297212280b1ca5a463b3833</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2024</creationdate><topic>Dyspnea</topic><topic>Edema</topic><topic>Embolization</topic><topic>Fatigue tests</topic><topic>Intervention</topic><topic>Lung diseases</topic><topic>Lymphangiography</topic><topic>Lymphatic system</topic><topic>Lymphedema</topic><topic>Magnetic resonance</topic><topic>Pleural effusion</topic><topic>Pulmonary functions</topic><topic>Respiration</topic><topic>Respiratory function</topic><topic>Thoracic duct</topic><topic>Thyroiditis</topic><topic>Weight loss</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Gupta, Mudit</creatorcontrib><creatorcontrib>Krishnamurthy, Ganesh</creatorcontrib><creatorcontrib>Smith, Christopher L</creatorcontrib><collection>PubMed</collection><collection>CrossRef</collection><collection>Bacteriology Abstracts (Microbiology B)</collection><collection>Calcium & Calcified Tissue Abstracts</collection><collection>Neurosciences Abstracts</collection><collection>Toxicology Abstracts</collection><collection>Virology and AIDS Abstracts</collection><collection>British Nursing Index</collection><collection>Environmental Sciences and Pollution Management</collection><collection>British Nursing Index (BNI) (1985 to Present)</collection><collection>AIDS and Cancer Research Abstracts</collection><collection>British Nursing Index</collection><collection>ProQuest Health & Medical Complete (Alumni)</collection><collection>ProQuest Newsstand Professional</collection><collection>Algology Mycology and Protozoology Abstracts (Microbiology C)</collection><collection>Nursing & Allied Health Premium</collection><collection>MEDLINE - Academic</collection><jtitle>The Lancet (British edition)</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Gupta, Mudit</au><au>Krishnamurthy, Ganesh</au><au>Smith, Christopher L</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion</atitle><jtitle>The Lancet (British edition)</jtitle><addtitle>Lancet</addtitle><date>2024-11-16</date><risdate>2024</risdate><volume>404</volume><issue>10466</issue><spage>1989</spage><epage>1990</epage><pages>1989-1990</pages><issn>0140-6736</issn><issn>1474-547X</issn><eissn>1474-547X</eissn><abstract>At age 13 years, after 3 years of intermittently being admitted to hospital with weight loss, exacerbations of dyspnoea, and an alpelisib-related thyroiditis, the patient had increasing fatigue and respiratory distress; pulmonary function testing indicated severe restrictive lung disease. A chest x-ray showed mild pulmonary oedema and an increase in the size of the right pleural effusion; repeat dynamic contrast-enhanced magnetic resonance lymphangiography showed extensive pulmonary lymphatic perfusion and a small thoracic duct (figure). Central conducting lymphatic anomaly is a heterogeneous form of a group of disorders, known as complex lymphatic anomalies, that encompasses any condition affecting the thoracic duct and cisterna chyli—the primary structures of the central lymphatic system.</abstract><cop>England</cop><pub>Elsevier Ltd</pub><pmid>39550173</pmid><doi>10.1016/S0140-6736(24)02355-9</doi><tpages>2</tpages></addata></record> |
| fulltext | fulltext |
| identifier | ISSN: 0140-6736 |
| ispartof | The Lancet (British edition), 2024-11, Vol.404 (10466), p.1989-1990 |
| issn | 0140-6736 1474-547X 1474-547X |
| language | eng |
| recordid | cdi_proquest_miscellaneous_3129221141 |
| source | Elsevier ScienceDirect Journals Complete |
| subjects | Dyspnea Edema Embolization Fatigue tests Intervention Lung diseases Lymphangiography Lymphatic system Lymphedema Magnetic resonance Pleural effusion Pulmonary functions Respiration Respiratory function Thoracic duct Thyroiditis Weight loss |
| title | Central conducting lymphatic anomaly with pulmonary lymphatic dysplasia causes restrictive lung disease and chronic pleural effusion |
| url | https://sfx.bib-bvb.de/sfx_tum?ctx_ver=Z39.88-2004&ctx_enc=info:ofi/enc:UTF-8&ctx_tim=2024-12-28T09%3A04%3A55IST&url_ver=Z39.88-2004&url_ctx_fmt=infofi/fmt:kev:mtx:ctx&rfr_id=info:sid/primo.exlibrisgroup.com:primo3-Article-proquest_cross&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.genre=article&rft.atitle=Central%20conducting%20lymphatic%20anomaly%20with%20pulmonary%20lymphatic%20dysplasia%20causes%20restrictive%20lung%20disease%20and%20chronic%20pleural%20effusion&rft.jtitle=The%20Lancet%20(British%20edition)&rft.au=Gupta,%20Mudit&rft.date=2024-11-16&rft.volume=404&rft.issue=10466&rft.spage=1989&rft.epage=1990&rft.pages=1989-1990&rft.issn=0140-6736&rft.eissn=1474-547X&rft_id=info:doi/10.1016/S0140-6736(24)02355-9&rft_dat=%3Cproquest_cross%3E3128530772%3C/proquest_cross%3E%3Curl%3E%3C/url%3E&disable_directlink=true&sfx.directlink=off&sfx.report_link=0&rft_id=info:oai/&rft_pqid=3128530772&rft_id=info:pmid/39550173&rft_els_id=S0140673624023559&rfr_iscdi=true |