Performance of upper limb entry item to predict forced vital capacity in dysferlin-deficient limb girdle muscular dystrophy

•Respiratory impairment is present in up to one-third-of patients with dysferlinopathy.•Spirometry is the gold standard for diagnosis and monitoring of respiratory impairment but is not always easily accessible.•The performance of upper limb (PUL) module is a clinical scale developed for patients wi...

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