Human diprosopus: Case report of a rare congenital abnormality

Diprosopus is a congenital anomaly in which partial or complete duplication of craniofacial structures occurs. Because it is rare, the mortality rate is high, and information concerning this anomaly is scarce. This study describes a case of human diprosopus in a 9‐year‐old male individual, who has s...

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Veröffentlicht in:Special care in dentistry 2024-07, Vol.44 (4), p.1083-1089
Hauptverfasser: Pontes, Maria Teresa Vasconcelos de Melo, Maia, Raiane Machado, da Silva, Luís Cândido Pinto, Manzi, Flávio Ricardo, Lima, Izabella Lucas de Abreu
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container_issue 4
container_start_page 1083
container_title Special care in dentistry
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creator Pontes, Maria Teresa Vasconcelos de Melo
Maia, Raiane Machado
da Silva, Luís Cândido Pinto
Manzi, Flávio Ricardo
Lima, Izabella Lucas de Abreu
description Diprosopus is a congenital anomaly in which partial or complete duplication of craniofacial structures occurs. Because it is rare, the mortality rate is high, and information concerning this anomaly is scarce. This study describes a case of human diprosopus in a 9‐year‐old male individual, who has severe complications associated with the central nervous, cardiovascular, respiratory, and digestive systems. Since birth, he has been monitored in a specialized hospital environment, where he has undergone several surgeries and multidisciplinary treatments. Regarding the craniofacial aspects, he had agenesis of the corpus callosum, floor of the nasal cavity, and floor of the anterior cranial fossa, in addition to the presence of bone dysplasia, ocular hypertelorism and cleft palate with nasal and oral teratoma. Regarding dental characteristics, the patient has duplication of the maxilla, mandible, tongue, and some teeth. After complementary imaging exams, several supernumerary teeth were found, with some being impacted and in complex regions, with an indication for extraction due to the risks of impaction, irruptive deviation, root resorption, and associated cystic or tumoral lesions. Because of the numerous complications, knowledge, and preparation of the entire team is necessary for the correct management of the case.
doi_str_mv 10.1111/scd.12991
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source Wiley Online Library Journals
subjects abnormalities
Bone dysplasia
Bone imaging
Bone surgery
Case reports
Childrens health
Cleft lip/palate
congenital abnormalities
Congenital diseases
conjoined
Corpus callosum
Environmental monitoring
Maxilla
Mortality
multiples
neural tube defects
Nose
Root resorption
Supernumerary
Teeth
Teratoma
twins
title Human diprosopus: Case report of a rare congenital abnormality
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