Elexacaftor/tezacaftor/ivacaftor improves chronic rhinosinusitis detected by magnetic resonance imaging in children with cystic fibrosis on long-term therapy with lumacaftor/ivacaftor

•The CRS-MRI sum score decreased after therapy initiation with ELX/TEZ/IVA in school-aged children with CF.•After therapy initiation with ELX/TEZ/IVA in school-aged children with CF, the prevalence and in maxillary and sphenoid sinuses the dominance of mucopyoceles decreased.•The strength in reducti...

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Veröffentlicht in:Journal of cystic fibrosis 2024-03, Vol.23 (2), p.234-241
Hauptverfasser: Wucherpfennig, Lena, Becker, Johanna K.Z., Wuennemann, Felix, Eichinger, Monika, Seitz, Angelika, Baumann, Ingo, Stahl, Mirjam, Graeber, Simon Y., Zhao, Shengkai, Chung, Jaehi, Schenk, Jens-Peter, Alrajab, Abdulsattar, Kauczor, Hans-Ulrich, Mall, Marcus A., Sommerburg, Olaf, Wielpütz, Mark O.
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Sprache:eng
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