Ulectomy in a patient with nephrotic syndrome under investigation for Galloway‐Mowat syndrome: a case report

The aim of this study is to report a case in which a patient with nephrotic syndrome underwent surgery to remove fibrous gum tissue (ulectomy). An 8‐year‐old patient, diagnosed with early onset nephrotic syndrome due to a mutation in the NUP107 gene, had received a kidney transplant and was therefor...

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Veröffentlicht in:Special care in dentistry 2024-07, Vol.44 (4), p.1054-1058
Hauptverfasser: Alves, Gabriela Reis, Javaroni, Julia Biliato, Moura, Ana Paula Gomes e, Consolaro, Alberto, Segato, Raquel Assed Bezerra
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container_issue 4
container_start_page 1054
container_title Special care in dentistry
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creator Alves, Gabriela Reis
Javaroni, Julia Biliato
Moura, Ana Paula Gomes e
Consolaro, Alberto
Segato, Raquel Assed Bezerra
description The aim of this study is to report a case in which a patient with nephrotic syndrome underwent surgery to remove fibrous gum tissue (ulectomy). An 8‐year‐old patient, diagnosed with early onset nephrotic syndrome due to a mutation in the NUP107 gene, had received a kidney transplant and was therefore taking various medications, including immunosuppressants. On oral examination, the patient was found to have a fibrous gingiva that was preventing the eruption of the upper permanent central incisors. A ulectomy was performed and the gingival tissue was sent for histopathological analysis, which showed normal aspects. The upper right central incisor was seen in the oral cavity 15 days after surgery. A second procedure was carried out to facilitate the eruption of the upper left incisor, which was visualized in the oral cavity 30 days later. In addition, oral manifestations such as maxillary atresia, ogival palate and mouth breathing were observed. Therefore, the role of the dental surgeon in the lives of transplanted children is considered important, as they often take various medications that can affect their oral health. Thus, early diagnosis and effective treatment will be essential to prevent future malocclusions and thus improve the quality of life of these patients.
doi_str_mv 10.1111/scd.12971
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source Wiley Online Library Journals Frontfile Complete
subjects Case reports
Childrens health
Gum disease
Histopathology
Immunosuppressive agents
immunosuppressive medications
Incisors
Kidney diseases
Kidney transplantation
Kidney transplants
Medical diagnosis
Mutation
Nephrotic syndrome
NUP107
Oral cavity
oral manifestations
Palate
Patients
Quality of life
Surgery
Surgical outcomes
Surgical techniques
ulectomy
title Ulectomy in a patient with nephrotic syndrome under investigation for Galloway‐Mowat syndrome: a case report
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