Trans-2,3-enoyl-CoA reductase-like-related catecholaminergic polymorphic ventricular tachycardia with regular ventricular tachycardia and response to flecainide

We describe a unique case of TECRL-CPVT presented with cardiac arrest. Post resuscitation, the patient developed regular ventricular tachycardia featuring a left purkinje system morphology. There was clear suppression of arrhythmia with the addition of flecainide and isolated ventricular ectopy causing secondary T-wave changes. A high index of suspicion was required to eventually make the diagnosis through whole exome sequencing.