Infantile hepatic cholestatis: An unusual case of Langerhans cells histiocytosis associated with advanced fibrosis

Infantile hepatic cholestatis: An unusual case of Langerhans cells histiocytosis associated with advanced fibrosis

Neonatal cholestasis is a clinical metabolic alteration requiring investigation of its eitiology. It is characterized by elevation of liver enzymes with cholestasis pattern and, in some cases, with acute liver failure. Its etiology is variable although the most frequent cause is atresia of extrahepa...

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Veröffentlicht in:Revista española de patología 2022-01, Vol.55 (1), p.63-67
Hauptverfasser: Martínez I Cózar, Vicent, Llavador Ros, Margarita, Évole Buselli, Montserrat, Andrés Moreno, María Del Mar, Polo Miquel, Begoña, Pérez Rojas, Judith
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container_title Revista española de patología
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creator Martínez I Cózar, Vicent
Llavador Ros, Margarita
Évole Buselli, Montserrat
Andrés Moreno, María Del Mar
Polo Miquel, Begoña
Pérez Rojas, Judith
description Neonatal cholestasis is a clinical metabolic alteration requiring investigation of its eitiology. It is characterized by elevation of liver enzymes with cholestasis pattern and, in some cases, with acute liver failure. Its etiology is variable although the most frequent cause is atresia of extrahepatic bile ducts. We present a case of a 23-month-old boy who presented with cholestasis and was finally diagnosed with systemic Langerhans cell histiocytosis.
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title Infantile hepatic cholestatis: An unusual case of Langerhans cells histiocytosis associated with advanced fibrosis
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