Effect of ibrutinib treatment on hemolytic anemia and acrocyanosis in cold agglutinin disease/cold agglutinin syndrome
Cold antibody-mediated autoimmune hemolytic anemia (cAIHA) is a rare disease, usually related to an underlying indolent clonal B-cell lymphoproliferative disorder. Jalink and colleagues describe an international retrospective analysis of Bruton tyrosine kinase (BTK) inhibition in patients with cAIHA...
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Veröffentlicht in: | Blood 2021-11, Vol.138 (20), p.2002-2005 |
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creator | Jalink, Marit Berentsen, Sigbjørn Castillo, Jorge J. Treon, Steven P. Cruijsen, Marjan Fattizzo, Bruno Cassin, Ramona Fotiou, Despina Kastritis, Efstathios De Haas, Masja Oosten, Liesbeth E.M. Frederiksen, Henrik Patriarca, Andrea D'Sa, Shirley Vos, Josephine M.I. |
description | Cold antibody-mediated autoimmune hemolytic anemia (cAIHA) is a rare disease, usually related to an underlying indolent clonal B-cell lymphoproliferative disorder. Jalink and colleagues describe an international retrospective analysis of Bruton tyrosine kinase (BTK) inhibition in patients with cAIHA. The data indicate a rapid and notable improvement in both the hemolytic anemia as well as acrocyanosis, suggesting that this may be an effective approach, regardless of underlying pathology or MYD88 mutational status. |
doi_str_mv | 10.1182/blood.2021012039 |
format | Article |
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subjects | Adenine - analogs & derivatives Adenine - therapeutic use Agammaglobulinaemia Tyrosine Kinase - antagonists & inhibitors Aged Aged, 80 and over Anemia, Hemolytic, Autoimmune - complications Anemia, Hemolytic, Autoimmune - drug therapy Cyanosis - complications Cyanosis - drug therapy Female Humans Male Middle Aged Piperidines - therapeutic use Protein Kinase Inhibitors - therapeutic use Retrospective Studies |
title | Effect of ibrutinib treatment on hemolytic anemia and acrocyanosis in cold agglutinin disease/cold agglutinin syndrome |
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