Effect of ibrutinib treatment on hemolytic anemia and acrocyanosis in cold agglutinin disease/cold agglutinin syndrome

Cold antibody-mediated autoimmune hemolytic anemia (cAIHA) is a rare disease, usually related to an underlying indolent clonal B-cell lymphoproliferative disorder. Jalink and colleagues describe an international retrospective analysis of Bruton tyrosine kinase (BTK) inhibition in patients with cAIHA...

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Veröffentlicht in:Blood 2021-11, Vol.138 (20), p.2002-2005
Hauptverfasser: Jalink, Marit, Berentsen, Sigbjørn, Castillo, Jorge J., Treon, Steven P., Cruijsen, Marjan, Fattizzo, Bruno, Cassin, Ramona, Fotiou, Despina, Kastritis, Efstathios, De Haas, Masja, Oosten, Liesbeth E.M., Frederiksen, Henrik, Patriarca, Andrea, D'Sa, Shirley, Vos, Josephine M.I.
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container_end_page 2005
container_issue 20
container_start_page 2002
container_title Blood
container_volume 138
creator Jalink, Marit
Berentsen, Sigbjørn
Castillo, Jorge J.
Treon, Steven P.
Cruijsen, Marjan
Fattizzo, Bruno
Cassin, Ramona
Fotiou, Despina
Kastritis, Efstathios
De Haas, Masja
Oosten, Liesbeth E.M.
Frederiksen, Henrik
Patriarca, Andrea
D'Sa, Shirley
Vos, Josephine M.I.
description Cold antibody-mediated autoimmune hemolytic anemia (cAIHA) is a rare disease, usually related to an underlying indolent clonal B-cell lymphoproliferative disorder. Jalink and colleagues describe an international retrospective analysis of Bruton tyrosine kinase (BTK) inhibition in patients with cAIHA. The data indicate a rapid and notable improvement in both the hemolytic anemia as well as acrocyanosis, suggesting that this may be an effective approach, regardless of underlying pathology or MYD88 mutational status.
doi_str_mv 10.1182/blood.2021012039
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subjects Adenine - analogs & derivatives
Adenine - therapeutic use
Agammaglobulinaemia Tyrosine Kinase - antagonists & inhibitors
Aged
Aged, 80 and over
Anemia, Hemolytic, Autoimmune - complications
Anemia, Hemolytic, Autoimmune - drug therapy
Cyanosis - complications
Cyanosis - drug therapy
Female
Humans
Male
Middle Aged
Piperidines - therapeutic use
Protein Kinase Inhibitors - therapeutic use
Retrospective Studies
title Effect of ibrutinib treatment on hemolytic anemia and acrocyanosis in cold agglutinin disease/cold agglutinin syndrome
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