Long‐term outcome after liver transplantation in children with type 1 glycogen storage disease

Patients with GSD type 1 (von Gierke disease) are initially managed medically to maintain normoglycemia. However, if they do not achieve good metabolic control, LT is then considered. We describe the long‐term outcome of 6 children with GSD type 1 who underwent LT. Retrospective chart review of the...

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Veröffentlicht in:	Pediatric transplantation 2021-03, Vol.25 (2), p.e13872-n/a
Hauptverfasser:	Yuen, Wing Yan, Quak, Seng Hock, Aw, Marion M., Karthik, Sivaramakrishnan Venkatesh
Format:	Artikel
Sprache:	eng
Schlagworte:	Adolescent Allopurinol Child Child, Preschool Children Enzymes Female Follow-Up Studies Glycogen glycogen storage disease Glycogen Storage Disease Type I - surgery Humans Hypercholesterolemia Hyperlactatemia Hypertriglyceridemia Hyperuricemia Hypoglycemia Infant Liver Transplantation Liver transplants Male metabolic control Metabolism paediatrics Retrospective Studies Storage diseases Transplants & implants Treatment Outcome von Gierke disease
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