Specific muscle strength is reduced in facioscapulohumeral dystrophy: An MRI based musculoskeletal analysis

•Specific muscle strength of the quadriceps muscle is reduced in patients with FSHD.•MRI and muscle modeling can be used to evaluate specific muscle strength in FSHD.•FSHD patients have lower contractile muscle volume and PCSA than healthy controls.•Clinical trials for FSHD should aim for restoratio...

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Veröffentlicht in:	Neuromuscular disorders : NMD 2018-03, Vol.28 (3), p.238-245
Hauptverfasser:	Marra, Marco A., Heskamp, Linda, Mul, Karlien, Lassche, Saskia, van Engelen, Baziel G.M., Heerschap, Arend, Verdonschot, Nico
Format:	Artikel
Sprache:	eng
Schlagworte:	Facioscapulohumeral muscular dystrophy Intrinsic weakness Musculoskeletal modeling Quantitative MRI Specific strength
Online-Zugang:	Volltext
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