Efficacy of Different Medical Therapies for the Treatment of Acute Laryngeal Attacks of Hereditary Angioedema due to C1-esterase Inhibitor Deficiency

Abstract Background Hereditary angioedema (HAE) is a rare disease characterized by C1-esterase inhibitor (C1-INH) deficiency, resulting in periodic attacks of acute edema, which can be life-threatening if they occur in the upper airway. No head-to-head comparisons of different treatment options for...

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Veröffentlicht in:The Journal of emergency medicine 2016-04, Vol.50 (4), p.567-580.e1
Hauptverfasser: Bork, Konrad, MD, Bernstein, Jonathan A., MD, Machnig, Thomas, MD, Craig, Timothy J., MD
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Sprache:eng
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