$Successful treatment with 4-phenylbutyrate in a patient with benign recurrent intrahepatic cholestasis type 2 refractory to biliary drainage and bilirubin absorption$

Successful treatment with 4-phenylbutyrate in a patient with benign recurrent intrahepatic cholestasis type 2 refractory to biliary drainage and bilirubin absorption

Aim Benign recurrent intrahepatic cholestasis type 2 (BRIC2) is caused by mutations in ABCB11, a gene encoding the bile salt export pump (BSEP) that mediates biliary bile salt secretion, and presents with repeated intermittent cholestasis with refractory itching. Currently, no effective medical ther...

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Veröffentlicht in:	Hepatology research 2016-02, Vol.46 (2), p.192-200
Hauptverfasser:	Hayashi, Hisamitsu, Naoi, Sotaro, Hirose, Yu, Matsuzaka, Yusuke, Tanikawa, Ken, Igarashi, Koji, Nagasaka, Hironori, Kage, Masayoshi, Inui, Ayano, Kusuhara, Hiroyuki
Format:	Artikel
Sprache:	eng
Schlagworte:	4-phenylbutyrate benign recurrent intrahepatic cholestasis bile salt export pump intrahepatic cholestasis
Online-Zugang:	Volltext
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