Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome

Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome

The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in β-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Veröffentlicht in:Annals of hematology 2004-09, Vol.83 (9), p.596
Hauptverfasser: Farmakis, Dimitrios, Vesleme, Vassiliki, Papadogianni, Argiroula, Tsaftaridis, Panagiotis, Kapralos, Pantelis, Aessopos, Athanasios
Format: Artikel
Sprache:eng
Schlagworte:
Aneurysms
Online-Zugang:Volltext
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
container_end_page
container_issue 9
container_start_page 596
container_title Annals of hematology
container_volume 83
creator Farmakis, Dimitrios
Vesleme, Vassiliki
Papadogianni, Argiroula
Tsaftaridis, Panagiotis
Kapralos, Pantelis
Aessopos, Athanasios
description The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in β-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of β-thalassemia patients, hence affecting the overall prognosis of the main disease.[PUBLICATION ABSTRACT]
doi_str_mv 10.1007/s00277-004-0859-6
format Article
fullrecord <record><control><sourceid>proquest_cross</sourceid><recordid>TN_cdi_proquest_journals_613981707</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><sourcerecordid>2085860241</sourcerecordid><originalsourceid>FETCH-LOGICAL-c1177-cba2431ff15d96bd34476bce68a93d393149ab5fa7086d7b47313fda5bb8ec613</originalsourceid><addsrcrecordid>eNotkE9PAyEQxYnRxFr9AN6IdxQWdllOpmn8lzTxomcyu7CW2oUKbGq_vTR1LjPJe3mT90PoltF7Rql8SJRWUhJKBaFtrUhzhmZM8IrQuhXnaEYVV6Quc4muUtpQyqpWVDO0X3g7xUMaIbseG7eFXK7gcRgwpN564_wXhhAzYOcx4F2Rrc947_IaP5K8hi2kZEcHGLw5GpKdTPgFn9dhBGyLXKKnkWzdt8Xp4E0Mo71GFwNsk73533P0-fz0sXwlq_eXt-ViRXrGSp--g0pwNgysNqrpDBdCNl1vmxYUN1xxJhR09QCSto2RnZCc8cFA3XWt7RvG5-julLuL4WeyKetNmKIvL3VRVcsklcXETqY-hpSiHfQuuhHiQTOqj3j1Ca8uePURr274H9tXb7A</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>613981707</pqid></control><display><type>article</type><title>Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome</title><source>SpringerLink Journals</source><creator>Farmakis, Dimitrios ; Vesleme, Vassiliki ; Papadogianni, Argiroula ; Tsaftaridis, Panagiotis ; Kapralos, Pantelis ; Aessopos, Athanasios</creator><creatorcontrib>Farmakis, Dimitrios ; Vesleme, Vassiliki ; Papadogianni, Argiroula ; Tsaftaridis, Panagiotis ; Kapralos, Pantelis ; Aessopos, Athanasios</creatorcontrib><description>The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in β-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of β-thalassemia patients, hence affecting the overall prognosis of the main disease.[PUBLICATION ABSTRACT]</description><identifier>ISSN: 0939-5555</identifier><identifier>EISSN: 1432-0584</identifier><identifier>DOI: 10.1007/s00277-004-0859-6</identifier><language>eng</language><publisher>Berlin: Springer Nature B.V</publisher><subject>Aneurysms</subject><ispartof>Annals of hematology, 2004-09, Vol.83 (9), p.596</ispartof><rights>Springer-Verlag 2004</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c1177-cba2431ff15d96bd34476bce68a93d393149ab5fa7086d7b47313fda5bb8ec613</citedby></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,776,780,27901,27902</link.rule.ids></links><search><creatorcontrib>Farmakis, Dimitrios</creatorcontrib><creatorcontrib>Vesleme, Vassiliki</creatorcontrib><creatorcontrib>Papadogianni, Argiroula</creatorcontrib><creatorcontrib>Tsaftaridis, Panagiotis</creatorcontrib><creatorcontrib>Kapralos, Pantelis</creatorcontrib><creatorcontrib>Aessopos, Athanasios</creatorcontrib><title>Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome</title><title>Annals of hematology</title><description>The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in β-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of β-thalassemia patients, hence affecting the overall prognosis of the main disease.[PUBLICATION ABSTRACT]</description><subject>Aneurysms</subject><issn>0939-5555</issn><issn>1432-0584</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2004</creationdate><recordtype>article</recordtype><sourceid>BENPR</sourceid><recordid>eNotkE9PAyEQxYnRxFr9AN6IdxQWdllOpmn8lzTxomcyu7CW2oUKbGq_vTR1LjPJe3mT90PoltF7Rql8SJRWUhJKBaFtrUhzhmZM8IrQuhXnaEYVV6Quc4muUtpQyqpWVDO0X3g7xUMaIbseG7eFXK7gcRgwpN564_wXhhAzYOcx4F2Rrc947_IaP5K8hi2kZEcHGLw5GpKdTPgFn9dhBGyLXKKnkWzdt8Xp4E0Mo71GFwNsk73533P0-fz0sXwlq_eXt-ViRXrGSp--g0pwNgysNqrpDBdCNl1vmxYUN1xxJhR09QCSto2RnZCc8cFA3XWt7RvG5-julLuL4WeyKetNmKIvL3VRVcsklcXETqY-hpSiHfQuuhHiQTOqj3j1Ca8uePURr274H9tXb7A</recordid><startdate>200409</startdate><enddate>200409</enddate><creator>Farmakis, Dimitrios</creator><creator>Vesleme, Vassiliki</creator><creator>Papadogianni, Argiroula</creator><creator>Tsaftaridis, Panagiotis</creator><creator>Kapralos, Pantelis</creator><creator>Aessopos, Athanasios</creator><general>Springer Nature B.V</general><scope>AAYXX</scope><scope>CITATION</scope><scope>3V.</scope><scope>7RV</scope><scope>7X7</scope><scope>7XB</scope><scope>88E</scope><scope>8AO</scope><scope>8FI</scope><scope>8FJ</scope><scope>8FK</scope><scope>ABUWG</scope><scope>AFKRA</scope><scope>BENPR</scope><scope>CCPQU</scope><scope>FYUFA</scope><scope>GHDGH</scope><scope>K9.</scope><scope>KB0</scope><scope>M0S</scope><scope>M1P</scope><scope>NAPCQ</scope><scope>PQEST</scope><scope>PQQKQ</scope><scope>PQUKI</scope><scope>PRINS</scope></search><sort><creationdate>200409</creationdate><title>Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome</title><author>Farmakis, Dimitrios ; Vesleme, Vassiliki ; Papadogianni, Argiroula ; Tsaftaridis, Panagiotis ; Kapralos, Pantelis ; Aessopos, Athanasios</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c1177-cba2431ff15d96bd34476bce68a93d393149ab5fa7086d7b47313fda5bb8ec613</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2004</creationdate><topic>Aneurysms</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Farmakis, Dimitrios</creatorcontrib><creatorcontrib>Vesleme, Vassiliki</creatorcontrib><creatorcontrib>Papadogianni, Argiroula</creatorcontrib><creatorcontrib>Tsaftaridis, Panagiotis</creatorcontrib><creatorcontrib>Kapralos, Pantelis</creatorcontrib><creatorcontrib>Aessopos, Athanasios</creatorcontrib><collection>CrossRef</collection><collection>ProQuest Central (Corporate)</collection><collection>Nursing &amp; Allied Health Database</collection><collection>Health &amp; Medical Collection</collection><collection>ProQuest Central (purchase pre-March 2016)</collection><collection>Medical Database (Alumni Edition)</collection><collection>ProQuest Pharma Collection</collection><collection>Hospital Premium Collection</collection><collection>Hospital Premium Collection (Alumni Edition)</collection><collection>ProQuest Central (Alumni) (purchase pre-March 2016)</collection><collection>ProQuest Central (Alumni Edition)</collection><collection>ProQuest Central UK/Ireland</collection><collection>ProQuest Central</collection><collection>ProQuest One Community College</collection><collection>Health Research Premium Collection</collection><collection>Health Research Premium Collection (Alumni)</collection><collection>ProQuest Health &amp; Medical Complete (Alumni)</collection><collection>Nursing &amp; Allied Health Database (Alumni Edition)</collection><collection>Health &amp; Medical Collection (Alumni Edition)</collection><collection>Medical Database</collection><collection>Nursing &amp; Allied Health Premium</collection><collection>ProQuest One Academic Eastern Edition (DO NOT USE)</collection><collection>ProQuest One Academic</collection><collection>ProQuest One Academic UKI Edition</collection><collection>ProQuest Central China</collection><jtitle>Annals of hematology</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Farmakis, Dimitrios</au><au>Vesleme, Vassiliki</au><au>Papadogianni, Argiroula</au><au>Tsaftaridis, Panagiotis</au><au>Kapralos, Pantelis</au><au>Aessopos, Athanasios</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome</atitle><jtitle>Annals of hematology</jtitle><date>2004-09</date><risdate>2004</risdate><volume>83</volume><issue>9</issue><spage>596</spage><pages>596-</pages><issn>0939-5555</issn><eissn>1432-0584</eissn><abstract>The development of a diffuse elastic tissue defect resembling pseudoxanthoma elasticum (PXE) is a recently established and frequently encountered clinical entity in β-thalassemia. The clinical spectrum of this disorder is not yet completely understood as it is continuously being enriched with novel complications that are often serious. We present here a thalassemia intermedia patient with typical PXE manifestations and a fusiform aneurysmatic dilatation of the ascending thoracic aorta, a previously unknown complication in these patients. An aortic aneurysm has itself a notable morbidity, while it may also impair the particularly susceptible cardiac function of β-thalassemia patients, hence affecting the overall prognosis of the main disease.[PUBLICATION ABSTRACT]</abstract><cop>Berlin</cop><pub>Springer Nature B.V</pub><doi>10.1007/s00277-004-0859-6</doi></addata></record>
fulltext fulltext
identifier ISSN: 0939-5555
ispartof Annals of hematology, 2004-09, Vol.83 (9), p.596
issn 0939-5555
1432-0584
language eng
recordid cdi_proquest_journals_613981707
source SpringerLink Journals
subjects Aneurysms
title Aneurysmatic dilatation of ascending aorta in a patient with ?-thalassemia and a pseudoxanthoma elasticum-like syndrome
url https://sfx.bib-bvb.de/sfx_tum?ctx_ver=Z39.88-2004&ctx_enc=info:ofi/enc:UTF-8&ctx_tim=2025-02-09T06%3A41%3A26IST&url_ver=Z39.88-2004&url_ctx_fmt=infofi/fmt:kev:mtx:ctx&rfr_id=info:sid/primo.exlibrisgroup.com:primo3-Article-proquest_cross&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.genre=article&rft.atitle=Aneurysmatic%20dilatation%20of%20ascending%20aorta%20in%20a%20patient%20with%20?-thalassemia%20and%20a%20pseudoxanthoma%20elasticum-like%20syndrome&rft.jtitle=Annals%20of%20hematology&rft.au=Farmakis,%20Dimitrios&rft.date=2004-09&rft.volume=83&rft.issue=9&rft.spage=596&rft.pages=596-&rft.issn=0939-5555&rft.eissn=1432-0584&rft_id=info:doi/10.1007/s00277-004-0859-6&rft_dat=%3Cproquest_cross%3E2085860241%3C/proquest_cross%3E%3Curl%3E%3C/url%3E&disable_directlink=true&sfx.directlink=off&sfx.report_link=0&rft_id=info:oai/&rft_pqid=613981707&rft_id=info:pmid/&rfr_iscdi=true