Cystic Fibrosis: an Update on Disease Pathophysiology, Management, and Novel Modalities of Therapy

Purpose of review To explain the underlying pathophysiology of cystic fibrosis and to describe current treatment modalities for disease manifestations, including an introduction to novel therapies known as CFTR modulator drugs, which are now available to over 50% of people with cystic fibrosis. Rece...

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