G473(P)Nutritional adequacy of Prader-Willi syndrome children on restricted diets: A 10 year review from a multidisciplinary clinic

Aims A vital component of the management of Prader-Willi Syndrome (PWS) is strict control of dietary intake whilst ensuring sufficient nutrition to prevent deficiencies. Surprisingly however there is very limited data in the literature surrounding this. Our observational study sought to describe mean caloric intake, proportion of energy contributed by macronutrients and identify common micronutrient deficiencies. Method PWS children attending our specialist multidisciplinary clinic complete weighed 3 day food diaries as part of their routine assessments. Analysis is completed using a specific computer package with results expressed as % of intake against UK reference nutrient intakes (RNI’s) adjusted for age and sex. Data was retrospectively reviewed from case notes. Abstract G473(P) Figure 1 Results 35 food diaries were returned from 11 PWS children (age range 1.1–12 years) 5 males and 6 females between August 2002 – March 2013. Mean caloric intake was 69.5% RNI (Range 38–103%). A mean lower caloric % of RNI was seen in the younger children (