Sex, Genotype, and Liver Volume Progression as Risk of Hospitalization Determinants in Autosomal Dominant Polycystic Liver Disease

BACKGROUND & AIMS: Autosomal dominant polycystic liver disease is a rare condition with a female preponderance, based mainly on pathogenic variants in 2 genes, PRKCSH and SEC63. Clinically, autosomal dominant polycystic liver disease is characterized by vast heterogeneity, ranging from asymptoma...

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Veröffentlicht in:GASTROENTEROLOGY 2024-05, Vol.166 (5), p.902-914
Hauptverfasser: Schoenauer, Ria, Sierks, Dana, Boerrigter, Melissa, Jawaid, Tabinda, Caroff, Lea, Audrezet, Marie-Pierre, Friedrich, Anja, Shaw, Melissa, Degenhardt, Jan, Forberger, Mirjam, de Fallois, Jonathan, Blaeker, Hendrik, Bergmann, Carsten, Goediker, Juliana, Schindler, Philipp, Schlevogt, Bernhard, Mueller, Roman-U, Berg, Thomas, Patterson, Ilse, Griffiths, William J, Sayer, John A, Popp, Bernt, Torres, Vicente E, Hogan, Marie C, Somlo, Stefan, Watnick, Terry J, Nevens, Frederik, Besse, Whitney, Gall, Emilie Cornec-Le, Harris, Peter C, Drenth, Joost P.H, Halbritter, Jan
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Sprache:eng
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