Intravenous immunoglobulins improve survival in monoclonal gammopathy-associated systemic capillary-leak syndrome

Abstract Background Monoclonal gammopathy-associated systemic capillary-leak syndrome, also known as Clarkson disease, is a rare condition characterized by recurrent life-threatening episodes of capillary hyper-permeability in the context of a monoclonal gammopathy. This study was conducted to bette...

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Veröffentlicht in:The American journal of medicine 2017-10, Vol.130 (10), p.1219.e19-1219.e27
Hauptverfasser: de Chambrun, Marc Pineton, MD, Gousseff, Marie, MD, Mauhin, Wladimir, MD, Lega, Jean-Christophe, MD, PhD, Lambert, Marc, MD, PhD, Rivière, Sophie, MD, Dossier, Antoine, MD, Ruivard, Marc, MD, PhD, Lhote, François, MD, Blaison, Gilles, MD, Alric, Laurent, MD, PhD, Agard, Christian, MD, PhD, Saadoun, David, MD, PhD, Graveleau, Julie, MD, Soubrier, Martin, MD, PhD, Lucchini-Lecomte, Marie-Josée, MD, Christides, Christine, MD, Bosseray, Annick, MD, Levesque, Hervé, MD, PhD, Viallard, Jean-François, MD, PhD, Tieulie, Nathalie, MD, Lovey, Pierre-Yves, MD, Le Moal, Sylvie, MD, Bibes, Béatrice, MD, Malizia, Giuseppe, MD, Abgueguen, Pierre, MD, Lifermann, François, MD, Ninet, Jacques, MD, PhD, Hatron, Pierre-Yves, MD, Amoura, Zahir, MD, MSc
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