Morbihan syndrome--an atypical report of a rare condition/Sindrome de Morbihan--relato atipico de uma doenca pouco conhecida

Morbihan syndrome is a rare condition and its pathogenesis is not fully known. This entityh is characterized by facial edema and facial erythema, with a slow, symmetrical appearance, affecting the upper portion of the face. This case report is about a patient with an atypical case of Morbihan syndrome, with asymmetric facial involvement. Clinical and histopathological aspects were highlighted aiming the diagnosis of this rare pathology, as well as possible differential diagnoses and treatment options. It has also been aimed to call attention to less typical forms of this disease. Keywords: Dermatology; Face; Edema; Rosacea; Erythema. A sindrome de Morbihan e uma doenca rara, de fisiopatologia pouco conhecida, tipicamente caracterizada por edema e eritema facial, de aparecimento lento, simetrico, afetando terco superior da face. Este relato de caso se trata de um paciente com caso atipico de Sindrome de Morbihan, com acometimento assimetrico de face. Foram ressaltados aspectos clinicos e histopatologicos para diagnostico dessa rara patologia, possiveis diagnosticos diferenciais e opcoes de tratamento. Tambem foi buscado difundir formas menos tipicas desta doenca. Descritores: Dermatologia; Face; Edema; Rosacea; Eritema.