Idiopathic pure red cell aplasia: A case series from India
Pure red cell aplasia (PRCA) is a rare hematologic disorder characterized by normocytic normochromic anemia with reticulocytopenia and depleted erythroid precursors. It is reported mainly from western countries. We report our experience in two patients of PRCA from India, the clinical characteristic...
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Veröffentlicht in: | Asian Journal of Medical Sciences 2023-05, Vol.14 (5), p.253-256 |
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container_title | Asian Journal of Medical Sciences |
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creator | Manoj U Mahajan Sunil Goel Harsh Patel Aseem Aasdhir Urvansh Mehta Kavita Gupta Shashi Sujanani Jagdish Vishnoi Nilesh Patira Kalu Ram Sharma |
description | Pure red cell aplasia (PRCA) is a rare hematologic disorder characterized by normocytic normochromic anemia with reticulocytopenia and depleted erythroid precursors. It is reported mainly from western countries. We report our experience in two patients of PRCA from India, the clinical characteristics, differential diagnosis, and their management. Our patients showed improvements following treatment with corticosteroids, blood transfusion, and/or rituximab. |
doi_str_mv | 10.71152/ajms.v14i5.3734 |
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title | Idiopathic pure red cell aplasia: A case series from India |
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