Visual System Impairment in a Mouse Model of Krabbe Disease: The Twitcher Mouse von Tonazzini, Ilaria, Cerri, Chiara, Del Grosso, Ambra, Antonini, Sara, Allegra, Manuela, Caleo, Matteo, Cecchini, Marco

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Dysregulated autophagy as a new aspect of the molecular pathogenesis of Krabbe disease von Del Grosso, Ambra, Angella, Lucia, Tonazzini, Ilaria, Moscardini, Aldo, Giordano, Nadia, Caleo, Matteo, Rocchiccioli, Silvia, Cecchini, Marco

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Cross-Linked Enzyme Aggregates as Versatile Tool for Enzyme Delivery: Application to Polymeric Nanoparticles von Galliani, Marianna, Santi, Melissa, Del Grosso, Ambra, Cecchettini, Antonella, Santorelli, Filippo Maria, Hofmann, Sandra L, Lu, Jui-Yun, Angella, Lucia, Cecchini, Marco, Signore, Giovanni

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Direct imaging of APP proteolysis in living cells von Parenti, Niccoló, Del Grosso, Ambra, Antoni, Claudia, Cecchini, Marco, Corradetti, Renato, Pavone, Francesco S, Calamai, Martino

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Brain-targeted enzyme-loaded nanoparticles: A breach through the blood-brain barrier for enzyme replacement therapy in Krabbe disease von Del Grosso, Ambra, Galliani, Marianna, Angella, Lucia, Santi, Melissa, Tonazzini, Ilaria, Parlanti, Gabriele, Signore, Giovanni, Cecchini, Marco

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Measuring Molecular Diffusion in Dynamic Subcellular Nanostructures by Fast Raster Image Correlation Spectroscopy and 3D Orbital Tracking von Begarani, Filippo, D’Autilia, Francesca, Ferri, Gianmarco, Pesce, Luca, Azzarello, Fabio, De Lorenzi, Valentina, Durso, William, Del Grosso, Ambra, Cecchini, Marco, Cardarelli, Francesco

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Reliable and Fast Genotyping Protocol for Galactosylceramidase (Galc) in the Twitcher (Twi) Mouse von Carpi, Sara, Del Grosso, Ambra, De Sarlo, Miriam, Colagiorgio, Laura, Scaccini, Luca, Tonazzini, Ilaria, Parlanti, Gabriele, Cecchini, Marco

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Untargeted Lipidomic Approach for Studying Different Nervous System Tissues of the Murine Model of Krabbe Disease von Alabed, Husam B R, Del Grosso, Ambra, Bellani, Valeria, Urbanelli, Lorena, Carpi, Sara, De Sarlo, Miriam, Bertocci, Lorenzo, Colagiorgio, Laura, Buratta, Sandra, Scaccini, Luca, Frongia Mancini, Dorotea, Tonazzini, Ilaria, Cecchini, Marco, Emiliani, Carla, Pellegrino, Roberto Maria

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Mechanotransduction Impairment in Primary Fibroblast Model of Krabbe Disease von Mezzena, Roberta, Del Grosso, Ambra, Pellegrino, Roberto Maria, Alabed, Husam B R, Emiliani, Carla, Tonazzini, Ilaria, Cecchini, Marco

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Chronic lithium administration in a mouse model for Krabbe disease von Del Grosso, Ambra, Parlanti, Gabriele, Angella, Lucia, Giordano, Nadia, Tonazzini, Ilaria, Ottalagana, Elisa, Carpi, Sara, Pellegrino, Roberto Maria, Alabed, Husam B. R., Emiliani, Carla, Caleo, Matteo, Cecchini, Marco

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Current treatment options and novel nanotechnology-driven enzyme replacement strategies for lysosomal storage disorders von Del Grosso, Ambra, Parlanti, Gabriele, Mezzena, Roberta, Cecchini, Marco

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Lithium improves cell viability in psychosine-treated MO3.13 human oligodendrocyte cell line via autophagy activation von Del Grosso, Ambra, Antonini, Sara, Angella, Lucia, Tonazzini, Ilaria, Signore, Giovanni, Cecchini, Marco

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Capturing Metabolism-Dependent Solvent Dynamics in the Lumen of a Trafficking Lysosome von Begarani, Filippo, D’Autilia, Francesca, Signore, Giovanni, Del Grosso, Ambra, Cecchini, Marco, Gratton, Enrico, Beltram, Fabio, Cardarelli, Francesco

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Quantitative Microproteomics Based Characterization of the Central and Peripheral Nervous System of a Mouse Model of Krabbe Disease[S] von Pellegrini, Davide, del Grosso, Ambra, Angella, Lucia, Giordano, Nadia, Dilillo, Marialaura, Tonazzini, Ilaria, Caleo, Matteo, Cecchini, Marco, McDonnell, Liam A.

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Chronic Rapamycin administration via drinking water mitigates the pathological phenotype in a Krabbe disease mouse model through autophagy activation von Del Grosso, Ambra, Carpi, Sara, De Sarlo, Miriam, Scaccini, Luca, Colagiorgio, Laura, Alabed, Husam B.R., Angella, Lucia, Pellegrino, Roberto Maria, Tonazzini, Ilaria, Emiliani, Carla, Cecchini, Marco

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Gene editing of DNAH11 restores normal cilia motility in primary ciliary dyskinesia von Lai, Michele, Pifferi, Massimo, Bush, Andrew, Piras, Martina, Michelucci, Angela, Di Cicco, Maria, del Grosso, Ambra, Quaranta, Paola, Cursi, Chiara, Tantillo, Elena, Franceschi, Sara, Mazzanti, Maria Chiara, Simi, Paolo, Saggese, Giuseppe, Boner, Attilio, Pistello, Mauro

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Reliable and Fast Genotyping Protocol for Galactosylceramidase Mouse von Carpi, Sara, Del Grosso, Ambra, De Sarlo, Miriam, Colagiorgio, Laura, Scaccini, Luca, Tonazzini, Ilaria, Parlanti, Gabriele, Cecchini, Marco

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Quantitative Microproteomics Based Characterization of the Central and Peripheral Nervous System of a Mouse Model of Krabbe Disease von Pellegrini, Davide, Del Grosso, Ambra, Angella, Lucia, Giordano, Nadia, Dilillo, Marialaura, Tonazzini, Ilaria, Caleo, Matteo, Cecchini, Marco, McDonnell, Liam A

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Quantitative Microproteomics Based Characterization of the Central and Peripheral Nervous System of a Mouse Model of Krabbe Disease von Pellegrini, Davide, Del Grosso, Ambra, Angella, Lucia, Giordano, Nadia, Dilillo, Marialaura, Tonazzini, Ilaria, Caleo, Matteo, Cecchini, Marco, McDonnell, Liam A

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Data from: Reliable and fast genotyping protocol for galactosylceramidase (GALC) in the Twitcher (Twi) mouse von Carpi, Sara, Del Grosso, Ambra, De Sarlo, Miriam, Colagiorgio, Laura, Scaccini, Luca, Tonazzini, Ilaria, Parlanti, Gabriele, Cecchini, Marco

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