Interactions in the Metabolism of Glutamate and the Branched-Chain Amino Acids and Ketoacids in the CNS von Yudkoff, Marc

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Beyond aerobic glycolysis: Transformed cells can engage in glutamine metabolism that exceeds the requirement for protein and nucleotide synthesis von DeBerardinis, Ralph J, Mancuso, Anthony, Daikhin, Evgueni, Nissim, Ilana, Yudkoff, Marc, Wehrli, Suzanne, Thompson, Craig B

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Myc Regulates a Transcriptional Program That Stimulates Mitochondrial Glutaminolysis and Leads to Glutamine Addiction von Wise, David R., DeBerardinis, Ralph J., Mancuso, Anthony, Sayed, Nabil, Zhang, Xiao-Yong, Pfeiffer, Harla K., Nissim, Ilana, Daikhin, Evgueni, Yudkoff, Marc, McMahon, Steven B., Thompson, Craig B.

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Inborn error of metabolism patients after liver transplantation: Outcomes of 35 patients over 27 years in one pediatric quaternary hospital von Pritchard, Amanda Barone, Izumi, Kosuke, Payan‐Walters, Irma, Yudkoff, Marc, Rand, Elizabeth B., Bhoj, Elizabeth

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Ketosis and brain handling of glutamate, glutamine, and GABA von Yudkoff, Marc, Daikhin, Yevgeny, Horyn, Oksana, Nissim, Ilana, Nissim, Itzhak

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ASL expression in ALDH1A1+ neurons in the substantia nigra metabolically contributes to neurodegenerative phenotype von Lerner, Shaul, Eilam, Raya, Adler, Lital, Baruteau, Julien, Kreiser, Topaz, Tsoory, Michael, Brandis, Alexander, Mehlman, Tevie, Ryten, Mina, Botia, Juan A., Ruiz, Sonia Garcia, Garcia, Alejandro Cisterna, Dionisi-Vici, Carlo, Ranucci, Giusy, Spada, Marco, Mazkereth, Ram, McCarter, Robert, Izem, Rima, Balmat, Thomas J., Richesson, Rachel, Gazit, Ehud, Nagamani, Sandesh C. S., Erez, Ayelet

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Compartmentation of Brain Glutamate Metabolism in Neurons and Glia von Daikhin, Yevgeny, Yudkoff, Marc

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The Molecular and Metabolic Influence of Long Term Agmatine Consumption von Nissim, Itzhak, Horyn, Oksana, Daikhin, Yevgeny, Chen, Pan, Li, Changhong, Wehrli, Suzanne L., Nissim, Ilana, Yudkoff, Marc

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Inflammation-induced preterm birth alters neuronal morphology in the mouse fetal brain von Burd, Irina, Bentz, Amy I., Chai, Jinghua, Gonzalez, Juan, Monnerie, Hubert, Le Roux, Peter D., Cohen, Akiva S., Yudkoff, Marc, Elovitz, Michal A.

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Brain metabolism of branched-chain amino acids von Yudkoff, Marc

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Early diagnosis of infantile-onset lysosomal acid lipase deficiency in the advent of available enzyme replacement therapy von Cohen, Jennifer L, Burfield, Jessica, Valdez-Gonzalez, Karen, Samuels, Angela, Stefanatos, Arianna K, Yudkoff, Marc, Pedro, Helio, Ficicioglu, Can

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Augmenting Ureagenesis in Patients with Partial Carbamyl Phosphate Synthetase 1 Deficiency with N-carbamyl- l -glutamate von Ah Mew, Nicholas, MD, McCarter, Robert, ScD, Daikhin, Yevgeny, PhD, Lichter-Konecki, Uta, MD, PhD, Nissim, Ilana, Yudkoff, Marc, MD, Tuchman, Mendel, MD

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Phenotypes of undiagnosed adults with actionable OTC and GLA variants von Gold, Jessica I., Madhavan, Sarina, Park, Joseph, Zouk, Hana, Perez, Emma, Strong, Alanna, Drivas, Theodore G., Karaa, Amel, Yudkoff, Marc, Rader, Daniel, Green, Robert C., Gold, Nina B.

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Primary coenzyme Q deficiency in Pdss2 mutant mice causes isolated renal disease von Peng, Min, Falk, Marni J, Haase, Volker H, King, Rhonda, Polyak, Erzsebet, Selak, Mary, Yudkoff, Marc, Hancock, Wayne W, Meade, Ray, Saiki, Ryoichi, Lunceford, Adam L, Clarke, Catherine F, Gasser, David L

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Ifosfamide-induced nephrotoxicity: mechanism and prevention von Nissim, Itzhak, Horyn, Oksana, Daikhin, Yevgeny, Nissim, Ilana, Luhovyy, Bohdan, Phillips, Peter C, Yudkoff, Marc

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N-carbamylglutamate enhancement of ureagenesis leads to discovery of a novel deleterious mutation in a newly defined enhancer of the NAGS gene and to effective therapy von Heibel, Sandra K., Ah Mew, Nicholas, Caldovic, Ljubica, Daikhin, Yevgeny, Yudkoff, Marc, Tuchman, Mendel

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A Signaling Role of Glutamine in Insulin Secretion von Li, Changhong, Buettger, Carol, Kwagh, Jae, Matter, Andrea, Daikhin, Yevgeny, Nissim, Ilana B, Collins, Heather W, Yudkoff, Marc, Stanley, Charles A, Matschinsky, Franz M

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Factors Determining the Selectivity of Protein Tyrosine Nitration von Souza, José M., Daikhin, Evgueni, Yudkoff, Marc, Raman, C.S., Ischiropoulos, Harry

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Very Long-Chain Acyl-CoA Dehydrogenase Deficiency in a Patient with Normal Newborn Screening by Tandem Mass Spectrometry von Ficicioglu, Can, MD, PhD, Coughlin, Curtis R., MS, Bennett, Michael J., PhD, Yudkoff, Marc, MD

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Regulation of Leucine-stimulated Insulin Secretion and Glutamine Metabolism in Isolated Rat Islets von Li, Changhong, Najafi, Habiba, Daikhin, Yevgeny, Nissim, Ilana B, Collins, Heather W, Yudkoff, Marc, Matschinsky, Franz M, Stanley, Charles A

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