Mitochondrial disease and cyclic vomiting syndrome von BOLES, R. G, WILLIAMS, J. C

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Photocycloaddition reactions of some 3-substituted cyclohexenones von Cantrell, Thomas S, Haller, Walfred S, Williams, Julian C

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Nutritional Goals in Glycogen Storage Disease von Williams, Julian C

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Progressive Neurologic Deterioration and Renal Failure Due to Storage of Glutamyl Ribose-5-Phosphate von Williams, Julian C, Butler, Ian J, Rosenberg, Harvey S, Verani, Regina, Scott, Charles I, Conley, Susan B

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Glycosaparaginase from human leukocytes. Inactivation and covalent modification with diazo-oxonorvaline von Kaartinen, V, Williams, J C, Tomich, J, Yates, J R, Hood, L E, Mononen, I

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Prevalence of medium-chain acyl-coenzyme A dehydrogenase deficiency in the sudden infant death syndrome von Arens, Raanan, Gozal, David, Jain, Karen, Muscati, Shamshad, Heuser, Eva T., Williams, Julian C., Keens, Thomas G., Davidso Ward, Sally L.

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Recurrent apparent life-threatening events during infancy: A manifestation of inborn errors of metabolism von Arens, Raanan, Gozal, David, Williams, Julian C., Davidson Ward, Sally L., Keens, Thomas G.

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Aspartylglycosaminuria in the Finnish Population: Identification of Two Point Mutations in the Heavy Chain of Glycoasparaginase von Mononen, Ilkka, Heisterkamp, Nora, Kaartinen, Vesa, Williams, Julian C., Yates, John R., Griffin, Patrick R., Hood, Leroy E., Groffen, John

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Echocardiographic abnormalities in the mucopolysaccharide storage diseases von Gross, Donald M., Williams, Julian C., Caprioli, Christine, Dominguez, Barbara, Howell, R.Rodney

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Electron microscopy in the diagnosis of lysosomal storage diseases von Vogler, Carole, Rosenberg, Harvey S., Williams, Julian C., Butler, Ian, Opitz, John M., Bernstein, Jay

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Chromosomal localization of the human glycoasparaginase gene to 4q32-q33 von MORRIS, C, HEISTERKAMP, N, GROFFEN, J, WILLIAMS, J. C, MONONEN, I

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Aspartylglycosaminuria in a non-Finnish patient caused by a donor splice mutation in the glycoasparaginase gene von MONONEN, HEISTERKAMP, N, KAARTINEN, MONONEN, T, WILLIAMS, JC, GROFFEN, J

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Postoperative alterations in interorgan glutamine exchange in enterectomized dogs von Souba, Wiley W., Roughneen, Patrick T., Goldwater, Diane L., Williams, Julian C., Rowlands, Brian J.

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Urine glyceraldehyde excretion is elevated in the renal Fanconi syndrome von Jonas, Adam J., Lin, Shen-Nan, Conley, Susan B., Schneider, Jerry A., Williams, Julian C., Caprioli, Richard C.

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BIOTIN-DEPENDENT PROPIONIC ACIDEMIA: A NEW VARIANT von Hillman, Richard E, Williams, Julian C

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Method for producing a cement precast floor tile von WILLIAMS JULIAN C

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Method of magnesium oxychloride cement stucco application von WILLIAMS JULIAN C

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Method of densifying light magnesia and of cements containing it von WILLIAMS JULIAN C

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Card index von WILLIAMS JULIAN C

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Nojirimycin-A potent inhibitor of purified lysosomal alpha-glucosidase from human liver von Chambers, James P., Elbein, Alan D., Williams, Julian C.

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