Human mitochondrial DNA replication machinery and disease von Young, Matthew J, Copeland, William C

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Inherited mitochondrial diseases of DNA replication von Copeland, William C

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Role of the mitochondrial DNA replication machinery in mitochondrial DNA mutagenesis, aging and age-related diseases von DeBalsi, Karen L, Hoff, Kirsten E, Copeland, William C

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POLG-related disorders and their neurological manifestations von Rahman, Shamima, Copeland, William C.

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Automated systematic evaluation of cryo-EM specimens with SmartScope von Bouvette, Jonathan, Huang, Qinwen, Riccio, Amanda A, Copeland, William C, Bartesaghi, Alberto, Borgnia, Mario J

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Structures of the mitochondrial single-stranded DNA binding protein with DNA and DNA polymerase γ von Riccio, Amanda A, Bouvette, Jonathan, Pedersen, Lars C, Somai, Shruti, Dutcher, Robert C, Borgnia, Mario J, Copeland, William C

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Ribonucleotide Discrimination and Reverse Transcription by the Human Mitochondrial DNA Polymerase von Kasiviswanathan, Rajesh, Copeland, William C.

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Ultrasensitive deletion detection links mitochondrial DNA replication, disease, and aging von Lujan, Scott A, Longley, Matthew J, Humble, Margaret H, Lavender, Christopher A, Burkholder, Adam, Blakely, Emma L, Alston, Charlotte L, Gorman, Grainne S, Turnbull, Doug M, McFarland, Robert, Taylor, Robert W, Kunkel, Thomas A, Copeland, William C

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Coordinated DNA polymerization by Polγ and the region of LonP1 regulated proteolysis von Riccio, Amanda A, Brannon, Asia J, Krahn, Juno M, Bouvette, Jonathan, Williams, Jason G, Borgnia, Mario J, Copeland, William C

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Structure-specific roles for PolG2–DNA complexes in maintenance and replication of mitochondrial DNA von Wojtaszek, Jessica L, Hoff, Kirsten E, Longley, Matthew J, Kaur, Parminder, Andres, Sara N, Wang, Hong, Williams, R Scott, Copeland, William C

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DNA polymerase gamma and mitochondrial disease: Understanding the consequence of POLG mutations von Chan, Sherine S.L., Copeland, William C.

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Mitochondrial toxicity of nrti antiviral drugs: an integrated cellular perspective von Lewis, William, Day, Brian J, Copeland, William C

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Mitochondrial single-stranded DNA binding protein novel de novo SSBP1 mutation in a child with single large-scale mtDNA deletion (SLSMD) clinically manifesting as Pearson, Kearns-S... von Gustafson, Margaret A, McCormick, Elizabeth M, Perera, Lalith, Longley, Matthew J, Bai, Renkui, Kong, Jianping, Dulik, Matthew, Shen, Lishuang, Goldstein, Amy C, McCormack, Shana E, Laskin, Benjamin L, Leroy, Bart P, Ortiz-Gonzalez, Xilma R, Ellington, Meredith G, Copeland, William C, Falk, Marni J

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Characterization of the human homozygous R182W POLG2 mutation in mitochondrial DNA depletion syndrome von Hoff, Kirsten E, DeBalsi, Karen L, Sanchez-Quintero, Maria J, Longley, Matthew J, Hirano, Michio, Naini, Ali B, Copeland, William C

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Long Patch Base Excision Repair in Mammalian Mitochondrial Genomes von Szczesny, Bartosz, Tann, Anne W., Longley, Matthew J., Copeland, William C., Mitra, Sankar

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Complementation of aprataxin deficiency by base excision repair enzymes in mitochondrial extracts von Çaglayan, Melike, Prasad, Rajendra, Krasich, Rachel, Longley, Matthew J, Kadoda, Kei, Tsuda, Masataka, Sasanuma, Hiroyuki, Takeda, Shunichi, Tano, Keizo, Copeland, William C, Wilson, Samuel H

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MMS exposure promotes increased MtDNA mutagenesis in the presence of replication-defective disease-associated DNA polymerase γ variants von Stumpf, Jeffrey D, Copeland, William C

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DNA polymerases in the mitochondria: A critical review of the evidence von Krasich, Rachel, Copeland, William C

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Polg2 is essential for mammalian embryogenesis and is required for mtDNA maintenance von Humble, Margaret M, Young, Matthew J, Foley, Julie F, Pandiri, Arun R, Travlos, Greg S, Copeland, William C

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RECQL4 localizes to mitochondria and preserves mitochondrial DNA integrity von Croteau, Deborah L., Rossi, Marie L., Canugovi, Chandrika, Tian, Jane, Sykora, Peter, Ramamoorthy, Mahesh, Wang, ZhengMing, Singh, Dharmendra Kumar, Akbari, Mansour, Kasiviswanathan, Rajesh, Copeland, William C., Bohr, Vilhelm A.

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