Field Anesthesia of the Maned Wolf (Chrysocyon brachyurus) in Bolivia von Bronson, Ellen, Deem, Sharon L., Westermann, Lena C. Patino, Alpire, Sixto Angulo, Emmons, Louise H.

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Pathogenic variants in GNPTAB and GNPTG encoding distinct subunits of GlcNAc-1-phosphotransferase differentially impact bone resorption in patients with mucolipidosis type II and I... von Di Lorenzo, Giorgia, Westermann, Lena M., Yorgan, Timur A., Stürznickel, Julian, Ludwig, Nataniel F., Ammer, Luise S., Baranowsky, Anke, Ahmadi, Shiva, Pourbarkhordariesfandabadi, Elham, Breyer, Sandra R., Board, Tim N., Foster, Anne, Mercer, Jean, Tylee, Karen, Velho, Renata Voltolini, Schweizer, Michaela, Renné, Thomas, Braulke, Thomas, Randon, Dévora N., Sperb-Ludwig, Fernanda, de Camargo Pinto, Louise Lapagesse, Moreno, Carolina Araujo, Cavalcanti, Denise P., Amling, Michael, Kutsche, Kerstin, Winter, Dominic, Muschol, Nicole M., Schwartz, Ida V. D., Rolvien, Tim, Danyukova, Tatyana, Schinke, Thorsten, Pohl, Sandra

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Transgenic inhibition of interleukin-6 trans-signaling does not prevent skeletal pathologies in mucolipidosis type II mice von Westermann, Lena Marie, Baranowsky, Anke, Di Lorenzo, Giorgia, Danyukova, Tatyana, Soul, Jamie, Schwartz, Jean-Marc, Hendrickx, Gretl, Amling, Michael, Rose-John, Stefan, Garbers, Christoph, Schinke, Thorsten, Pohl, Sandra

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First person - Lena Marie Westermann von Westermann, Lena Marie

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Imbalanced cellular metabolism compromises cartilage homeostasis and joint function in a mouse model of mucolipidosis type III gamma von Westermann, Lena Marie, Fleischhauer, Lutz, Vogel, Jonas, Jenei-Lanzl, Zsuzsa, Ludwig, Nataniel Floriano, Schau, Lynn, Morellini, Fabio, Baranowsky, Anke, Yorgan, Timur A., Di Lorenzo, Giorgia, Schweizer, Michaela, Pinheiro, Bruna de Souza, Guarany, Nicole Ruas, Sperb-Ludwig, Fernanda, Visioli, Fernanda, Silva, Thiago Oliveira, Soul, Jamie, Hendrickx, Gretl, Wiegert, J. Simon, Schwartz, Ida V. D., Clausen-Schaumann, Hauke, Zaucke, Frank, Schinke, Thorsten, Pohl, Sandra, Danyukova, Tatyana

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Analysis of drug-specific antibody response against cerliponase alfa in CLN2 patients by applying a novel two-step assay von Westermann, Lena Marie, Junginger, Zoe-Isabella, Mann, Anna Marei, Tolosa, Eva, Schulz, Angela

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Hamburg iNCL scale: A new tool for the quantitative description of disease progression in infantile CLN1 patients von Nickel, Miriam, Schwering, Christoph, Westermann, Lena, Wibbeler, Eva, Lezius, Susanne, Schulz, Angela

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Real-world clinical outcomes of intraventricular cerliponase alfa in CLN2 disease: 4.5-year update from an independent ongoing observational study von Schulz, Angela, Schwering, Christoph, Wibbeler, Eva, Westermann, Lena, Dulz, Simon, Lezius, Susanne, Nickel, Miriam

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The relationship between the expanded neuronal ceroid lipofuscinosis 2 (CLN2) clinical rating scale for motor function (CLN2 CRS-MX) and GAITRite® parameters von Hagenah, Luca, Schwering, Christoph, Wilson, Catherine, Wibbeler, Eva, Westermann, Lena Marie, Cho, Yoonjin, Nickel, Miriam, Schulz, Angela, Phillips, Dawn

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The expanded neuronal ceroid lipofuscinosis 2 (CLN2) clinical rating scale for motor and language function: Development and inter-rater reliability von Phillips, Dawn, Cho, Yoonjin, Nevoret, Marie-Laure, Wood, Michelle, Nickel, Miriam, Schwering, Christoph, Westermann, Lena Marie, Schulz, Angela

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Safety and efficacy of cerliponase alfa in children with neuronal ceroid lipofuscinosis type 2 (CLN2 disease): an open-label extension study von Schulz, Angela, Specchio, Nicola, de Los Reyes, Emily, Gissen, Paul, Nickel, Miriam, Trivisano, Marina, Aylward, Shawn C, Chakrapani, Anupam, Schwering, Christoph, Wibbeler, Eva, Westermann, Lena Marie, Ballon, Douglas J, Dyke, Jonathan P, Cherukuri, Anu, Bondade, Shailesh, Slasor, Peter, Cohen Pfeffer, Jessica

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Transgenic inhibition of interleukin-6 trans-signaling does not prevent skeletal pathologies in mucolipidosis type II mice von Westermann, Lena Marie, Baranowsky, Anke, Di Lorenzo, Giorgia, Danyukova, Tatyana, Soul, Jamie, Schwartz, Jean-Marc, Hendrickx, Gretl, Amling, Michael, Rose-John, Stefan, Garbers, Christoph, Schinke, Thorsten, Pohl, Sandra

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Distinct Modes of Balancing Glomerular Cell Proteostasis in Mucolipidosis Type II and III Prevent Proteinuria von Sachs, Wiebke, Sachs, Marlies, Krueger, Elke, Zielinski, Stephanie, Kretz, Oliver, Huber, Tobias B., Baranowsky, Anke, Westermann, Lena Marie, Velho, Renata Voltolini, Ludwig, Nataniel Floriano, Yorgan, Timur Alexander, Di Lorenzo, Giorgia, Kollmann, Katrin, Braulke, Thomas, Schwartz, Ida Vanessa, Schinke, Thorsten, Danyukova, Tatyana, Pohl, Sandra, Meyer-Schwesinger, Catherine

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Imbalanced cellular metabolism compromises cartilage homeostasis and joint function in a mouse model of mucolipidosis type III gamma von Westermann, Lena Marie, Fleischhauer, Lutz, Vogel, Jonas, Jenei-Lanzl, Zsuzsa, Ludwig, Nataniel Floriano, Schau, Lynn, Morellini, Fabio, Baranowsky, Anke, Yorgan, Timur A, Di Lorenzo, Giorgia, Schweizer, Michaela, Pinheiro, Bruna de Souza, Guarany, Nicole Ruas, Sperb-Ludwig, Fernanda, Visioli, Fernanda, Silva, Thiago Oliveira, Soul, Jamie, Hendrickx, Gretl, Wiegert, J. Simon, Schwartz, Ida V.D, Clausen-Schaumann, Hauke, Zaucke, Frank, Schinke, Thorsten, Pohl, Sandra, Danyukova, Tatyana

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Computertomographische Analyse der ossären Mikroarchitektur mit räumlichem Bezug zu einem osteochondralen Defekt – Entwicklung einer distanzabhängigen Darstellungsmethode von Westermann, Lena

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Imbalanced cellular metabolism compromises cartilage homeostasis and joint function in a mouse model of mucolipidosis type III gamma von Westermann, Lena M, Fleischhauer, Lutz, Vogel, Jonas, Jenei-Lanzl, Zsuzsa, Floriano Ludwig, Nataniel, Schau, Lynn, Morellini, Fabio, Baranowsky, Anke, Yorgan, Timur A, Di Lorenzo, Giorgia, Schweizer, Michaela, de Souza Pinheiro, Bruna, Guarany, Nicole Ruas, Sperb-Ludwig, Fernanda, Visioli, Fernanda, Oliveira Silva, Thiago, Soul, Jamie, Hendrickx, Gretl, Wiegert, J Simon, Schwartz, Ida V D, Clausen-Schaumann, Hauke, Zaucke, Frank, Schinke, Thorsten, Pohl, Sandra, Danyukova, Tatyana

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Updated: Data upload for Tagless LysoIP method for molecular profiling of lysosomal content in clinical samples von Saarela, Daniel, Lis, Pawel, Gomes, Sara, Nirujogi, Raja, Dong, Wentao, Rawat, Eshaan, Glendinning, Sophie, Zeneviciute, Karolina, Bagnoli, Enrico, Fasimoye, Rotimi, Lin, Cindy, Nyame, Kwamina, Boros, Fanni A., Zunke, Frederike, Lamoliatte, Frederic, Elshani, Sadik, Jaconelli, Matthew, Jans, Judith, Huisman, Margriet A., Posern, Christian, Westermann, Lena, Schulz, Angela, van Hasselt, Peter, Alessi, Dario, Abu-Remaileh, Monther, Sammler, Esther

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Triple RNA-Seq Reveals Synergy in a Human Virus-Fungus Co-infection Model von Seelbinder, Bastian, Wallstabe, Julia, Marischen, Lothar, Weiss, Esther, Wurster, Sebastian, Page, Lukas, Löffler, Claudia, Bussemer, Lydia, Schmitt, Anna-Lena, Wolf, Thomas, Linde, Jörg, Cicin-Sain, Luka, Becker, Jennifer, Kalinke, Ulrich, Vogel, Jörg, Panagiotou, Gianni, Einsele, Hermann, Westermann, Alexander J., Schäuble, Sascha, Loeffler, Juergen

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Microbial regulation of hexokinase 2 links mitochondrial metabolism and cell death in colitis von Hinrichsen, Finn, Hamm, Jacob, Westermann, Magdalena, Schröder, Lena, Shima, Kensuke, Mishra, Neha, Walker, Alesia, Sommer, Nina, Klischies, Kenneth, Prasse, Daniela, Zimmermann, Johannes, Kaiser, Sina, Bordoni, Dora, Fazio, Antonella, Marinos, Georgios, Laue, Georg, Imm, Simon, Tremaroli, Valentina, Basic, Marijana, Häsler, Robert, Schmitz, Ruth A., Krautwald, Stefan, Wolf, Andrea, Stecher, Bärbel, Schmitt-Kopplin, Philippe, Kaleta, Christoph, Rupp, Jan, Bäckhed, Fredrik, Rosenstiel, Philip, Sommer, Felix

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Increased levels of mitochondrial import factor Mia40 prevent the aggregation of polyQ proteins in the cytosol von Schlagowski, Anna M, Knöringer, Katharina, Morlot, Sandrine, Sánchez Vicente, Ana, Flohr, Tamara, Krämer, Lena, Boos, Felix, Khalid, Nabeel, Ahmed, Sheraz, Schramm, Jana, Murschall, Lena M, Haberkant, Per, Stein, Frank, Riemer, Jan, Westermann, Benedikt, Braun, Ralf J, Winklhofer, Konstanze F, Charvin, Gilles, Herrmann, Johannes M

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