Pathogenic cascades in lysosomal disease--Why so complex? von Walkley, S. U

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Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice von KOLLMANN, K, DAMME, M, KÄKELÄ, R, WALKLEY, S. U, BRAULKE, T, MARKMANN, S, MORELLE, W, SCHWEIZER, M, HERMANS-BORGMEYER, I, RÖCHERT, A. K, POHL, S, LÜBKE, T, MICHALSKI, J.-C

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Bone Marrow Transplantation Corrects the Enzyme Defect in Neurons of the Central Nervous System in a Lysosomal Storage Disease von WALKLEY, S. U, THRALL, M. A, DOBRENIS, K, HUANG, M, MARCH, P. A, SIEGEL, D. A, WURZELMANN, S

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Gangliosides as Modulators of Dendritogenesis in Normal and Storage Disease-affected Pyramidal Neurons von Walkley, Steven U., Zervas, Mark, Wiseman, Samson

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Lysosomal storage diseases of animals: an essay in comparative pathology von Jolly, R.D. (Massey University, Palmerston North, New Zealand.), Walkley, S.U

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Abnormal neuronal metabolism and storage in mucopolysaccharidosis type VI (Maroteaux-Lamy) disease von Walkley, S. U., Thrall, M. A., Haskins, M. E., Mitchell, T. W., Wenger, D. A., Brown, D. E., Dial, S., Seim, H.

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A mouse model for mucopolysaccharidosis type III A (Sanfilippo syndrome) von Bhaumik, Mantu, Muller, Vivienne J., Rozaklis, Tina, Linda, Johnson, Dobrenis, Kostantin, Bhattacharyya, Riddhi, Wurzelmann, Sarah, Finamore, Peter, Hopwood, John J., Walkley, Steven U., Stanley, Pamela

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GABAergic neuroaxonal dystrophy and other cytopathological alterations in feline Niemann-Pick disease type C von MARCH, P. A, THRALL, M. A, BROWN, D. E, MITCHELL, T. W, LOWENTHAL, A. C, WALKLEY, S. U

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Pyramidal neurons with ectopic dendrites in storage diseases exhibit increased GM2 ganglioside immunoreactivity von Walkley, S.U.

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Neurons in Niemann-Pick Disease Type C Accumulate Gangliosides as Well as Unesterified Cholesterol and Undergo Dendritic and Axonal Alterations von ZERVAS, MARK, DOBRENIS, KOSTANTIN, WALKLEY, STEVEN U

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Mitochondrial dysfunction in the neuronal ceroid-lipofuscinoses (Batten disease) von Jolly, R.D., Brown, S., Das, A.M., Walkley, S.U.

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Secondary accumulation of gangliosides in lysosomal storage disorders von Walkley, Steven U

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Altered vitamin E status in Niemann-Pick type C disease von Ulatowski, L., Parker, R., Davidson, C., Yanjanin, N., Kelley, T.J., Corey, D., Atkinson, J., Porter, F., Arai, H., Walkley, S.U., Manor, D.

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Critical role for glycosphingolipids in Niemann-Pick disease type C von Zervas, Mark, Somers, Kyra L, Thrall, Mary Anna, Walkley, Steven U

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Cellular Pathology of Lysosomal Storage Disorders von Walkley, Steven U.

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Consequences of NPC1 and NPC2 loss of function in mammalian neurons von Walkley, Steven U., Suzuki, Kinuko

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Differential subcellular localization of cholesterol, gangliosides, and glycosaminoglycans in murine models of mucopolysaccharide storage disorders von McGlynn, Robert, Dobrenis, Kostantin, Walkley, Steven U.

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GM2 ganglioside and pyramidal neuron dendritogenesis von WALKLEY, S. U, SIEGEL, D. A, DOBRENIS, K

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Bone marrow transplantation for lysosomal diseases von Walkley, S.U., Dobrenis, K.

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Feline Niemann-Pick disease type C von BROWN, D. E, THRALL, M. A, WALKLEY, S. U, WENGER, D. A, MITCHELL, T. W, SMITH, M. O, ROYALS, K. L, MARCH, P. A, ALLISON, R. W

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