Structure of the human GlcNAc-1-phosphotransferase αβ subunits reveals regulatory mechanism for lysosomal enzyme glycan phosphorylation von Li, Hua, Lee, Wang-Sik, Feng, Xiang, Bai, Lin, Jennings, Benjamin C., Liu, Lin, Doray, Balraj, Canfield, William M., Kornfeld, Stuart, Li, Huilin

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Structural Requirements for Efficient Processing and Activation of Recombinant Human UDP-N-acetylglucosamine:Lysosomal-enzyme-N-acetylglucosamine-1-phosphotransferase von Kudo, Mariko, Canfield, William M.

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Structural basis for recognition of phosphodiester-containing lysosomal enzymes by the cation-independent mannose 6-phosphate receptor von Olson, Linda J., Peterson, Francis C., Castonguay, Alicia, Bohnsack, Richard N., Kudo, Mariko, Gotschall, Russell R., Canfield, William M., Volkman, Brian F., Dahms, Nancy M.

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Mucolipidosis II (I-Cell Disease) and Mucolipidosis IIIA (Classical Pseudo-Hurler Polydystrophy) Are Caused by Mutations in the GlcNAc-Phosphotransferase α/β–Subunits Precursor Gen... von Kudo, Mariko, Brem, Michael S., Canfield, William M.

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Hyaluronan Biosynthesis by Class I Streptococcal Hyaluronan Synthases Occurs at the Reducing End von Tlapak-Simmons, Valarie L., Baron, Christina A., Gotschall, Russell, Haque, Dewan, Canfield, William M., Weigel, Paul H.

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Glycoengineered Acid α-Glucosidase With Improved Efficacy at Correcting the Metabolic Aberrations and Motor Function Deficits in a Mouse Model of Pompe Disease von Zhu, Yunxiang, Jiang, Ji-Lei, Gumlaw, Nathan K, Zhang, Jinhua, Bercury, Scott D, Ziegler, Robin J, Lee, Karen, Kudo, Mariko, Canfield, William M, Edmunds, Timothy, Jiang, Canwen, Mattaliano, Robert J, Cheng, Seng H

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Functions of the α, β, and γ Subunits of UDP-GlcNAc:Lysosomal Enzyme N-Acetylglucosamine-1-phosphotransferase von Qian, Yi, Lee, Intaek, Lee, Wang-Sik, Qian, Meiqian, Kudo, Mariko, Canfield, William M., Lobel, Peter, Kornfeld, Stuart

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Cloning and Expression of Human Core 1 β1,3-Galactosyltransferase von Ju, Tongzhong, Brewer, Kevin, D'Souza, Anil, Cummings, Richard D., Canfield, William M.

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Cation-independent mannose 6-phosphate receptor: a composite of distinct phosphomannosyl binding sites von Bohnsack, Richard N, Song, Xuezheng, Olson, Linda J, Kudo, Mariko, Gotschall, Russell R, Canfield, William M, Cummings, Richard D, Smith, David F, Dahms, Nancy M

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The α- and β-subunits of the Human UDP-N-acetylglucosamine:Lysosomal Enzyme Phosphotransferase Are Encoded by a Single cDNA von Kudo, Mariko, Bao, Ming, D'Souza, Anil, Ying, Fu, Pan, Huaqin, Roe, Bruce A., Canfield, William M.

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Domain 5 of the Cation-Independent Mannose 6-Phosphate Receptor Preferentially Binds Phosphodiesters (Mannose 6-Phosphate N-Acetylglucosamine Ester) von Chavez, Carrie A, Bohnsack, Richard N, Kudo, Mariko, Gotschall, Russell R, Canfield, William M, Dahms, Nancy M

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Purification, Characterization, and Subunit Structure of Rat Core 1 β1,3-Galactosyltransferase von Ju, Tongzhong, Cummings, Richard D., Canfield, William M.

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Lysosomal Acid α-Glucosidase Consists of Four Different Peptides Processed from a Single Chain Precursor von Moreland, Rodney J., Jin, Xiaoying, Zhang, X. Kate, Decker, Roger W., Albee, Karen L., Lee, Karen L., Cauthron, Robert D., Brewer, Kevin, Edmunds, Tim, Canfield, William M.

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A Novel Glycosulfopeptide Binds to P-selectin and Inhibits Leukocyte Adhesion to P-selectin von Leppänen, Anne, Mehta, Padmaja, Ouyang, Ying-Bin, Ju, Tongzhong, Helin, Jari, Moore, Kevin L., van Die, Irma, Canfield, William M., McEver, Rodger P., Cummings, Richard D.

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Species-specific differences in the processing of acid α-glucosidase are due to the amino acid identity at position 201 von Moreland, Rodney J., Higgins, Sheri, Zhou, AnQiang, VanStraten, Peter, Cauthron, Robert D., Brem, Michael, McLarty, Beverly J., Kudo, Mariko, Canfield, William M.

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Molecular basis of variant pseudo-hurler polydystrophy (mucolipidosis IIIC) von Raas-Rothschild, A, Cormier-Daire, V, Bao, M, Genin, E, Salomon, R, Brewer, K, Zeigler, M, Mandel, H, Toth, S, Roe, B, Munnich, A, Canfield, W M

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Molecular order in mucolipidosis II and III nomenclature von Cathey, Sara S., Kudo, Mariko, Tiede, Stephan, Raas-Rothschild, Annick, Braulke, Thomas, Beck, Michael, Taylor, Harold A., Canfield, William M., Leroy, Jules G., Neufeld, Elizabeth F., McKusick, Victor A.

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Cation-independent Mannose 6-Phosphate Receptor von Bohnsack, Richard N., Song, Xuezheng, Olson, Linda J., Kudo, Mariko, Gotschall, Russell R., Canfield, William M., Cummings, Richard D., Smith, David F., Dahms, Nancy M.

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Anticoagulant properties of bovine plasma protein C following activation by thrombin von Kisiel, Walter, Canfield, William M, Ericsson, Lowell H, Davie, Earl W

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Residues Throughout the Cytoplasmic Domain Affect the Internalization Efficiency of P-selectin () von Setiadi, Hendra, Disdier, Magali, Green, Samuel A., Canfield, William M., McEver, Rodger P.

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