Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains von Orrú, Christina D, Groveman, Bradley R, Raymond, Lynne D, Hughson, Andrew G, Nonno, Romolo, Zou, Wenquan, Ghetti, Bernardino, Gambetti, Pierluigi, Caughey, Byron

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Lack of Transmission of Chronic Wasting Disease Prions to Human Cerebral Organoids von Groveman, Bradley R, Williams, Katie, Race, Brent, Foliaki, Simote, Thomas, Tina, Hughson, Andrew G, Walters, Ryan O, Zou, Wenquan, Haigh, Cathryn L

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Stress and viral insults do not trigger E200K PrP conversion in human cerebral organoids von Smith, Anna, Groveman, Bradley R, Winkler, Clayton, Williams, Katie, Walters, Ryan, Yuan, Jue, Zou, Wenquan, Peterson, Karin, Foliaki, Simote T, Haigh, Cathryn L

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Structural evidence for the critical role of the prion protein hydrophobic region in forming an infectious prion von Abskharon, Romany, Wang, Fei, Wohlkonig, Alexandre, Ruan, Juxin, Soror, Sameh, Giachin, Gabriele, Pardon, Els, Zou, Wenquan, Legname, Giuseppe, Ma, Jiyan, Steyaert, Jan

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Transmission characteristics of variably protease-sensitive prionopathy von Notari, Silvio, Xiao, Xiangzhu, Espinosa, Juan Carlos, Cohen, Yvonne, Qing, Liuting, Aguilar-Calvo, Patricia, Kofskey, Diane, Cali, Ignazio, Cracco, Laura, Kong, Qingzhong, Torres, Juan Maria, Zou, Wenquan, Gambetti, Pierluigi

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Neuronal excitatory-to-inhibitory balance is altered in cerebral organoid models of genetic neurological diseases von Foliaki, Simote T, Schwarz, Benjamin, Groveman, Bradley R, Walters, Ryan O, Ferreira, Natalia C, Orrù, Christina D, Smith, Anna, Wood, Aleksandar, Schmit, Olivia M, Freitag, Phoebe, Yuan, Jue, Zou, Wenquan, Bosio, Catharine M, Carroll, James A, Haigh, Cathryn L

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Evaluating the Diagnostic Efficacy of Using Pooled Samples for Chronic Wasting Disease Testing and Surveillance von Hepker, Monica, Zhang, Jianqiang, Anantharam, Vellareddy, Kanthasamy, Anumantha G, Yuan, Jue, Zou, Wenquan, Ruden, Rachel M

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COASY variant as a new genetic cause of riboflavin-responsive lipid storage myopathy von Zheng, Yilei, Liufu, Tongling, Wen, Bing, Zhou, Chao, Liu, Lingchun, Qiu, Yusen, Zou, Wenquan, Zhang, Wei, Li, Yu, Pei, Jianfeng, Zeng, Yiheng, Chen, Wanjin, Zhang, Chunhua, Yuan, Yun, Wang, Guochun, Yan, Chuanzhu, Lu, Xin, Deng, Jianwen, Wang, Zhaoxia, Hong, Daojun

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Chronic Wasting Disease of Elk: Transmissibility to Humans Examined by Transgenic Mouse Models von Kong, Qingzhong, Huang, Shenghai, Zou, Wenquan, Vanegas, Difernando, Wang, Meiling, Wu, Di, Yuan, Jue, Zheng, Mengjie, Bai, Hua, Deng, Huayun, Chen, Ken, Jenny, Allen L, O'Rourke, Katherine, Belay, Ermias D, Schonberger, Lawrence B, Petersen, Robert B, Sy, Man-Sun, Chen, Shu G, Gambetti, Pierluigi

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Pathogenic Prion Protein Isoforms Are Not Present in Cerebral Organoids Generated from Asymptomatic Donors Carrying the E200K Mutation Associated with Familial Prion Disease von Foliaki, Simote, Groveman, Bradley, Yuan, Jue, Walters, Ryan, Zhang, Shulin, Tesar, Paul, Zou, Wenquan, Haigh, Cathryn

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Genetic Influence on the Structural Variations of the Abnormal Prion Protein von Parchi, P, Zou, W, Wang, W, Brown, P, Capellari, S, Ghetti, B, Kopp, N, Schulz-Schaeffer, W J, Kretzschmar, H A, Head, M W, Ironside, J W, Gambetti, P, Chen, S G

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Correction: Bank Vole Prion Protein As an Apparently Universal Substrate for RT-QuIC-Based Detection and Discrimination of Prion Strains von Orrú, Christina D, Groveman, Bradley R, Raymond, Lynne D, Hughson, Andrew G, Nonno, Romolo, Zou, Wenquan, Ghetti, Bernardino, Gambetti, Pierluigi, Caughey, Byron

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In Vivo Diagnosis of Synucleinopathies: A Comparative Study of Skin Biopsy and RT-QuIC von Donadio, Vincenzo, Wang, Zerui, Incensi, Alex, Rizzo, Giovanni, Fileccia, Enrico, Vacchiano, Veria, Capellari, Sabina, Magnani, Martina, Scaglione, Cesa, Stanzani Maserati, Michelangelo, Avoni, Patrizia, Liguori, Rocco, Zou, Wenquan

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Real Time Quaking Induced Conversion (RT-QuIC) for Skin Alpha-Synuclein Seeding Activity in Parkinson Disease Versus Controls (P1-1.Virtual) von Gunzler, Steven, Tatsuoka, Curtis, Elkasaby, Mohamed, Wang, Alexander, Chen, Shu, Wang, Zerui, Zou, Wenquan

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Different Patterns of Truncated Prion Protein Fragments Correlate with Distinct Phenotypes in P102L Gerstmann--Straussler--Scheinker Disease von Parchi, Piero, Chen, Shu G., Brown, Paul, Zou, Wenquan, Capellari, Sabina, Budka, Herbert, Hainfellner, Johannes, Reyes, Patricio F., Golden, Gregory T., Hauw, Jean J., Gajdusek, D. Carleton, Gambetti, Pierluigi

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SKIN α-SYNUCLEIN SEEDING ACTIVITY IN ADULT PATIENTS WITH TYPE 1 GAUCHER DISEASE von LoPiccolo, Mary Kate, Wang, Zerui, Fierro, Luca, Stauffer, Chanan, Zhang, Jing, Tatsuoka, Curtis, Alcalay, Roy, Balwani, Manisha, Zou, Wenquan

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Skin α-synuclein seeding activity in adult patients with Gaucher disease type 1 von LoPiccolo, Mary Kate, Wang, Zerui, Fierro, Luca, Stauffer, Chanan, Zhang, Jing, Tatsouka, Curtis, Alcalay, Roy, Zou, Wenquan, Balwani, Manisha

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In Vivo Diagnosis of Synucleinopathies: A Comparative Study of Skin Biopsy and RT-QuIC von Donadio, Vincenzo, Wang, Zerui, Incensi, Alex, Rizzo, Giovanni, Fileccia, Enrico, Vacchiano, Veria, Capellari, Sabina, Magnani, Martina, Scaglione, Cesa, Stanzani Maserati, Michelangelo, Avoni, Patrizia, Liguori, Rocco, Zou, Wenquan

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Cellular prion protein (PrP(C)) and its role in stress responses von Zeng, Liang, Zou, Wenquan, Wang, Gongxian

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Prion protein is essential for diabetic retinopathy-associated neovascularization von Zhu, Lingyan, Xu, Jixiong, Liu, Ying, Gong, Tian, Liu, Jianying, Huang, Qiong, Fischbach, Shane, Zou, Wenquan, Xiao, Xiangwei

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