2.7 Å cryo-EM structure of ex vivo RML prion fibrils von Manka, Szymon W., Zhang, Wenjuan, Wenborn, Adam, Betts, Jemma, Joiner, Susan, Saibil, Helen R., Collinge, John, Wadsworth, Jonathan D. F.

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A naturally occurring variant of the human prion protein completely prevents prion disease von Asante, Emmanuel A., Smidak, Michelle, Grimshaw, Andrew, Houghton, Richard, Tomlinson, Andrew, Jeelani, Asif, Jakubcova, Tatiana, Hamdan, Shyma, Richard-Londt, Angela, Linehan, Jacqueline M., Brandner, Sebastian, Alpers, Michael, Whitfield, Jerome, Mead, Simon, Wadsworth, Jonathan D. F., Collinge, John

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Structural features distinguishing infectious ex vivo mammalian prions from non-infectious fibrillar assemblies generated in vitro von Terry, Cassandra, Harniman, Robert L., Sells, Jessica, Wenborn, Adam, Joiner, Susan, Saibil, Helen R., Miles, Mervyn J., Collinge, John, Wadsworth, Jonathan D. F.

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Spontaneous generation of prions and transmissible PrP amyloid in a humanised transgenic mouse model of A117V GSS von Asante, Emmanuel A., Linehan, Jacqueline M., Tomlinson, Andrew, Jakubcova, Tatiana, Hamdan, Shyma, Grimshaw, Andrew, Smidak, Michelle, Jeelani, Asif, Nihat, Akin, Mead, Simon, Brandner, Sebastian, Wadsworth, Jonathan D. F., Collinge, John

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Overexpression of mouse prion protein in transgenic mice causes a non-transmissible spongiform encephalopathy von Jackson, Graham S., Linehan, Jacqueline, Brandner, Sebastian, Asante, Emmanuel A., Wadsworth, Jonathan D. F., Collinge, John

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A Novel Prion Disease Associated with Diarrhea and Autonomic Neuropathy von Mead, Simon, Gandhi, Sonia, Beck, Jon, Caine, Diana, Gallujipali, Dillip, Carswell, Christopher, Hyare, Harpreet, Joiner, Susan, Ayling, Hilary, Lashley, Tammaryn, Linehan, Jacqueline M, Al-Doujaily, Huda, Sharps, Bernadette, Revesz, Tamas, Sandberg, Malin K, Reilly, Mary M, Koltzenburg, Martin, Forbes, Alastair, Rudge, Peter, Brandner, Sebastian, Warren, Jason D, Wadsworth, Jonathan D.F, Wood, Nicholas W, Holton, Janice L, Collinge, John

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Human Prion Protein with Valine 129 Prevents Expression of Variant CJD Phenotype von Jonathan D. F. Wadsworth, Asante, Emmanuel A., Desbruslais, Melanie, Linehan, Jacqueline M., Joiner, Susan, Gowland, Ian, Welch, Julie, Stone, Lisa, Lloyd, Sarah E., Hill, Andrew F., Brandner, Sebastian, Collinge, John

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Molecular pathology of human prion disease von Wadsworth, Jonathan D. F., Collinge, John

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Clinical Trial Simulations Based on Genetic Stratification and the Natural History of a Functional Outcome Measure in Creutzfeldt-Jakob Disease von Mead, Simon, Burnell, Matthew, Lowe, Jessica, Thompson, Andrew, Lukic, Ana, Porter, Marie-Claire, Carswell, Christopher, Kaski, Diego, Kenny, Janna, Mok, Tze How, Bjurstrom, Nina, Franko, Edit, Gorham, Michele, Druyeh, Ronald, Wadsworth, Jonathan D. F, Jaunmuktane, Zane, Brandner, Sebastian, Hyare, Harpreet, Rudge, Peter, Walker, A. Sarah, Collinge, John

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A structural basis for prion strain diversity von Manka, Szymon W., Wenborn, Adam, Betts, Jemma, Joiner, Susan, Saibil, Helen R., Collinge, John, Wadsworth, Jonathan D. F.

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Prion strains viewed through the lens of cryo-EM von Manka, Szymon W., Wenborn, Adam, Collinge, John, Wadsworth, Jonathan D. F.

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Detection and characterization of proteinase K-sensitive disease-related prion protein with thermolysin von Cronier, Sabrina, Gros, Nathalie, Tattum, M Howard, Jackson, Graham S, Clarke, Anthony R, Collinge, John, Wadsworth, Jonathan D F

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Isolation of proteinase K-sensitive prions using pronase E and phosphotungstic acid von D'Castro, Laura, Wenborn, Adam, Gros, Nathalie, Joiner, Susan, Cronier, Sabrina, Collinge, John, Wadsworth, Jonathan D F

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Variant Creutzfeldt–Jakob Disease in a Patient with Heterozygosity at PRNP Codon 129 von Mok, Tzehow, Jaunmuktane, Zane, Joiner, Susan, Campbell, Tracy, Morgan, Catherine, Wakerley, Benjamin, Golestani, Farhad, Rudge, Peter, Mead, Simon, Jäger, H. Rolf, Wadsworth, Jonathan D.F, Brandner, Sebastian, Collinge, John

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Molecular classification of sporadic Creutzfeldt–Jakob disease von Hill, Andrew F., Joiner, Susan, Wadsworth, Jonathan D. F., Sidle, Katie C. L., Bell, Jeanne E., Budka, Herbert, Ironside, James W., Collinge, John

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Evaluation of plasma tau and neurofilament light chain biomarkers in a 12-year clinical cohort of human prion diseases von Thompson, Andrew G. B., Anastasiadis, Prodromos, Druyeh, Ronald, Whitworth, Ines, Nayak, Annapurna, Nihat, Akin, Mok, Tze How, Rudge, Peter, Wadsworth, Jonathan D. F., Rohrer, Jonathan, Schott, Jonathan M., Heslegrave, Amanda, Zetterberg, Henrik, Collinge, John, Jackson, Graham S., Mead, Simon

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Absence of spontaneous disease and comparative prion susceptibility of transgenic mice expressing mutant human prion proteins von Asante, Emmanuel A, Gowland, Ian, Grimshaw, Andrew, Linehan, Jacqueline M, Smidak, Michelle, Houghton, Richard, Osiguwa, Olufunmilayo, Tomlinson, Andrew, Joiner, Susan, Brandner, Sebastian, Wadsworth, Jonathan D. F, Collinge, John

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Recent Advances in Understanding Mammalian Prion Structure: A Mini Review von Terry, Cassandra, Wadsworth, Jonathan D F

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Prion neuropathology follows the accumulation of alternate prion protein isoforms after infective titre has peaked von Sandberg, Malin K., Al-Doujaily, Huda, Sharps, Bernadette, De Oliveira, Michael Wiggins, Schmidt, Christian, Richard-Londt, Angela, Lyall, Sarah, Linehan, Jacqueline M., Brandner, Sebastian, Wadsworth, Jonathan D. F., Clarke, Anthony R., Collinge, John

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Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein von Wadsworth, Jonathan D. F., Joiner, Susan, Linehan, Jacqueline M., Cooper, Sharon, Powell, Caroline, Mallinson, Gary, Buckell, Jennifer, Gowland, Ian, Asante, Emmanuel A., Budka, Herbert, Brandner, Sebastian, Collinge, John

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