Cellular Mechanotransduction Relies on Tension-Induced and Chaperone-Assisted Autophagy von Ulbricht, Anna, Eppler, Felix J., Tapia, Victor E., van der Ven, Peter F.M., Hampe, Nico, Hersch, Nils, Vakeel, Padmanabhan, Stadel, Daniela, Haas, Albert, Saftig, Paul, Behrends, Christian, Fürst, Dieter O., Volkmer, Rudolf, Hoffmann, Bernd, Kolanus, Waldemar, Höhfeld, Jörg

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Xin Is a Marker of Skeletal Muscle Damage Severity in Myopathies von Nilsson, Mats I, Nissar, Aliyah A, Al-Sajee, Dhuha, Tarnopolsky, Mark A, Parise, Gianni, Lach, Boleslav, Fürst, Dieter O, van der Ven, Peter F.M, Kley, Rudolf A, Hawke, Thomas J

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Filamin C-related myopathies: pathology and mechanisms von Fürst, Dieter O., Goldfarb, Lev G., Kley, Rudolf A., Vorgerd, Matthias, Olivé, Montse, van der Ven, Peter F. M.

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Isoform-specific functions of synaptopodin-2 variants in cytoskeleton stabilization and autophagy regulation in muscle under mechanical stress von Lohanadan, Keerthika, Molt, Sibylle, Dierck, Franziska, van der Ven, Peter F.M., Frey, Norbert, Höhfeld, Jörg, Fürst, Dieter O.

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Mutations in the N-terminal Actin-Binding Domain of Filamin C Cause a Distal Myopathy von DUFF, Rachael M, TAY, Valerie, SONG, Jaeguen, DJINOVIC-CARUGO, Kristina, PENTTILÄ, Sini, RAHEEM, Olayinka, REARDON, Katrina, MALANDRINI, Alessandro, GAMBELLI, Simona, VILLANOVA, Marcello, NOWAK, Kristen J, WILLIAMS, David R, HACKMAN, Peter, LANDERS, John E, BROWN, Robert H, UDD, Bjarne, LAING, Nigel G, RAVENSCROFT, Gianina, MCLEAN, Catriona, KENNEDY, Paul, STEINBACH, Alina, SCHÖFFLER, Wiebke, VAN DER VEN, Peter F. M, FÜRST, Dieter O

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A Mutation in the Dimerization Domain of Filamin C Causes a Novel Type of Autosomal Dominant Myofibrillar Myopathy von Vorgerd, Matthias, van der Ven, Peter F.M., Bruchertseifer, Vera, Löwe, Thomas, Kley, Rudolf A., Schröder, Rolf, Lochmüller, Hanns, Himmel, Mirko, Koehler, Katrin, Fürst, Dieter O., Huebner, Angela

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Sarcomeric lesions and remodeling proximal to intercalated disks in overload-induced cardiac hypertrophy von Kebir, Sied, Orfanos, Zacharias, Schuld, Julia, Linhart, Markus, Lamberz, Christian, van der Ven, Peter F.M., Schrickel, Jan, Kirfel, Gregor, Fürst, Dieter O., Meyer, Rainer

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In vivo characterization of human myofibrillar myopathy genes in zebrafish von Bührdel, John B., Hirth, Sofia, Keßler, Mirjam, Westphal, Sören, Forster, Monika, Manta, Linda, Wiche, Gerhard, Schoser, Benedikt, Schessl, Joachim, Schröder, Rolf, Clemen, Christoph S., Eichinger, Ludwig, Fürst, Dieter O., van der Ven, Peter F.M., Rottbauer, Wolfgang, Just, Steffen

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Assembly of Titin, Myomesin and M-protein into the Sarcomeric M band in Differentiating Human Skeletal Muscle Cells in vitro von van der Ven, P F, Fürst, D O

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Mutations in the human muscle LIM protein gene in families with hypertrophic cardiomyopathy von GEIER, Christian, PERROT, Andreas, FÜRST, Dieter O, VORNWALD, Arnold, VON HODENBERG, Eberhard, NÜRNBERG, Peter, SCHEFFOLD, Thomas, DIETZ, Rainer, OSTERZIEL, Karl Josef, ÖZCELIK, Cemil, BINNER, Priska, COUNSELL, Damian, HOFFMANN, Katrin, PILZ, Bernhard, MARTINIAK, Yvonne, GEHMLICH, Katja, VAN DER VEN, Peter F. M

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Unusual splicing events result in distinct Xin isoforms that associate differentially with filamin c and Mena/VASP von van der Ven, Peter F.M., Ehler, Elisabeth, Vakeel, Padmanabhan, Eulitz, Stefan, Schenk, Jörg A., Milting, Hendrik, Micheel, Burkhard, Fürst, Dieter O.

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The pathomechanism of filaminopathy: altered biochemical properties explain the cellular phenotype of a protein aggregation myopathy von Löwe, Thomas, Kley, Rudolf A., van der Ven, Peter F.M., Himmel, Mirko, Huebner, Angela, Vorgerd, Matthias, Fürst, Dieter O.

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Recessive Mutations in SYNPO2 as a Candidate of Monogenic Nephrotic Syndrome von Mao, Youying, Schneider, Ronen, van der Ven, Peter F.M., Assent, Marvin, Lohanadan, Keerthika, Klämbt, Verena, Buerger, Florian, Kitzler, Thomas M., Deutsch, Konstantin, Nakayama, Makiko, Majmundar, Amar J., Mann, Nina, Hermle, Tobias, Onuchic-Whitford, Ana C., Zhou, Wei, Margam, Nandini Nagarajan, Duncan, Roy, Marquez, Jonathan, Khokha, Mustafa, Fathy, Hanan M., Kari, Jameela A., El Desoky, Sherif, Eid, Loai A., Awad, Hazem Subhi, Al-Saffar, Muna, Mane, Shrikant, Lifton, Richard P., Fürst, Dieter O., Shril, Shirlee, Hildebrandt, Friedhelm

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Myotilin, the limb-girdle muscular dystrophy 1A (LGMD1A) protein, cross-links actin filaments and controls sarcomere assembly von Salmikangas, Paula, van der Ven, Peter F.M., Lalowski, Maciej, Taivainen, Anu, Zhao, Fang, Suila, Heli, Schröder, Rolf, Lappalainen, Pekka, Fürst, Dieter O., Carpén, Olli

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Enrichment and terminal differentiation of striated muscle progenitors in vitro von Becher, Ulrich M., Breitbach, Martin, Sasse, Philipp, Garbe, Stephan, van der Ven, Peter F.M., Fürst, Dieter O., Fleischmann, Bernd K.

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Distribution of ferritin complex in the adult brain and altered composition in neuroferritinopathy due to a novel variant in the ferritin heavy chain gene FTH1 (c.409_410del; p.H13... von Umathum, Vincent, Weber, Axel, Amsel, Daniel, Alexopoulos, Ioannis, Becker, Christina, Roth, Angela, Günther, Andreas, Selignow, Carmen, Ritschel, Nadja, Nishimura, Anna, Schaiter, Alexander, Németh, Attila, Ven, Peter F. M., Acker, Till, Schänzer, Anne

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Disorganization of the Desmin Cytoskeleton and Mitochondrial Dysfunction in Plectin-Related Epidermolysis Bullosa Simplex with Muscular Dystrophy von SCHRÖDER, ROLF, KUNZ, WOLFRAM S, ROUAN, FATIMA, PFENDNER, ELLEN, TOLKSDORF, KAREN, KAPPES-HORN, KARIN, ALTENSCHMIDT-MEHRING, MANUELA, KNOBLICH, RUPERT, VAN DER VEN, PETER F.M, REIMANN, JENS, FÜRST, DIETER O, BLÜMCKE, INGMAR, VIELHABER, STEFAN, ZILLIKENS, DETLEF, EMING, SABINE, KLOCKGETHER, THOMAS, UITTO, JOUNI, WICHE, GERHARD, ROLFS, ARNDT

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Filamin C interacts with the muscular dystrophy KY protein and is abnormally distributed in mouse KY deficient muscle fibres von Beatham, Jane, Romero, Rosario, Townsend, Stuart K.M., Hacker, Terry, van der Ven, Peter F.M., Blanco, Gonzalo

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Filamin-A-interacting protein 1 (FILIP1) is a dual compartment protein linking myofibrils and microtubules during myogenic differentiation and upon mechanical stress von Grande, Valentina, Schuld, Julia, van der Ven, Peter F. M., Gruss, Oliver J., Fürst, Dieter O.

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Filamin C is a highly dynamic protein associated with fast repair of myofibrillar microdamage von Leber, Yvonne, Ruparelia, Avnika A, Kirfel, Gregor, van der Ven, Peter F M, Hoffmann, Bernd, Merkel, Rudolf, Bryson-Richardson, Robert J, Fürst, Dieter O

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