Food Products Made with Glycomacropeptide, a Low-Phenylalanine Whey Protein, Provide a New Alternative to Amino Acid–Based Medical Foods for Nutrition Management of Phenylketonuria... von van Calcar, Sandra C., PhD, RD, Ney, Denise M., PhD, RD

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Recommendations for the nutrition management of phenylalanine hydroxylase deficiency von Singh, Rani H., Rohr, Fran, Frazier, Dianne, Cunningham, Amy, Mofidi, Shideh, Ogata, Beth, Splett, Patricia L., Moseley, Kathryn, Huntington, Kathleen, Acosta, Phyllis B., Vockley, Jerry, Van Calcar, Sandra C.

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The efficacy of Carbamylglutamate impacts the nutritional management of patients with N-Acetylglutamate synthase deficiency von Singh, Rani H, Bourdages, Marie-Hélène, Kurtz, Angela, MacLoed, Erin, Norman, Chelsea, Ratko, Suzanne, van Calcar, Sandra C, Kenneson, Aileen

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Abnormal Eating Behaviors Are Common in Children with Fetal Alcohol Spectrum Disorder von Amos-Kroohs, Robyn M., PhD, Fink, Birgit A., BA, Smith, Carol J., BS, Chin, Lyanne, BS, Van Calcar, Sandra C., PhD, RD, Wozniak, Jeffrey R., PhD, Smith, Susan M., PhD

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Prevalence and mutation analysis of short/branched chain acyl-CoA dehydrogenase deficiency (SBCADD) detected on newborn screening in Wisconsin von Van Calcar, Sandra C., Baker, Mei W., Williams, Phillip, Jones, Susan A., Xiong, Blia, Thao, Mai Choua, Lee, Sheng, Yang, Mai Khou, Rice, Greg M., Rhead, William, Vockley, Jerry, Hoffman, Gary, Durkin, Maureen S.

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Metabolomic Insights into the Nutritional Status of Adults and Adolescents with Phenylketonuria Consuming a Low-Phenylalanine Diet in Combination with Amino Acid and Glycomacropept... von Levy, Harvey L., Gleason, Sally T., Rohr, Frances, Murali, Sangita G., Ney, Denise M., Stroup, Bridget M., van Calcar, Sandra C.

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International clinical guideline for the management of classical galactosemia: diagnosis, treatment, and follow-up von Welling, Lindsey, Bernstein, Laurie E., Berry, Gerard T., Burlina, Alberto B., Eyskens, François, Gautschi, Matthias, Grünewald, Stephanie, Gubbels, Cynthia S., Knerr, Ina, Labrune, Philippe, van der Lee, Johanna H., MacDonald, Anita, Murphy, Elaine, Portnoi, Pat A., Õunap, Katrin, Potter, Nancy L., Rubio-Gozalbo, M. Estela, Spencer, Jessica B., Timmers, Inge, Treacy, Eileen P., Van Calcar, Sandra C., Waisbren, Susan E., Bosch, Annet M.

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Newborn screening 50 years later: access issues faced by adults with PKU von Berry, Susan A., Brown, Christine, Grant, Mitzie, Greene, Carol L., Jurecki, Elaina, Koch, Jean, Moseley, Kathryn, Suter, Ruth, van Calcar, Sandra C., Wiles, Judy, Cederbaum, Stephen

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Outcomes and genotype-phenotype correlations in 52 individuals with VLCAD deficiency diagnosed by NBS and enrolled in the IBEM-IS database von Pena, Loren D.M., van Calcar, Sandra C., Hansen, Joyanna, Edick, Mathew J., Walsh Vockley, Cate, Leslie, Nancy, Cameron, Cynthia, Mohsen, Al-Walid, Berry, Susan A., Arnold, Georgianne L., Vockley, Jerry

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Inappropriate Feeding Behaviors and Dietary Intakes in Children with Fetal Alcohol Spectrum Disorder or Probable Prenatal Alcohol Exposure von Werts, Rachel L., Van Calcar, Sandra C., Wargowski, David S., Smith, Susan M.

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A re-evaluation of life-long severe galactose restriction for the nutrition management of classic galactosemia von Van Calcar, Sandra C., Bernstein, Laurie E., Rohr, Frances J., Scaman, Christine H., Yannicelli, Steven, Berry, Gerard T.

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Breakfast with glycomacropeptide compared with amino acids suppresses plasma ghrelin levels in individuals with phenylketonuria von MacLeod, Erin L., Clayton, Murray K., van Calcar, Sandra C., Ney, Denise M.

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Improved nutritional management of phenylketonuria by using a diet containing glycomacropeptide compared with amino acids von VAN CALCAR, Sandra C, MACLEOD, Erin L, GLEASON, Sally T, ETZEL, Mark R, CLAYTON, Murray K, WOLFF, Jon A, NEY, Denise M

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Galactose Content of Legumes, Caseinates, and Some Hard Cheeses: Implications for Diet Treatment of Classic Galactosemia von Van Calcar, Sandra C, Bernstein, Laurie E, Rohr, Frances J, Yannicelli, Steven, Berry, Gerard T, Scaman, Christine H

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Reassessment of phenylalanine tolerance in adults with phenylketonuria is needed as body mass changes von MacLeod, Erin L., Gleason, Sally T., van Calcar, Sandra C., Ney, Denise M.

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Acceptable low-phenylalanine foods and beverages can be made with glycomacropeptide from cheese whey for individuals with PKU von Lim, Kyungwha, van Calcar, Sandra C., Nelson, Kathryn L., Gleason, Sally T., Ney, Denise M.

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Dietary Glycomacropeptide Supports Growth and Reduces the Concentrations of Phenylalanine in Plasma and Brain in a Murine Model of Phenylketonuria von NEY, Denise M, HULL, Angela K, VAN CALCAR, Sandra C, XIAOWEN LIU, ETZEL, Mark R

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L-Carnitine Administration Reduces Number of Episodes in Cyclic Vomiting Syndrome von Van Calcar, Sandra C., Harding, Cary O., Wolff, Jon A.

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Prospective Diagnosis of 2-Methylbutyryl-CoA Dehydrogenase Deficiency in the Hmong Population by Newborn Screening Using Tandem Mass Spectrometry von Matern, Dietrich, He, Miao, Berry, Susan A, Rinaldo, Piero, Whitley, Chester B, Madsen, Pia P, van Calcar, Sandra C, Lussky, Richard C, Andresen, Brage S, Wolff, Jon A, Vockley, Jerry

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Bone Health in Classic Galactosemia: Systematic Review and Meta-Analysis von van Erven, Britt, Welling, Lindsey, van Calcar, Sandra C., Doulgeraki, Artemis, Eyskens, François, Gribben, Joanna, Treacy, Eileen P., Vos, Rein, Waisbren, Susan E., Rubio-Gozalbo, M. Estela, Bosch, Annet M.

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