Mitochondrial pharmacotherapy during pregnancy and lactation in an ADPKD mouse model: a win for both mothers and their offspring von Wang, Wei, Tran, Pamela V

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Kidney epithelial targeted mitochondrial transcription factor A deficiency results in progressive mitochondrial depletion associated with severe cystic disease von Ishii, Ken, Kobayashi, Hanako, Taguchi, Kensei, Guan, Nan, Li, Andraia, Tong, Carmen, Davidoff, Olena, Tran, Pamela V., Sharma, Madhulika, Chandel, Navdeep S., Kapp, Meghan E., Fogo, Agnes B., Brooks, Craig R., Haase, Volker H.

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Actin cytoskeletal regulation of ciliogenesis in development and disease von Hufft-Martinez, Brittany M, Wang, Henry H, Saadi, Irfan, Tran, Pamela V

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Quinomycin A reduces cyst progression in polycystic kidney disease von Radadiya, Priyanka S., Thornton, Mackenzie M., Daniel, Emily A., Idowu, Jessica Y., Wang, Wei, Magenheimer, Brenda, Subramaniam, Dharmalingam, Tran, Pamela V., Calvet, James P., Wallace, Darren P., Sharma, Madhulika

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Unique spatiotemporal requirements for intraflagellar transport genes during forebrain development von Snedeker, John, Schock, Elizabeth N, Struve, Jamie N, Chang, Ching-Fang, Cionni, Megan, Tran, Pamela V, Brugmann, Samantha A, Stottmann, Rolf W

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IFT‐A deficiency in juvenile mice impairs biliary development and exacerbates ADPKD liver disease von Wang, Wei, Pottorf, Tana S, Wang, Henry H, Dong, Ruochen, Kavanaugh, Matthew A, Cornelius, Joseph T, Dennis, Katie L, Apte, Udayan, Pritchard, Michele T, Sharma, Madhulika, Tran, Pamela V

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Dysfunction of intraflagellar transport proteins beyond the primary cilium von Tran, Pamela V

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Genetic interaction of mammalian IFT‐A paralogs regulates cilia disassembly, ciliary entry of membrane protein, Hedgehog signaling, and embryogenesis von Wang, Wei, Allard, Bailey A., Pottorf, Tana S., Wang, Henry H., Vivian, Jay L., Tran, Pamela V.

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Aberrant Regulation of Notch3 Signaling Pathway in Polycystic Kidney Disease von Idowu, Jessica, Home, Trisha, Patel, Nisha, Magenheimer, Brenda, Tran, Pamela V., Maser, Robin L., Ward, Christopher J., Calvet, James P., Wallace, Darren P., Sharma, Madhulika

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SPECC1L deficiency causes shortened primary cilia and genetically interacts with IFT‐A deficiency to affect palatogenesis von Hufft‐Martinez, Brittany M., Goering, Jeremy P., Stestiv, Marta, Moedritzer, Michael J., Wang, Henry H., Tran, Pamela V., Saadi, Irfan

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Intraflagellar Transport Proteins as Regulators of Primary Cilia Length von Wang, Wei, Jack, Brittany M., Wang, Henry H., Kavanaugh, Matthew A., Maser, Robin L., Tran, Pamela V.

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Ciclopirox olamine induces ferritinophagy and reduces cyst burden in polycystic kidney disease von Radadiya, Priyanka S., Thornton, Mackenzie M., Puri, Rajni, Yerrathota, Sireesha, Dinh-Phan, Johnny, Magenheimer, Brenda, Subramaniam, Dharmalingam, Tran, Pamela, Zhu, Hao, Bolisetty, Subhashini, Calvet, James P., Wallace, Darren P., Sharma, Madhulika

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Inhibition of Hedgehog signaling suppresses proliferation and microcyst formation of human Autosomal Dominant Polycystic Kidney Disease cells von Silva, Luciane M., Jacobs, Damon T., Allard, Bailey A., Fields, Timothy A., Sharma, Madhulika, Wallace, Darren P., Tran, Pamela V.

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THM1 negatively modulates mouse sonic hedgehog signal transduction and affects retrograde intraflagellar transport in cilia von Turbe-Doan, Annick, Shah, Jagesh V, Stottmann, Rolf W, Chesebro, Allyson L, Haycraft, Courtney J, Yoder, Bradley K, Qiu, Haiyan, Beier, David R, Tran, Pamela V, Besschetnova, Tatiana Y, Herron, Bruce J, Scherz, Paul J

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Downregulating hedgehog signaling reduces renal cystogenic potential of mouse models von Tran, Pamela V, Talbott, George C, Turbe-Doan, Annick, Jacobs, Damon T, Schonfeld, Michael P, Silva, Luciane M, Chatterjee, Anindita, Prysak, Mary, Allard, Bailey A, Beier, David R

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Ttc21b deficiency attenuates autosomal dominant polycystic kidney disease in a kidney tubular- and maturation-dependent manner von Wang, Wei, Silva, Luciane M., Wang, Henry H., Kavanaugh, Matthew A., Pottorf, Tana S., Allard, Bailey A., Jacobs, Damon T., Dong, Ruochen, Cornelius, Joseph T., Chaturvedi, Aakriti, Swenson-Fields, Katherine I., Fields, Timothy A., Pritchard, Michele T., Sharma, Madhulika, Slawson, Chad, Wallace, Darren P., Calvet, James P., Tran, Pamela V.

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Thm2 interacts with paralog, Thm1, and sensitizes to Hedgehog signaling in postnatal skeletogenesis von Allard, Bailey A., Wang, Wei, Pottorf, Tana S., Mumtaz, Hammad, Jack, Brittany M., Wang, Henry H., Silva, Luciane M., Jacobs, Damon T., Wang, Jinxi, Bumann, Erin E., Tran, Pamela V.

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Genetic Interaction of Thm2 and Thm1 Shapes Postnatal Craniofacial Bone von Bumann, Erin E, Hahn Leat, Portia, Wang, Henry H, Hufft-Martinez, Brittany M, Wang, Wei, Tran, Pamela V

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Corrigendum to “Ttc21b deficiency attenuates autosomal dominant polycystic kidney disease in a kidney tubular- and maturation-dependent manner.” Kidney Int. 2022;102:577–591 von Wang, Wei, Silva, Luciane M., Wang, Henry H., Kavanaugh, Matthew A., Pottorf, Tana S., Allard, Bailey A., Jacobs, Damon T., Dong, Ruochen, Cornelius, Joseph T., Chaturvedi, Aakriti, Swenson-Fields, Katherine I., Fields, Timothy A., Pritchard, Michele T., Sharma, Madhulika, Slawson, Chad, Wallace, Darren P., Calvet, James P., Tran, Pamela V.

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Casein kinase 1ε and 1α as novel players in polycystic kidney disease and mechanistic targets for (R)-roscovitine and (S)-CR8 von Billot, Katy, Coquil, Charlène, Villiers, Benoit, Josselin-Foll, Béatrice, Desban, Nathalie, Delehouzé, Claire, Oumata, Nassima, Le Meur, Yannick, Boletta, Alessandra, Weimbs, Thomas, Grosch, Melanie, Witzgall, Ralph, Saunier, Sophie, Fischer, Evelyne, Pontoglio, Marco, Fautrel, Alain, Mrug, Michal, Wallace, Darren, Tran, Pamela V, Trudel, Marie, Bukanov, Nikolay, Ibraghimov-Beskrovnaya, Oxana, Meijer, Laurent

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