Expression of CTNS Alleles: Subcellular Localization and Aminoglycoside Correction in Vitro von Helip-Wooley, A., Park, M.A., Lemons, R.M., Thoene, J.G.

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Mediated calcium transport by isolated human fibroblast lysosomes von LEMONS, R. M, THOENE, J. G

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Characterization of carrier-mediated transport systems for small neutral amino acids in human fibroblast lysosomes von Pisoni, R.L., Flickinger, K.S., Thoene, J.G., Christensen, H.N.

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Impaired intestinal absorption of biotin in juvenile multiple carboxylase deficiency von Thoene, J.G, Lemons, R, Baker, H

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Cystine depletion of cystinotic tissues by phosphocysteamine (WR638) von Thoene, J.G., Lemons, R.

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Dual-column high-performance liquid chromatographic urinary organic acid profiling von Buchanan, D.N., Thoene, J.G.

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Photodiode array ultraviolet spectrophotometric profiling of carboxylic acids in physiological fluids von BUCHANAN, D. N, THOENE, J. G

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