Interdomain Contacts and the Stability of Serralysin Protease from Serratia marcescens von Zhang, Liang, Morrison, Anneliese J, Thibodeau, Patrick H

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Loss of cardiomyocyte CYB5R3 impairs redox equilibrium and causes sudden cardiac death von Carew, Nolan T, Schmidt, Heidi M, Yuan, Shuai, Galley, Joseph C, Hall, Robert, Altmann, Helene M, Hahn, Scott A, Miller, Megan P, Wood, Katherine C, Gabris, Bethann, Stapleton, Margaret C, Hartwick, Sean, Fazzari, Marco, Wu, Yijen L, Trebak, Mohamed, Kaufman, Brett A, McTiernan, Charles F, Schopfer, Francisco J, Navas, Placido, Thibodeau, Patrick H, McNamara, Dennis M, Salama, Guy, Straub, Adam C

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Small heat shock proteins target mutant cystic fibrosis transmembrane conductance regulator for degradation via a small ubiquitin-like modifier-dependent pathway von Ahner, Annette, Gong, Xiaoyan, Schmidt, Bela Z, Peters, Kathryn W, Rabeh, Wael M, Thibodeau, Patrick H, Lukacs, Gergely L, Frizzell, Raymond A

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Iron bioavailability regulates Pseudomonas aeruginosa interspecies interactions through type VI secretion expression von Haas, Allison L., Zemke, Anna C., Melvin, Jeffrey A., Armbruster, Catherine R., Hendricks, Matthew R., Moore, John, Nouraie, Seyed Mehdi, Thibodeau, Patrick H., Lee, Stella E., Bomberger, Jennifer M.

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Non-native Conformers of Cystic Fibrosis Transmembrane Conductance Regulator NBD1 Are Recognized by Hsp27 and Conjugated to SUMO-2 for Degradation von Gong, Xiaoyan, Ahner, Annette, Roldan, Ariel, Lukacs, Gergely L., Thibodeau, Patrick H., Frizzell, Raymond A.

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Calcium-induced Folding and Stabilization of the Pseudomonas aeruginosa Alkaline Protease von Zhang, Liang, Conway, James F., Thibodeau, Patrick H.

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Modulation of the epithelial sodium channel (ENaC) by bacterial metalloproteases and protease inhibitors von Butterworth, Michael B, Zhang, Liang, Liu, Xiaoning, Shanks, Robert M, Thibodeau, Patrick H

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Regulation of ABCC6 trafficking and stability by a conserved C-terminal PDZ-like sequence von Xue, Peng, Crum, Chelsea M, Thibodeau, Patrick H

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Commentary on Variants in the ABCC6 Gene Implicated in Pseudoxanthoma Elasticum, a Heritable Ectopic Mineralization Disorder von Zheng, Aiping, Thibodeau, Patrick H.

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Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator von Lewis, Hal A, Buchanan, Sean G, Burley, Stephen K, Conners, Kris, Dickey, Mark, Dorwart, Michael, Fowler, Richard, Gao, Xia, Guggino, William B, Hendrickson, Wayne A, Hunt, John F, Kearins, Margaret C, Lorimer, Don, Maloney, Peter C, Post, Kai W, Rajashankar, Kanagalaghatta R, Rutter, Marc E, Sauder, J Michael, Shriver, Stephanie, Thibodeau, Patrick H, Thomas, Philip J, Zhang, Marie, Zhao, Xun, Emtage, Spencer

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Structural analysis reveals pathomechanisms associated with pseudoxanthoma elasticum–causing mutations in the ABCC6 transporter von Ran, Yanchao, Zheng, Aiping, Thibodeau, Patrick H.

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Stabilization of Nucleotide Binding Domain Dimers Rescues ABCC6 Mutants Associated with Pseudoxanthoma Elasticum von Ran, Yanchao, Thibodeau, Patrick H.

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ESCRT-dependent targeting of plasma membrane localized KCa3.1 to the lysosomes von Balut, Corina M, Gao, Yajuan, Murray, Sandra A, Thibodeau, Patrick H, Devor, Daniel C

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The Cystic Fibrosis-causing Mutation ΔF508 Affects Multiple Steps in Cystic Fibrosis Transmembrane Conductance Regulator Biogenesis von Thibodeau, Patrick H., Richardson, John M., Wang, Wei, Millen, Linda, Watson, Jarod, Mendoza, Juan L., Du, Kai, Fischman, Sharon, Senderowitz, Hanoch, Lukacs, Gergely L., Kirk, Kevin, Thomas, Philip J.

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Activation of the Epithelial Sodium Channel (ENaC) by the Alkaline Protease from Pseudomonas aeruginosa von Butterworth, Michael B., Zhang, Liang, Heidrich, Elisa M., Myerburg, Michael M., Thibodeau, Patrick H.

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CFTR regulatory region interacts with NBD1 predominantly via multiple transient helices von Baker, Jennifer M R, Hudson, Rhea P, Kanelis, Voula, Choy, Wing-Yiu, Thibodeau, Patrick H, Thomas, Philip J, Forman-Kay, Julie D

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NMR evidence for differential phosphorylation-dependent interactions in WT and ΔF508 CFTR von Kanelis, Voula, Hudson, Rhea P, Thibodeau, Patrick H, Thomas, Philip J, Forman-Kay, Julie D

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Stabilization of a nucleotide-binding domain of the cystic fibrosis transmembrane conductance regulator yields insight into disease-causing mutations von Vernon, Robert M., Chong, P. Andrew, Lin, Hong, Yang, Zhengrong, Zhou, Qingxian, Aleksandrov, Andrei A., Dawson, Jennifer E., Riordan, John R., Brouillette, Christie G., Thibodeau, Patrick H., Forman-Kay, Julie D.

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Identification of SlpB, a Cytotoxic Protease from Serratia marcescens von Shanks, Robert M Q, Stella, Nicholas A, Hunt, Kristin M, Brothers, Kimberly M, Zhang, Liang, Thibodeau, Patrick H

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Mutations in the Yeast Hsp70, Ssa1, at P417 Alter ATP Cycling, Interdomain Coupling, and Specific Chaperone Functions von Needham, Patrick G., Patel, Hardik J., Chiosis, Gabriela, Thibodeau, Patrick H., Brodsky, Jeffrey L.

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