NorUDCA promotes degradation of α1-antitrypsin mutant Z protein by inducing autophagy through AMPK/ULK1 pathway von Tang, Youcai, Blomenkamp, Keith S, Fickert, Peter, Trauner, Michael, Teckman, Jeffrey H

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Rapamycin reduces intrahepatic alpha-1-antitrypsin mutant Z protein polymers and liver injury in a mouse model von Kaushal, Shalesh, Annamali, Mani, Blomenkamp, Keith, Rudnick, David, Halloran, Donna, Brunt, Elizabeth M, Teckman, Jeffrey H

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Bone marrow stem cell therapy partially ameliorates pathological consequences in livers of mice expressing mutant human α1‐antitrypsin von Baligar, Prakash, Kochat, Veena, Arindkar, Shailendra K., Equbal, Zaffar, Mukherjee, Snehashish, Patel, Swati, Nagarajan, Perumal, Mohanty, Sujata, Teckman, Jeffrey H., Mukhopadhyay, Asok

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Biomarkers Associated With Future Severe Liver Disease in Children With Alpha-1-Antitrypsin Deficiency von Teckman, Jeffrey H., Buchanan, Paula, Blomenkamp, Keith Steven, Heyer-Chauhan, Nina, Burling, Keith, Lomas, David A.

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AFM Imaging Reveals Topographic Diversity of Wild Type and Z Variant Polymers of Human α1-Proteinase Inhibitor von Gaczynska, Maria, Karpowicz, Przemyslaw, Stuart, Christine E, Norton, Malgorzata G, Teckman, Jeffrey H, Marszal, Ewa, Osmulski, Pawel A

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Liver Disease in Alpha-1 Antitrypsin Deficiency: Current Understanding and Future Therapy von Teckman, Jeffrey H.

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Quality of Life and Its Determinants in a Multicenter Cohort of Children with Alagille Syndrome von Kamath, Binita M., MBBChir, Chen, Zhen, MS, Romero, Rene, MD, Fredericks, Emily M., PhD, Alonso, Estella M., MD, Arnon, Ronen, MD, Heubi, James, MD, Hertel, Paula M., MD, Karpen, Saul J., MD, PhD, Loomes, Kathleen M., MD, Murray, Karen F., MD, Rosenthal, Philip, MD, Schwarz, Kathleen B., MD, Subbarao, Girish, MD, Teckman, Jeffrey H., MD, Turmelle, Yumirle P., MD, Wang, Kasper S., MD, Sherker, Averell H., MD, Sokol, Ronald J., MD, Magee, John C., MD

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Amelioration of Alpha-1 Antitrypsin Deficiency Diseases with Genome Editing in Transgenic Mice von Shen, Shen, Sanchez, Minerva E, Blomenkamp, Keith, Corcoran, Erik M, Marco, Eugenio, Yudkoff, Clifford J, Jiang, Haiyan, Teckman, Jeffrey H, Bumcrot, David, Albright, Charles F

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Pathophysiology of Alpha-1 Antitrypsin Deficiency Liver Disease von Teckman, Jeffrey H., Blomenkamp, Keith S.

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Characteristics of hepatocellular carcinoma in a murine model of alpha-1-antitrypsin deficiency von Marcus, Nancy Y., Brunt, Elizabeth M., Blomenkamp, Keith, Ali, Faiza, Rudnick, David A., Ahmad, Muneeb, Teckman, Jeffrey H.

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Up-regulation of miR-34b/c by JNK and FOXO3 protects from liver fibrosis von Piccolo, Pasquale, Ferriero, Rosa, Barbato, Anna, Attanasio, Sergio, Monti, Marcello, Perna, Claudia, Borel, Florie, Annunziata, Patrizia, Carissimo, Annamaria, De Cegli, Rossella, Quagliata, Luca, Terracciano, Luigi M., Housset, Chantal, Teckman, Jeffrey H., Mueller, Christian, Brunetti-Pierri, Nicola

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Alpha-1 antitrypsin deficiency liver disease von Patel, Dhiren, McAllister, Shannon L, Teckman, Jeffrey H

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Oxidative stress contributes to liver damage in a murine model of alpha-1-antitrypsin deficiency von Marcus, Nancy Y, Blomenkamp, Keith, Ahmad, Muneeb, Teckman, Jeffrey H

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Shear wave elastography correlates with liver fibrosis scores in pediatric patients with liver disease von Farmakis, Shannon G., Buchanan, Paula M., Guzman, Miguel A., Hardy, Anna K., Jain, Ajay K., Teckman, Jeffrey H.

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Advances in Alpha-1-Antitrypsin Deficiency Liver Disease von Teckman, Jeffrey H., Jain, Ajay

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Eating Disorders are Prominent Among the Comorbidities of Eosinophilic Esophagitis in a U.S. Midwestern Children’s Hospital von Powell, Sara D., Teckman, Jeffrey H., Becker, Bradley A.

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Hepatic Histology in Treatment‐naïve Children With Chronic Hepatitis B Infection Living in the United States and Canada von Rodriguez‐Baez, Norberto, Murray, Karen F., Kleiner, David E., Ling, Simon C., Rosenthal, Philip, Carlin, Kristen, Cooper, Kara, Schwarz, Kathleen B., Schwarzenberg, Sarah J., Teckman, Jeffrey H., Ghany, Marc G., Alawad, Ahmad Samer

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Semiquantitation of Monomer and Polymer Alpha-1 Antitrypsin by Centrifugal Separation and Assay by Western Blot of Soluble and Insoluble Components von Blomenkamp, Keith S., Teckman, Jeffrey H.

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α1-Antitrypsin Deficiency in Childhood von Teckman, Jeffrey H

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Mitochondrial autophagy and injury in the liver in alpha 1-antitrypsin deficiency von Teckman, Jeffrey H, An, Jae-Koo, Blomenkamp, Keith, Schmidt, Bela, Perlmutter, David

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