Elucidating the Beneficial Role of PPAR Agonists in Cardiac Diseases von Khuchua, Zaza, Glukhov, Aleksandr I, Strauss, Arnold W, Javadov, Sabzali

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Cardiac metabolic pathways affected in the mouse model of barth syndrome von Huang, Yan, Powers, Corey, Madala, Satish K, Greis, Kenneth D, Haffey, Wendy D, Towbin, Jeffrey A, Purevjav, Enkhsaikhan, Javadov, Sabzali, Strauss, Arnold W, Khuchua, Zaza

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The PPAR pan-agonist bezafibrate ameliorates cardiomyopathy in a mouse model of Barth syndrome von Huang, Yan, Powers, Corey, Moore, Victoria, Schafer, Caitlin, Ren, Mindong, Phoon, Colin K L, James, Jeanne F, Glukhov, Alexander V, Javadov, Sabzali, Vaz, Frédéric M, Jefferies, John L, Strauss, Arnold W, Khuchua, Zaza

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The Effects of PPAR Stimulation on Cardiac Metabolic Pathways in Barth Syndrome Mice von Schafer, Caitlin, Moore, Vicky, Dasgupta, Nupur, Javadov, Sabzali, James, Jeanne F, Glukhov, Alexander I, Strauss, Arnold W, Khuchua, Zaza

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Mitochondrial trifunctional protein deficiency in human cultured fibroblasts: effects of bezafibrate von Djouadi, Fatima, Habarou, Florence, Le Bachelier, Carole, Ferdinandusse, Sacha, Schlemmer, Dimitri, Benoist, Jean François, Boutron, Audrey, Andresen, Brage S., Visser, Gepke, de Lonlay, Pascale, Olpin, Simon, Fukao, Toshiyuki, Yamaguchi, Seiji, Strauss, Arnold W., Wanders, Ronald J. A., Bastin, Jean

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How many minors are participating in clinical research today? An estimate and important lessons learned von Ittenbach, Richard F., Corsmo, Jeremy J., Kissling, Alison D., Strauss, Arnold W.

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A Zebrafish Model of Human Barth Syndrome Reveals the Essential Role of Tafazzin in Cardiac Development and Function von Khuchua, Zaza, Yue, Zou, Batts, Lorene, Strauss, Arnold W

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A Fetal Fatty-Acid Oxidation Disorder as a Cause of Liver Disease in Pregnant Women von Ibdah, Jamal A, Bennett, Michael J, Rinaldo, Piero, Zhao, Yiwen, Gibson, Beverly, Sims, Harold F, Strauss, Arnold W

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Evaluation of Fellows' CrossTalk Effectiveness in Promoting Transdisciplinary Networking and Research von Wikenheiser-Brokamp, Kathryn A., MD, PhD, Klein, Melissa, MD, MEd, Hershey, Gurjit K. Khurana, MD, PhD, Devarajan, Prasad, MD, DeWitt, Thomas G., MD, Loch, Jill, MEd, Strauss, Arnold W., MD, Muglia, Louis J., MD, PhD, Hostetter, Margaret K., MD

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Human placenta metabolizes fatty acids: implications for fetal fatty acid oxidation disorders and maternal liver diseases von Shekhawat, Prem, Bennett, Michael J, Sadovsky, Yoel, Nelson, D. Michael, Rakheja, Dinesh, Strauss, Arnold W

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Enhancing Pediatric Fellows' Research Training: Development of an Office of Pediatric Clinical Fellowships von Klein, Melissa, MD, MEd, Khurana Hershey, Gurjit K., MD, PhD, Devarajan, Prasad, MD, Muglia, Louis J., MD, PhD, Wikenheiser-Brokamp, Kathryn A., MD, PhD, Loch, Jill, MEd, Hostetter, Margaret K., MD, Strauss, Arnold W., MD, DeWitt, Thomas G., MD

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Spectrum of Medium-Chain Acyl-CoA Dehydrogenase Deficiency Detected by Newborn Screening von Hsu, Ho-Wen, Zytkovicz, Thomas H, Comeau, Anne Marie, Strauss, Arnold W, Marsden, Deborah, Shih, Vivian E, Grady, George F, Eaton, Roger B

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Pitfalls of neonatal screening for very-long-chain acyl-CoA dehydrogenase deficiency using tandem mass spectrometry von Schymik, Ina, Liebig, Michaela, Mueller, Martina, Wendel, Udo, Mayatepek, Ertan, Strauss, Arnold W., Wanders, Ronald J.A., Spiekerkoetter, Ute

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Peripheral neuropathy, episodic myoglobinuria, and respiratory failure in deficiency of the mitochondrial trifunctional protein von Spiekerkoetter, Ute, Bennett, Michael J., Ben-Zeev, Bruria, Strauss, Arnold W., Tein, Ingrid

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Mechanism of Hyperinsulinism in Short-chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency Involves Activation of Glutamate Dehydrogenase von Li, Changhong, Chen, Pan, Palladino, Andrew, Narayan, Srinivas, Russell, Laurie K., Sayed, Samir, Xiong, Guoxiang, Chen, Jie, Stokes, David, Butt, Yasmeen M., Jones, Patricia M., Collins, Heather W., Cohen, Noam A., Cohen, Akiva S., Nissim, Itzhak, Smith, Thomas J., Strauss, Arnold W., Matschinsky, Franz M., Bennett, Michael J., Stanley, Charles A.

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Molecular heterogeneity in very-long-chain acyl-CoA dehydrogenase deficiency causing pediatric cardiomyopathy and sudden death von MATHUR, A, SIMS, H. F, GOPALAKRISHNAN, D, GIBSON, B, RINALDO, P, VOCKLEY, J, HUG, G, STRAUSS, A. W

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Polymorphic ventricular tachycardia and abnormal Ca2+ handling in very-long-chain acyl-CoA dehydrogenase null mice von Werdich, Andreas A, Baudenbacher, Franz, Dzhura, Igor, Jeyakumar, Loice H, Kannankeril, Prince J, Fleischer, Sidney, LeGrone, Alison, Milatovic, Dejan, Aschner, Michael, Strauss, Arnold W, Anderson, Mark E, Exil, Vernat J

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Cardiac-specific VLCAD deficiency induces dilated cardiomyopathy and cold intolerance von Xiong, Dingding, He, Huamei, James, Jeanne, Tokunaga, Chonan, Powers, Corey, Huang, Yan, Osinska, Hanna, Towbin, Jeffrey A, Purevjav, Enkhsaikhan, Balschi, James A, Javadov, Sabzali, McGowan, Jr, Francis X, Strauss, Arnold W, Khuchua, Zaza

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Tissue carnitine homeostasis in very-long-chain acyl-CoA dehydrogenase-deficient mice von SPIEKERKOETTER, Ute, TOKUNAGA, Chonan, WANDERS, Ronald J, STRAUSS, Arnold W, WENDEL, Udo, MAYATEPEK, Ertan, IJLST, Lodewijk, VAZ, Frederic M, VAN VLIES, Naomi, OVERMARS, Henk, DURAN, Marinus, WIJBURG, Frits A

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Diagnosis of Very Long Chain Acyl-Dehydrogenase Deficiency From an Infant's Newborn Screening Card von Wood, John C, Magera, Mark J, Rinaldo, Piero, Seashore, Margretta Reed, Strauss, Arnold W, Friedman, Alan

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