Expanded CTG repeats within the DMPK 3' UTR causes severe skeletal muscle wasting in an inducible mouse model for myotonic dystrophy von Orengo, James P, Chambon, Pierre, Metzger, Daniel, Mosier, Dennis R, Snipes, G. Jackson, Cooper, Thomas A

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Oral Curcumin Mitigates the Clinical and Neuropathologic Phenotype of the Trembler-J Mouse: A Potential Therapy for Inherited Neuropathy von Khajavi, Mehrdad, Shiga, Kensuke, Wiszniewski, Wojciech, He, Feng, Shaw, Chad A., Yan, Jiong, Wensel, Theodore G., Snipes, G. Jackson, Lupski, James R.

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Curcumin facilitates a transitory cellular stress response in Trembler-J mice von Okamoto, Yuji, Pehlivan, Davut, Wiszniewski, Wojciech, Beck, Christine R, Snipes, G Jackson, Lupski, James R, Khajavi, Mehrdad

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Curcumin Treatment Abrogates Endoplasmic Reticulum Retention and Aggregation-Induced Apoptosis Associated with Neuropathy-Causing Myelin Protein Zero–Truncating Mutants von Khajavi, Mehrdad, Inoue, Ken, Wiszniewski, Wojciech, Ohyama, Tomoko, Snipes, G. Jackson, Lupski, James R.

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The Texas Immuno-Oncology Biorepository, a statewide biospecimen collection and clinical informatics system to enable longitudinal tumor and immune profiling von Kelly, Ronan J., Whitsett, Timothy G., Snipes, G. Jackson, Dobin, Sheila M., Finholt, Jennifer, Settele, Natalie, Priest, Elisa L., Youens, Kenneth, Wallace, Lucy B., Schwartz, Gary, Wong, Lucas, Henderson, Sherronda M., Gowan, Alan C., Fonkem, Ekokobe, Juarez, Maria I., Murray, Christal E., Wu, Jeffrey, Van Keuren-Jensen, Kendall, Pirrotte, Patrick, Highlander, Sarah, Contente, Tania, Baker, Angela, Victorino, Jose, Berens, Michael E.

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Molecular Mechanisms, Diagnosis, and Rational Approaches to Management of and Therapy for Charcot-Marie-Tooth Disease and Related Peripheral Neuropathies von Saifi, Gulam Mustafa, Szigeti, Kinga, Snipes, Jackson G., Garcia, Carlos A., Lupski, James R.

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Phenotypic Differences between Peripheral Myelin Protein-22 (PMP22) and Myelin Protein Zero (P0) Mutations Associated with Charcot-Marie-Tooth-Related Diseases von SHAMES, IGOR, FRASER, ANDREW, COLBY, JOSHUA, ORFALI, WAYEL, SNIPES, G JACKSON

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Reprogramming tumor-infiltrating dendritic cells for CD103+ CD8+ mucosal T-cell differentiation and breast cancer rejection von Wu, Te-Chia, Xu, Kangling, Banchereau, Romain, Marches, Florentina, Yu, Chun I, Martinek, Jan, Anguiano, Esperanza, Pedroza-Gonzalez, Alexander, Snipes, G Jackson, O'Shaughnessy, Joyce, Nishimura, Stephen, Liu, Yong-Jun, Pascual, Virginia, Banchereau, Jacques, Oh, Sangkon, Palucka, Karolina

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Characterization of Chronic Bronchopulmonary Pseudomonas aeruginosa Infection in Resistant and Susceptible Inbred Mouse Strains von Tam, Mifong, Jackson Snipes, G, Stevenson, Mary M

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Progressive Limb Weakness and Sensory Loss in a Young Woman von Glass, Hannah, Srour, Myriam, Pari, Giovanna, Karpati, George, Snipes, G. Jackson

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Upregulation of Hypoxia-Inducible Factor (HIF)-1α and HIF-2α in Leptomeningeal Vascular Malformations of Sturge-Weber Syndrome von Comati, Amina, Beck, Heike, Halliday, William, Snipes, G Jackson, Plate, Karl Heinz, Acker, Till

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A Protein Induced during Nerve Growth (GAP-43) Is a Major Component of Growth-Cone Membranes von J. H. Pate Skene, Jacobson, Richard D., Snipes, G. Jackson, McGuire, C. Brain, Norden, Jeanette J., Freeman, John A.

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Suppression of Rac activity induces apoptosis of human glioma cells but not normal human astrocytes von SENGER, Donna L, TUDAN, Christopher, GUIOT, Marie-Christine, MAZZONI, Irene E, MOLENKAMP, Gabriele, LEBLANC, Richard, ANTEL, Jack, OLIVIER, Andre, SNIPES, G. Jackson, KAPLAN, David R

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PMP22 Carrying the Trembler or Trembler-J Mutation Is Intracellularly Retained in Myelinating Schwann Cells von Colby, Joshua, Nicholson, Robert, Dickson, Kathleen M., Orfali, Wayel, Naef, Roland, Suter, Ueli, Snipes, G.Jackson

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Upregulation of the Endosomal-Lysosomal Pathway in the Trembler-J Neuropathy von Notterpek, Lucia, Shooter, Eric M, Snipes, G. Jackson

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Signaling pathways mediating axon-Schwann cell interactions von Snipes, G.Jackson, Suter, Ueli

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Charcot-Marie-Tooth Disease Type 1A -- Association with a Spontaneous Point Mutation in the PMP22 Gene von Roa, Benjamin B, Garcia, Carlos A, Suter, Ueli, Kulpa, Deanna A, Wise, Carol A, Mueller, Jane, Welcher, Andrew A, Snipes, G. Jackson, Shooter, Eric M, Patel, Pragna I, Lupski, James R

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Temporal expression pattern of peripheral myelin protein 22 during in vivo and in vitro myelination von Notterpek, Lucia, Snipes, G. Jackson, Shooter, Eric M.

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The gene for the peripheral myelin protein PMP-22 is a candidate for Charcot-Marie-Tooth disease type 1A von Patel, Pragna I, Roa, Benjamin B, Welcher, Andrew A, Schoener-Scott, Raymond, Trask, Barbara J, Pentao, Liu, Snipes, G. Jackson, Garcia, Carlos A, Francke, Uta, Shooter, Eric M, Lupski, James R, Suter, Ueli

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Intracerebral Adenovirus-mediated p53 Tumor Suppressor Gene Therapy for Experimental Human Glioma von HEWEI LI, ALONSO-VANEGAS, M, COLICOS, M. A, JUNG, S. S, LOCHMULLER, H, SADIKOT, A. F, SNIPES, G. J, SETH, P, KARPATI, G, NALBANTOGLU, J

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