Genetics of Sudden Cardiac Death von Bezzina, Connie R, Lahrouchi, Najim, Priori, Silvia G

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Desmoplakin Cardiomyopathy, a Fibrotic and Inflammatory Form of Cardiomyopathy Distinct From Typical Dilated or Arrhythmogenic Right Ventricular Cardiomyopathy von Smith, Eric D., Lakdawala, Neal K., Papoutsidakis, Nikolaos, Aubert, Gregory, Mazzanti, Andrea, McCanta, Anthony C., Agarwal, Prachi P., Arscott, Patricia, Dellefave-Castillo, Lisa M., Vorovich, Esther E., Nutakki, Kavitha, Wilsbacher, Lisa D., Priori, Silvia G., Jacoby, Daniel L., McNally, Elizabeth M., Helms, Adam S.

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Inherited Dysfunction of Sarcoplasmic Reticulum Ca2+ Handling and Arrhythmogenesis von Priori, Silvia G, Chen, S.R Wayne

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Transmural APD heterogeneity determines ventricular arrhythmogenesis in LQT8 syndrome: Insights from Bidomain computational modeling von Scacchi, Simone, Pavarino, Luca F, Mazzanti, Andrea, Trancuccio, Alessandro, Priori, Silvia G, Colli Franzone, Piero

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Gene-Specific Therapy With Mexiletine Reduces Arrhythmic Events in Patients With Long QT Syndrome Type 3 von Mazzanti, Andrea, MD, Maragna, Riccardo, BS, Faragli, Alessandro, MD, Monteforte, Nicola, MD, Bloise, Raffaella, MD, Memmi, Mirella, PhD, Novelli, Valeria, PhD, Baiardi, Paola, PhD, Bagnardi, Vincenzo, PhD, Etheridge, Susan P., MD, Napolitano, Carlo, MD, PhD, Priori, Silvia G., MD, PhD

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Independent validation and clinical implications of the risk prediction model for long QT syndrome (1-2-3-LQTS-Risk) von Mazzanti, Andrea, Trancuccio, Alessandro, Kukavica, Deni, Pagan, Eleonora, Wang, Meng, Mohsin, Muhammad, Peterson, Derick, Bagnardi, Vincenzo, Zareba, Wojciech, Priori, Silvia G

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A novel computational model of swine ventricular myocyte reveals new insights into disease mechanisms and therapeutic approaches in Timothy Syndrome von Trancuccio, Alessandro, Tarifa, Carmen, Bongianino, Rossana, Priori, Silvia G., Santiago, Demetrio J.

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Drugs and Brugada syndrome patients: Review of the literature, recommendations, and an up-to-date website (www.brugadadrugs.org) von Postema, Pieter G., MD, Wolpert, Christian, MD, Amin, Ahmad S., MD, Probst, Vincent, MD, PhD, Borggrefe, Martin, MD, PhD, Roden, Dan M., MD, Priori, Silvia G., MD, PhD, Tan, Hanno L., MD, PhD, Hiraoka, Masayasu, MD, PhD, Brugada, Josep, MD, PhD, Wilde, Arthur A.M., MD, PhD

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Novel Insight Into the Natural History of Short QT Syndrome von Mazzanti, Andrea, MD, Kanthan, Ajita, MBBS, PhD, Monteforte, Nicola, MD, Memmi, Mirella, PhD, Bloise, Raffaella, MD, Novelli, Valeria, PhD, Miceli, Carlotta, MS, O'Rourke, Sean, BS, Borio, Gianluca, MS, Zienciuk-Krajka, Agnieszka, MD, Curcio, Antonio, MD, PhD, Surducan, Andreea Elena, MS, Colombo, Mario, MS, Napolitano, Carlo, MD, PhD, Priori, Silvia G., MD, PhD

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Beta Blocker Therapy for Long QT Syndrome and Catecholaminergic Polymorphic Ventricular Tachycardia: Are all beta blockers equivalent? von Ackerman, Michael J., MD, PhD, Priori, Silvia G., MD, PhD, Dubin, Anne, MD, FHRS, Kowey, Peter, MD, Linker, Nicholas J., MD, FHRS, Slotwiner, David, MD, FHRS, Triedman, John, MD, FHRS, CCDS, CEPS, Van Hare, George F., MD, FHRS, CCDS, CEPS, Gold, Michael R., MD, PhD, FHRS

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Allele Specific Silencing of Mutant mRNA Rescues Ultrastructural and Arrhythmic Phenotype in Mice Carriers of the R4496C Mutation in the Ryanodine Receptor Gene (RYR2) von Bongianino, Rossana, Denegri, Marco, Mazzanti, Andrea, Lodola, Francesco, Vollero, Alessandra, Boncompagni, Simona, Fasciano, Silvia, Rizzo, Giulia, Mangione, Damiano, Barbaro, Serena, Di Fonso, Alessia, Napolitano, Carlo, Auricchio, Alberto, Protasi, Feliciano, Priori, Silvia G

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KCNJ2 mutation in short QT syndrome 3 results in atrial fibrillation and ventricular proarrhythmia von Deo, Makarand, Ruan, Yanfei, Pandit, Sandeep V., Shah, Kushal, Berenfeld, Omer, Blaufox, Andrew, Cerrone, Marina, Noujaim, Sami F., Denegri, Marco, Jalife, José, Priori, Silvia G.

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HRS/EHRA Expert Consensus Statement on the State of Genetic Testing for the Channelopathies and Cardiomyopathies von Ackerman, Michael J., MD, PhD, Priori, Silvia G., MD, PhD, Willems, Stephan, MD, PhD, Berul, Charles, MD, FHRS, CCDS, Brugada, Ramon, MD, PhD, Calkins, Hugh, MD, FHRS, CCDS, Camm, A. John, MD, FHRS, Ellinor, Patrick T., MD, PhD, Gollob, Michael, MD, Hamilton, Robert, MD, CCDS, Hershberger, Ray E., MD, Judge, Daniel P., MD, Le Marec, Hervè, MD, McKenna, William J., MD, Schulze-Bahr, Eric, MD, PhD, Semsarian, Chris, MBBS, PhD, Towbin, Jeffrey A., MD, Watkins, Hugh, MD, PhD, Wilde, Arthur, MD, PhD, Wolpert, Christian, MD, Zipes, Douglas P., MD, FHRS

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Genetically engineered SCN5A mutant pig hearts exhibit conduction defects and arrhythmias von Park, David S, Cerrone, Marina, Morley, Gregory, Vasquez, Carolina, Fowler, Steven, Liu, Nian, Bernstein, Scott A, Liu, Fang-Yu, Zhang, Jie, Rogers, Christopher S, Priori, Silvia G, Chinitz, Larry A, Fishman, Glenn I

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Risk for Life-Threatening Cardiac Events in Patients With Genotype-Confirmed Long-QT Syndrome and Normal-Range Corrected QT Intervals von Goldenberg, Ilan, MD, Horr, Samuel, MA, Moss, Arthur J., MD, Lopes, Coeli M., PhD, Barsheshet, Alon, MD, McNitt, Scott, MS, Zareba, Wojciech, MD, PhD, Andrews, Mark L., BBA, Robinson, Jennifer L., MS, Locati, Emanuela H., MD, Ackerman, Michael J., MD, PhD, Benhorin, Jesaia, MD, Kaufman, Elizabeth S., MD, Napolitano, Carlo, MD, Platonov, Pyotr G., MD, PhD, Priori, Silvia G., MD, PhD, Qi, Ming, MD, Schwartz, Peter J., MD, Shimizu, Wataru, MD, PhD, Towbin, Jeffrey A., MD, Vincent, G. Michael, MD, Wilde, Arthur A.M., MD, PhD, Zhang, Li, MD

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The Structural-Functional Crosstalk of the Calsequestrin System: Insights and Pathological Implications von Marabelli, Chiara, Santiago, Demetrio J, Priori, Silvia G

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Executive Summary: HRS/EHRA/APHRS Expert Consensus Statement on the Diagnosis and Management of Patients with Inherited Primary Arrhythmia Syndromes von Priori, Silvia G., MD, PhD, Wilde, Arthur A., MD, PhD, Horie, Minoru, MD, PhD, Cho, Yongkeun, MD, PhD, Behr, Elijah R., MA, MBBS, MD, FRCP, Berul, Charles, MD, FHRS, CCDS, Blom, Nico, MD, PhD, Brugada, Josep, MD, PhD, Chiang, Chern-En, MD, PhD, Huikuri, Heikki, MD, Kannankeril, Prince, MD, Krahn, Andrew, MD, FHRS, Leenhardt, Antoine, MD, Moss, Arthur, MD, Schwartz, Peter J., MD, Shimizu, Wataru, MD, PhD, Tomaselli, Gordon, MD, FHRS, Tracy, Cynthia, MD

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Short Communication: Flecainide Exerts an Antiarrhythmic Effect in a Mouse Model of Catecholaminergic Polymorphic Ventricular Tachycardia by Increasing the Threshold for Triggered... von Liu, Nian, Denegri, Marco, Ruan, Yanfei, Avelino-Cruz, José Everardo, Perissi, Andrea, Negri, Sara, Napolitano, Carlo, Coetzee, William A, Boyden, Penelope A, Priori, Silvia G

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Diagnosis and treatment of catecholaminergic polymorphic ventricular tachycardia von Napolitano, Carlo, MD, PhD, Priori, Silvia G., MD, PhD

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Catecholaminergic Polymorphic Ventricular Tachycardia von Liu, Nian, Ruan, Yanfei, Priori, Silvia G

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