Mitochondrial RNA Granules Are Centers for Posttranscriptional RNA Processing and Ribosome Biogenesis von Antonicka, Hana, Shoubridge, Eric A.

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The Mitochondrial RNA-Binding Protein GRSF1 Localizes to RNA Granules and Is Required for Posttranscriptional Mitochondrial Gene Expression von Antonicka, Hana, Sasarman, Florin, Nishimura, Tamiko, Paupe, Vincent, Shoubridge, Eric A.

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Reconstitution of mitochondria derived vesicle formation demonstrates selective enrichment of oxidized cargo von Soubannier, Vincent, Rippstein, Peter, Kaufman, Brett A, Shoubridge, Eric A, McBride, Heidi M

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MITRAC Links Mitochondrial Protein Translocation to Respiratory-Chain Assembly and Translational Regulation von Mick, David U., Dennerlein, Sven, Wiese, Heike, Reinhold, Robert, Pacheu-Grau, David, Lorenzi, Isotta, Sasarman, Florin, Weraarpachai, Woranontee, Shoubridge, Eric A., Warscheid, Bettina, Rehling, Peter

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BOLA3 and NFU1 link mitoribosome iron-sulfur cluster assembly to multiple mitochondrial dysfunctions syndrome von Zhong, Hui, Janer, Alexandre, Khalimonchuk, Oleh, Antonicka, Hana, Shoubridge, Eric A, Barrientos, Antoni

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LONP1 Is Required for Maturation of a Subset of Mitochondrial Proteins, and Its Loss Elicits an Integrated Stress Response von Zurita Rendón, Olga, Shoubridge, Eric A.

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Multi-OMICS study of a CHCHD10 variant causing ALS demonstrates metabolic rewiring and activation of endoplasmic reticulum and mitochondrial unfolded protein responses von Straub, Isabella R, Weraarpachai, Woranontee, Shoubridge, Eric A

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A High-Density Human Mitochondrial Proximity Interaction Network von Antonicka, Hana, Lin, Zhen-Yuan, Janer, Alexandre, Aaltonen, Mari J., Weraarpachai, Woranontee, Gingras, Anne-Claude, Shoubridge, Eric A.

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The mitochondrial DNA genetic bottleneck results from replication of a subpopulation of genomes von Shoubridge, Eric A, Wai, Timothy, Teoli, Daniella

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CCDC90A (MCUR1) Is a Cytochrome c Oxidase Assembly Factor and Not a Regulator of the Mitochondrial Calcium Uniporter von Paupe, Vincent, Prudent, Julien, Dassa, Emmanuel P., Rendon, Olga Zurita, Shoubridge, Eric A.

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Mutations in Iron-Sulfur Cluster Scaffold Genes NFU1 and BOLA3 Cause a Fatal Deficiency of Multiple Respiratory Chain and 2-Oxoacid Dehydrogenase Enzymes von Cameron, Jessie M., Janer, Alexandre, Levandovskiy, Valeriy, MacKay, Nevena, Rouault, Tracey A., Tong, Wing-Hang, Ogilvie, Isla, Shoubridge, Eric A., Robinson, Brian H.

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Mutations in the mitochondrial methionyl-tRNA synthetase cause a neurodegenerative phenotype in flies and a recessive ataxia (ARSAL) in humans von Bayat, Vafa, Thiffault, Isabelle, Jaiswal, Manish, Tétreault, Martine, Donti, Taraka, Sasarman, Florin, Bernard, Geneviève, Demers-Lamarche, Julie, Dicaire, Marie-Josée, Mathieu, Jean, Vanasse, Michel, Bouchard, Jean-Pierre, Rioux, Marie-France, Lourenco, Charles M, Li, Zhihong, Haueter, Claire, Shoubridge, Eric A, Graham, Brett H, Brais, Bernard, Bellen, Hugo J

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The Role of Mitochondrial DNA Copy Number in Mammalian Fertility von WAI, Timothy, AO, Asangla, XIAOYUN ZHANG, CYR, Daniel, DUFORT, Daniel, SHOUBRIDGE, Eric A

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The human mitochondrial translation factor TACO1 alleviates mitoribosome stalling at polyproline stretches von Brischigliaro, Michele, Krüger, Annika, Moran, J Conor, Antonicka, Hana, Ahn, Ahram, Shoubridge, Eric A, Rorbach, Joanna, Barrientos, Antoni

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A proximity-dependent biotinylation map of a human cell von Go, Christopher D., Knight, James D. R., Rajasekharan, Archita, Rathod, Bhavisha, Hesketh, Geoffrey G., Abe, Kento T., Youn, Ji-Young, Samavarchi-Tehrani, Payman, Zhang, Hui, Zhu, Lucie Y., Popiel, Evelyn, Lambert, Jean-Philippe, Coyaud, Étienne, Cheung, Sally W. T., Rajendran, Dushyandi, Wong, Cassandra J., Antonicka, Hana, Pelletier, Laurence, Palazzo, Alexander F., Shoubridge, Eric A., Raught, Brian, Gingras, Anne-Claude

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Human GTPBP5 (MTG2) fuels mitoribosome large subunit maturation by facilitating 16S rRNA methylation von Maiti, Priyanka, Antonicka, Hana, Gingras, Anne-Claude, Shoubridge, Eric A, Barrientos, Antoni

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Mitochondrial disease therapy from thin air? von Shoubridge, Eric A.

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Biomedicine: Replacing the cell's power plants von Shoubridge, Eric A

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SPTLC1 variants associated with ALS produce distinct sphingolipid signatures through impaired interaction with ORMDL proteins von Lone, Museer A, Aaltonen, Mari J, Zidell, Aliza, Pedro, Helio F, Morales Saute, Jonas A, Mathew, Shalett, Mohassel, Payam, Bönnemann, Carsten G, Shoubridge, Eric A, Hornemann, Thorsten

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Replacing the cell's power plants von Shoubridge, Eric A.

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