Brainstem development requires galactosylceramidase and is critical for pathogenesis in a model of Krabbe disease von Weinstock, Nadav I., Kreher, Conlan, Favret, Jacob, Nguyen, Duc, Bongarzone, Ernesto R., Wrabetz, Lawrence, Feltri, M. Laura, Shin, Daesung

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Neuron-specific ablation of the Krabbe disease gene galactosylceramidase in mice results in neurodegeneration von Kreher, Conlan, Favret, Jacob, Weinstock, Nadav I, Maulik, Malabika, Hong, Xinying, Gelb, Michael H, Wrabetz, Lawrence, Feltri, M Laura, Shin, Daesung

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Ablation of lipocalin-2 reduces neuroinflammation in a mouse model of Krabbe disease von Favret, Jacob, Maulik, Malabika, Masoom, Rayan, Kushwaha, Meghana, Thompson, Devin, Browne, Richard, Shin, Daesung

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Dicer ablation in oligodendrocytes provokes neuronal impairment in mice von Shin, Daesung, Shin, Ji-Yeon, McManus, Michael T., Ptáček, Louis J., Fu, Ying-Hui

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Lysosomal Functions in Glia Associated with Neurodegeneration von Kreher, Conlan, Favret, Jacob, Maulik, Malabika, Shin, Daesung

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Macrophages Expressing GALC Improve Peripheral Krabbe Disease by a Mechanism Independent of Cross-Correction von Weinstock, Nadav I., Shin, Daesung, Dhimal, Narayan, Hong, Xinying, Irons, Eric E., Silvestri, Nicholas J., Reed, Chelsey B., Nguyen, Duc, Sampson, Oliver, Cheng, Yung-Chih, Lau, Joseph T.Y., Bongarzone, Ernesto R., Kofler, Julia, Escolar, Maria L., Gelb, Michael H., Wrabetz, Lawrence, Feltri, M. Laura

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Very large G protein-coupled receptor 1 regulates myelin-associated glycoprotein via Gαs/Gαq-mediated protein kinases A/C von Shin, Daesung, Lin, Shu-Ting, Fu, Ying-Hui, Ptáček, Louis J.

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Pre-clinical Mouse Models of Neurodegenerative Lysosomal Storage Diseases von Favret, Jacob M, Weinstock, Nadav I, Feltri, M Laura, Shin, Daesung

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Dissecting the role of oligodendroglial NFkB signaling in the pathogenesis of Krabbe disease von Favret, Jacob, Kushawa, Meghana, Shin, Daesung

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Exploring the death and signaling of galactosylceramidase-deficient oligodendrocytes von Kushwaha, Meghana, Bhagavatula, Anjali, Favret, Jacob, Shin, Daesung

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Perinatal loss of galactosylceramidase in both oligodendrocytes and microglia is crucial for the pathogenesis of Krabbe disease in mice von Favret, Jacob, Nawaz, Mohammed Haseeb, Patel, Mayuri, Khaledi, Hamid, Gelb, Michael, Shin, Daesung

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Mechanisms of demyelination and neurodegeneration in globoid cell leukodystrophy von Feltri, M. Laura, Weinstock, Nadav I., Favret, Jacob, Dhimal, Narayan, Wrabetz, Lawrence, Shin, Daesung

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Altered Trafficking and Processing of GALC Mutants Correlates with Globoid Cell Leukodystrophy Severity von Shin, Daesung, Feltri, M Laura, Wrabetz, Lawrence

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N-terminal Extension of Canine Glutamine Synthetase Created by Splicing Alters Its Enzymatic Property von Shin, Daesung, Park, Chankyu

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Ribose Utilization with an Excess of Mutarotase Causes Cell Death Due to Accumulation of Methylglyoxal von KIM, Insook, KIM, Eunjung, YOO, Seokho, SHIN, Daesung, MIN, Bumchan, SONG, Jeeyeon, PARK, Chankyu

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Temporal Galc deletion reveals a critical vulnerable period in the pathogenesis of Krabbe leukodystrophy von Shin, Daesung, Weinstock, Nadav, Feltri, Laura, Wrabetz, Lawrence

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Metabolic profiling reveals biochemical pathways and potential biomarkers associated with the pathogenesis of K rabbe disease von Weinstock, Nadav I., Wrabetz, Lawrence, Feltri, M. Laura, Shin, Daesung

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Metabolic profiling reveals biochemical pathways and potential biomarkers associated with the pathogenesis of Krabbe disease von Weinstock, Nadav I., Wrabetz, Lawrence, Feltri, M. Laura, Shin, Daesung

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Galc ablation in Schwann cells produces a demyelinating peripheral neuropathy characterized by psychosine formation but lacking globoid cells von Weinstock, Nadav I., Shin, Daesung, Bongarzone, Ernesto R., Nguyen, Duc, Silvestri, Nicholas J., Wrabetz, Lawrence, Laura Feltri, M.

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miR-32 and its target SLC45A3 regulate the lipid metabolism of oligodendrocytes and myelin von Shin, D, Howng, S.Y.B, Ptáček, L.J, Fu, Y.-H

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