X-linked dilated cardiomyopathy with neutropenia, growth retardation, and 3-methylglutaconic aciduria von Kelley, Richard I., Cheatham, John P., Clark, Bernard J., Nigro, Michael A., Powell, Berkley R., Sherwood, Geoffrey W., Sladky, John T., Swisher, William P.

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Long-chain L-3-hydroxyacyl-coenzyme A dehydrogenase deficiency neuropathy : Response to cod liver oil von TEIN, I, VAJSAR, J, MACMILLAN, L, SHERWOOD, W. G

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Pancreatitis in patients with organic acidemias von Kahler, Stephen G., Sherwood, W.Geoffrey, Woolf, David, Lawless, Stephen T., Zaritsky, Arno, Bonham, James, Taylor, C.J., Clarke, Joe T.R., Durie, Peter, Leonard, James V.

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Variable clinical presentation in patients with defective E1 component of pyruvate dehydrogenase complex von ROBINSON, B. H, MACMILLAN, H, PETROVA-BENEDICT, R, SHERWOOD, W. G

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Phenotypic heterogeneity in the syndromes of 3-methylglutaconic aciduria von Gibson, K.M., Sherwood, W.G., Hoffmann, G.F., Stumpf, D.A., Dianzanl, I., Schutgens, R.B.H., Barth, P.G., Weismann, U., Bachmann, C., Schrynemackers-Pitance, P., Verloes, A., Narisawa, K., Mino, M., Ohya, N., Kelley, R.I.

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Secondary 3‐hydroxydicarboxylic aciduria mimicking long‐chain 3‐hydroxyacyl‐CoA dehydrogenase deficiency von Bennett, M. J., Weinberger, M. J., Sherwood, W. G., Burlina, A. B.

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Reliable prenatal diagnosis of Canavan disease (aspartoacylase deficiency): Comparison of enzymatic and metabolite analysis von Bennett, M. J., Gibson, K. M., Sherwood, W. G., Divry, P., Rolland, M. O., Elpeleg, O. N., Rinaldo, P., Jakobs, C.

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Fetal Polycystic Kidney Disease Associated with Glutaric Aciduria Type II: An Inborn Error of Energy Metabolism von Whitfield, Jonathan, Hurst, David, Bennett, Michael J., Sherwood, W. Geoff, Hogg, Ronald, Gonsoulin, Whitney

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Secondary inhibition of multiple NAD‐requiring dehydrogenases in respiratory chain complex I deficiency: Possible metabolic markers for the primary defect von Bennett, M. J., Sherwood, W. G., Gibson, K. M., Burlina, A. B.

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Lactic acidaemia von Robinson, B. H., Sherwood, W. G.

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The genetic heterogeneity of lactic acidosis: occurrence of recognizable inborn errors of metabolism in pediatric population with lactic acidosis von Robinson, B H, Taylor, J, Sherwood, W G

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Cardiac manifestations in disorders of fat and carnitine metabolism in infancy von Ino, Toshihiro, Sherwood, W.Geoffrey, Benson, Lee N., Wilson, Gregory J., Freedom, Robert M., Rowe, Richard D.

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The molecular basis for the two different clinical presentations of classical pyruvate carboxylase deficiency von ROBINSON, B. H, ŒI, J, SHERWOOD, W. G, APPLEGARTH, D, WONG, L, HAWORTH, J, GOODYER, P, CASEY, R, ZALESKI, L. A

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Dilated cardiomyopathy with neutropenia, short stature, and abnormal carnitine metabolism von Ino, Toshihiro, Sherwood, W. Geoffrey, Cutz, Ernest, Benson, Lee N., Rose, Vera, Freedom, Robert M.

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Deficiency of dihydrolipoyl dehydrogenase (a component of the pyruvate and alpha-ketoglutarate dehydrogenase complexes): a cause of congenital chronic lactic acidosis in infancy von Robinson, B H, Taylor, J, Sherwood, W G

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Partial biotinidase deficiency associated with Coffin-Siris syndrome von Burlina, A B, Sherwood, W G, Zacchello, F

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Neonatal screening for biotinidase deficiency in north eastern Italy von BURLINA, A. B, SHERWOOD, W. G, MARCHIORO, M. V, DALLA BERNARDINA, B, GABURRO, D

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Evidence for a defect of holocarboxylase synthetase activity in cultured lymphoblasts from a patient with biotin-responsive multiple carboxylase deficiency von Saunders, M E, Sherwood, W G, Duthie, M, Surh, L, Gravel, R A

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A Rotating Ring‐Disk Electrode Study of the Underpotential Deposition of Mercury on Gold von Sherwood, W. G., Bruckenstein, Stanley

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Pyruvate dehydrogenase phosphatase deficiency: a cause of congenital chronic lactic acidosis in infancy von Robinson, B H, Sherwood, W G

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