Novel Model of Tendon Regeneration Reveals Distinct Cell Mechanisms Underlying Regenerative and Fibrotic Tendon Healing von Howell, Kristen, Chien, Chun, Bell, Rebecca, Laudier, Damien, Tufa, Sara F., Keene, Douglas R., Andarawis-Puri, Nelly, Huang, Alice H.

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In vivo topical gene therapy for recessive dystrophic epidermolysis bullosa: a phase 1 and 2 trial von Gurevich, Irina, Agarwal, Pooja, Zhang, PeiPei, Dolorito, John A., Oliver, Stacie, Liu, Henry, Reitze, Nicholas, Sarma, Nikhil, Bagci, Isin Sinem, Sridhar, Kunju, Kakarla, Visesha, Yenamandra, Vamsi K., O’Malley, Mark, Prisco, Marco, Tufa, Sara F., Keene, Douglas R., South, Andrew P., Krishnan, Suma M., Marinkovich, M. Peter

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Creation and characterization of novel rat model for recessive dystrophic epidermolysis bullosa: Frameshift mutation of the Col7a1 gene leads to severe blistered phenotype von Stone, William, Strege, Chloe, Miller, William, Geurts, Aron M, Grzybowski, Michael, Riddle, Megan, Lees, Christopher, Eide, Cindy, Keene, Douglas R, Tufa, Sara F, Seelig, Davis, McGrath, John, Tolar, Jakub

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The Fraser Complex Proteins (Frem1, Frem2, and Fras1) Can Form Anchoring Cords in the Absence of AMACO at the Dermal-Epidermal Junction of Mouse Skin von Esho, Temitope, Kobbe, Birgit, Tufa, Sara F, Keene, Douglas R, Paulsson, Mats, Wagener, Raimund

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QR-313, an Antisense Oligonucleotide, Shows Therapeutic Efficacy for Treatment of Dominant and Recessive Dystrophic Epidermolysis Bullosa: A Preclinical Study von Bornert, Olivier, Hogervorst, Marieke, Nauroy, Pauline, Bischof, Johannes, Swildens, Jim, Athanasiou, Ioannis, Tufa, Sara F., Keene, Douglas R., Kiritsi, Dimitra, Hainzl, Stefan, Murauer, Eva M., Marinkovich, M. Peter, Platenburg, Gerard, Hausser, Ingrid, Wally, Verena, Ritsema, Tita, Koller, Ulrich, Haisma, Elisabeth M., Nyström, Alexander

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Tgfβ signaling is critical for maintenance of the tendon cell fate von Tan, Guak-Kim, Pryce, Brian A, Stabio, Anna, Brigande, John V, Wang, ChaoJie, Xia, Zheng, Tufa, Sara F, Keene, Douglas R, Schweitzer, Ronen

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Abnormal Activation of BMP Signaling Causes Myopathy in Fbn2 Null Mice von Sengle, Gerhard, Carlberg, Valerie, Tufa, Sara F, Charbonneau, Noe L, Smaldone, Silvia, Carlson, Eric J, Ramirez, Francesco, Keene, Douglas R, Sakai, Lynn Y

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Loss of Smad4 in the scleraxis cell lineage results in postnatal joint contracture von Schlesinger, Saundra Y., Seo, Seongkyung, Pryce, Brian A., Tufa, Sara F., Keene, Douglas R., Huang, Alice H., Schweitzer, Ronen

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Musculoskeletal integration at the wrist underlies the modular development of limb tendons von Huang, Alice H, Riordan, Timothy J, Pryce, Brian, Weibel, Jennifer L, Watson, Spencer S, Long, Fanxin, Lefebvre, Veronique, Harfe, Brian D, Stadler, H Scott, Akiyama, Haruhiko, Tufa, Sara F, Keene, Douglas R, Schweitzer, Ronen

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New insights into the structural role of EMILINs within the human skin microenvironment von Schiavinato, Alvise, Marcous, Fady, Zuk, Alexandra V., Keene, Douglas R., Tufa, Sara F., Mosquera, Laura M., Zigrino, Paola, Mauch, Cornelia, Eckes, Beate, Francois, Katrien, De Backer, Julie, Hunzelmann, Nicolas, Moinzadeh, Pia, Krieg, Thomas, Callewaert, Bert, Sengle, Gerhard

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Characterization of TGFβ1-induced tendon-like structure in the scaffold-free three-dimensional tendon cell culture system von Koo, Bon-hyeock, Lee, Yeon-Ju, Park, Na Rae, Heo, Su Chin, Hudson, David M., Fernandes, Aysel A., Friday, Chet S., Hast, Michael W., Corr, David T., Keene, Douglas R., Tufa, Sara F., Dyment, Nathaniel A., Joeng, Kyu Sang

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Microenvironmental regulation by fibrillin-1 von Sengle, Gerhard, Tsutsui, Ko, Keene, Douglas R, Tufa, Sara F, Carlson, Eric J, Charbonneau, Noe L, Ono, Robert N, Sasaki, Takako, Wirtz, Mary K, Samples, John R, Fessler, Liselotte I, Fessler, John H, Sekiguchi, Kiyotoshi, Hayflick, Susan J, Sakai, Lynn Y

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Tendon and motor phenotypes in the Crtap -/- mouse model of recessive osteogenesis imperfecta von Grol, Matthew William, Haelterman, Nele A, Lim, Joohyun, Munivez, Elda M, Archer, Marilyn, Hudson, David M, Tufa, Sara F, Keene, Douglas R, Lei, Kevin, Park, Dongsu, Kuzawa, Cole D, Ambrose, Catherine G, Eyre, David R, Lee, Brendan H

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Anchoring Cords: A Distinct Suprastructure in the Developing Skin von Esho, Temitope, Tufa, Sara F., Kobbe, Birgit, Wohl, Alexander P., Sengle, Gerhard, Paulsson, Mats, Keene, Douglas R., Wagener, Raimund

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Elevated TGFβ signaling contributes to ocular anterior segment dysgenesis in Col4a1 mutant mice von Mao, Mao, Labelle-Dumais, Cassandre, Tufa, Sara F., Keene, Douglas R., Gould, Douglas B.

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Connective Tissue Ultrastructure: A Direct Comparison between Conventional Specimen Preparation and High‐Pressure Freezing/Freeze‐Substitution von Keene, Douglas R., Tufa, Sara F.

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Thicker Sections (300-500 nm) Observed in the Conventional TEM May Reveal Extended Structures Not Recognized in Ultrathin Sections von Keene, Douglas R., Tufa, Sara F.

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Lysyl hydroxylase 3–mediated post-translational modifications are required for proper biosynthesis of collagen α1α1α2(IV) von Ishikawa, Yoshihiro, Taga, Yuki, Coste, Thibault, Tufa, Sara F., Keene, Douglas R., Mizuno, Kazunori, Tournier-Lasserve, Elisabeth, Gould, Douglas B.

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Type I and type V procollagen triple helix uses different subsets of the molecular ensemble for lysine posttranslational modifications in the rER von Ishikawa, Yoshihiro, Taga, Yuki, Zientek, Keith, Mizuno, Nobuyo, Salo, Antti M., Semenova, Olesya, Tufa, Sara F., Keene, Douglas R., Holden, Paul, Mizuno, Kazunori, Gould, Douglas B., Myllyharju, Johanna, Bächinger, Hans Peter

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Unraveling the role of TGFβ signaling in thoracic aortic aneurysm and dissection using Fbn1 mutant mouse models von Deleeuw, Violette, Carlson, Eric, Renard, Marjolijn, Zientek, Keith D., Wilmarth, Phillip A., Reddy, Ashok P., Manalo, Elise C., Tufa, Sara F., Keene, Douglas R., Olbinado, Margie, Stampanoni, Marco, Kanki, Sachiko, Yanagisawa, Hiromi, Mosquera, Laura Muiño, Sips, Patrick, De Backer, Julie, Sakai, Lynn Y.

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