Imbalanced OPA1 processing and mitochondrial fragmentation cause heart failure in mice von Wai, Timothy, García-Prieto, Jaime, Baker, Michael J, Merkwirth, Carsten, Benit, Paule, Rustin, Pierre, Rupérez, Francisco Javier, Barbas, Coral, Ibañez, Borja, Langer, Thomas

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Mitochondria are physiologically maintained at close to 50 °C von Chrétien, Dominique, Bénit, Paule, Ha, Hyung-Ho, Keipert, Susanne, El-Khoury, Riyad, Chang, Young-Tae, Jastroch, Martin, Jacobs, Howard T, Rustin, Pierre, Rak, Malgorzata

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SDH Mutations Establish a Hypermethylator Phenotype in Paraganglioma von Letouzé, Eric, Martinelli, Cosimo, Loriot, Céline, Burnichon, Nelly, Abermil, Nasséra, Ottolenghi, Chris, Janin, Maxime, Menara, Mélanie, Nguyen, An Thach, Benit, Paule, Buffet, Alexandre, Marcaillou, Charles, Bertherat, Jérôme, Amar, Laurence, Rustin, Pierre, De Reyniès, Aurélien, Gimenez-Roqueplo, Anne-Paule, Favier, Judith

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Evolutionarily conserved susceptibility of the mitochondrial respiratory chain to SDHI pesticides and its consequence on the impact of SDHIs on human cultured cells von Bénit, Paule, Kahn, Agathe, Chretien, Dominique, Bortoli, Sylvie, Huc, Laurence, Schiff, Manuel, Gimenez-Roqueplo, Anne-Paule, Favier, Judith, Gressens, Pierre, Rak, Malgorzata, Rustin, Pierre

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Spermidine and resveratrol induce autophagy by distinct pathways converging on the acetylproteome von Morselli, Eugenia, Mariño, Guillermo, Bennetzen, Martin V, Eisenberg, Tobias, Megalou, Evgenia, Schroeder, Sabrina, Cabrera, Sandra, Bénit, Paule, Rustin, Pierre, Criollo, Alfredo, Kepp, Oliver, Galluzzi, Lorenzo, Shen, Shensi, Malik, Shoaib Ahmad, Maiuri, Maria Chiara, Horio, Yoshiyuki, López-Otín, Carlos, Andersen, Jens S, Tavernarakis, Nektarios, Madeo, Frank, Kroemer, Guido

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A critical approach to the therapy of mitochondrial respiratory chain and oxidative phosphorylation diseases von DiMauro, Salvatore, Rustin, Pierre

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CHCHD2 accumulates in distressed mitochondria and facilitates oligomerization of CHCHD10 von Huang, Xiaoping, Wu, Beverly P, Nguyen, Diana, Liu, Yi-Ting, Marani, Melika, Hench, Jürgen, Bénit, Paule, Kozjak-Pavlovic, Vera, Rustin, Pierre, Frank, Stephan, Narendra, Derek P

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Defects in succinate dehydrogenase in gastrointestinal stromal tumors lacking KIT and PDGFRA mutations von Janeway, Katherine A, Kim, Su Young, Lodish, Maya, Nosé, Vânia, Rustin, Pierre, Gaal, José, Dahia, Patricia L.M, Liegl, Bernadette, Ball, Evan R, Raygada, Margarita, Lai, Angela H, Kelly, Lorna, Hornick, Jason L, O'Sullivan, Maureen, de Krijger, Ronald R, Dinjens, Winand N.M, Demetri, George D, Antonescu, Cristina R, Fletcher, Jonathan A, Helman, Lee, Stratakis, Constantine A

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Genetic and biochemical intricacy shapes mitochondrial cytopathies von Turnbull, Douglass M, Rustin, Pierre

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Interaction between AIF and CHCHD4 Regulates Respiratory Chain Biogenesis von Hangen, Emilie, Féraud, Olivier, Lachkar, Sylvie, Mou, Haiwei, Doti, Nunzianna, Fimia, Gian Maria, Lam, Ngoc-vy, Zhu, Changlian, Godin, Isabelle, Muller, Kevin, Chatzi, Afroditi, Nuebel, Esther, Ciccosanti, Fabiola, Flamant, Stéphane, Bénit, Paule, Perfettini, Jean-Luc, Sauvat, Allan, Bennaceur-Griscelli, Annelise, Ser-Le Roux, Karine, Gonin, Patrick, Tokatlidis, Kostas, Rustin, Pierre, Piacentini, Mauro, Ruvo, Menotti, Blomgren, Klas, Kroemer, Guido, Modjtahedi, Nazanine

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PGC-1α is dispensable for exercise-induced mitochondrial biogenesis in skeletal muscle von Rowe, Glenn C, El-Khoury, Riyad, Patten, Ian S, Rustin, Pierre, Arany, Zolt

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Acute and chronic mitochondrial respiratory chain deficiency differentially regulate lysosomal biogenesis von Fernández-Mosquera, Lorena, Diogo, Cátia V., Yambire, King Faisal, Santos, Gabriela L., Luna Sánchez, Marta, Bénit, Paule, Rustin, Pierre, Lopez, Luis Carlos, Milosevic, Ira, Raimundo, Nuno

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SLC25A32 Mutations and Riboflavin-Responsive Exercise Intolerance von Schiff, Manuel, Veauville-Merllié, Alice, Su, Chen Hsien, Tzagoloff, Alexander, Rak, Malgorzata, Ogier de Baulny, Hélène, Boutron, Audrey, Smedts-Walters, Hélène, Romero, Norma B, Rigal, Odile, Rustin, Pierre, Vianey-Saban, Christine, Acquaviva-Bourdain, Cécile

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Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia von Paupe, Vincent, Dassa, Emmanuel P, Goncalves, Sergio, Auchère, Françoise, Lönn, Maria, Holmgren, Arne, Rustin, Pierre

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Respiratory-chain diseases related to complex III deficiency von Bénit, Paule, Lebon, Sophie, Rustin, Pierre

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The Warburg effect is genetically determined in inherited pheochromocytomas von Favier, Judith, Brière, Jean-Jacques, Burnichon, Nelly, Rivière, Julie, Vescovo, Laure, Benit, Paule, Giscos-Douriez, Isabelle, De Reyniès, Aurélien, Bertherat, Jérôme, Badoual, Cécile, Tissier, Frédérique, Amar, Laurence, Libé, Rosella, Plouin, Pierre-François, Jeunemaitre, Xavier, Rustin, Pierre, Gimenez-Roqueplo, Anne-Paule

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Mitochondrial temperature homeostasis resists external metabolic stresses von Terzioglu, Mügen, Veeroja, Kristo, Montonen, Toni, Ihalainen, Teemu O, Salminen, Tiina S, Bénit, Paule, Rustin, Pierre, Chang, Young-Tae, Nagai, Takeharu, Jacobs, Howard T

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Alternative oxidase expression in the mouse enables bypassing cytochrome c oxidase blockade and limits mitochondrial ROS overproduction von El-Khoury, Riyad, Dufour, Eric, Rak, Malgorzata, Ramanantsoa, Nelina, Grandchamp, Nicolas, Csaba, Zsolt, Duvillié, Bertrand, Bénit, Paule, Gallego, Jorge, Gressens, Pierre, Sarkis, Chamsy, Jacobs, Howard T, Rustin, Pierre

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Targeted Deletion of AIF Decreases Mitochondrial Oxidative Phosphorylation and Protects from Obesity and Diabetes von Pospisilik, J. Andrew, Knauf, Claude, Joza, Nicholas, Benit, Paule, Orthofer, Michael, Cani, Patrice D., Ebersberger, Ingo, Nakashima, Tomoki, Sarao, Renu, Neely, Gregory, Esterbauer, Harald, Kozlov, Andrey, Kahn, C. Ronald, Kroemer, Guido, Rustin, Pierre, Burcelin, Remy, Penninger, Josef M.

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Author Correction: miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy von Sanson, Mathilde, Vu Hong, Ai, Massourides, Emmanuelle, Bourg, Nathalie, Suel, Laurence, Amor, Fatima, Corre, Guillaume, Bénit, Paule, Barthelemy, Inès, Blot, Stephane, Bigot, Anne, Pinset, Christian, Rustin, Pierre, Servais, Laurent, Voit, Thomas, Richard, Isabelle, Israeli, David

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