miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy von Sanson, Mathilde, Vu Hong, Ai, Massourides, Emmanuelle, Bourg, Nathalie, Suel, Laurence, Amor, Fatima, Corre, Guillaume, Bénit, Paule, Barthelemy, Inès, Blot, Stephane, Bigot, Anne, Pinset, Christian, Rustin, Pierre, Servais, Laurent, Voit, Thomas, Richard, Isabelle, Israeli, David

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BH3 mimetics activate multiple pro-autophagic pathways von Malik, S A, Orhon, I, Morselli, E, Criollo, A, Shen, S, Mariño, G, BenYounes, A, Bénit, P, Rustin, P, Maiuri, M C, Kroemer, G

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Accumulation of Krebs cycle intermediates and over-expression of HIF1α in tumours which result from germline FH and SDH mutations von Pollard, P.J., Brière, J.J., Alam, N.A., Barwell, J., Barclay, E., Wortham, N.C., Hunt, T., Mitchell, M., Olpin, S., Moat, S.J., Hargreaves, I.P., Heales, S.J., Chung, Y.L., Griffiths, J.R., Dalgleish, A., McGrath, J.A., Gleeson, M.J., Hodgson, S.V., Poulsom, R., Rustin, P., Tomlinson, I.P.M.

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The R22X Mutation of the SDHD Gene in Hereditary Paraganglioma Abolishes the Enzymatic Activity of Complex II in the Mitochondrial Respiratory Chain and Activates the Hypoxia Pathw... von Gimenez-Roqueplo, Anne-Paule, Favier, Judith, Rustin, Pierre, Mourad, Jean-Jacques, Plouin, Pierre-François, Corvol, Pierre, Rötig, Agnès, Jeunemaitre, Xavier

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Pro-oxidant/antioxidant balance controls pancreatic β-cell differentiation through the ERK1/2 pathway von Hoarau, E, Chandra, V, Rustin, P, Scharfmann, R, Duvillie, B

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Effect of idebenone on cardiomyopathy in Friedreich's ataxia: a preliminary study von Rustin, Pierre, von Kleist-Retzow, Jürgen-Christoph, Chantrel-Groussard, Karine, Sidi, Daniel, Munnich, Arnold, Rötig, Agnès

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HIV-1 Tat protein directly induces mitochondrial membrane permeabilization and inactivates cytochrome c oxidase von Lecoeur, H, Borgne-Sanchez, A, Chaloin, O, El-Khoury, R, Brabant, M, Langonné, A, Porceddu, M, Brière, J-J, Buron, N, Rebouillat, D, Péchoux, C, Deniaud, A, Brenner, C, Briand, J-P, Muller, S, Rustin, P, Jacotot, E

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A brain-specific isoform of mitochondrial apoptosis-inducing factor: AIF2 von Hangen, E, De Zio, D, Bordi, M, Zhu, C, Dessen, P, Caffin, F, Lachkar, S, Perfettini, J-L, Lazar, V, Benard, J, Fimia, G M, Piacentini, M, Harper, F, Pierron, G, Vicencio, J M, Bénit, P, de Andrade, A, Höglinger, G, Culmsee, C, Rustin, P, Blomgren, K, Cecconi, F, Kroemer, G, Modjtahedi, N

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Idebenone and reduced cardiac hypertrophy in Friedreich's ataxia von Hausse, A O, Aggoun, Y, Bonnet, D, Sidi, D, Munnich, A, Rötig, A, Rustin, P

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Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia von Seznec, Hervé, Simon, Delphine, Monassier, Laurent, Criqui-Filipe, Paola, Gansmuller, Anne, Rustin, Pierre, Koenig, Michel, Puccio, Hélène

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Mutant NDUFS3 subunit of mitochondrial complex I causes Leigh syndrome von Bénit, P, Slama, A, Cartault, F, Giurgea, I, Chretien, D, Lebon, S, Marsac, C, Munnich, A, Rötig, A, Rustin, P

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Imbalanced OPA1 processing and mitochondrial fragmentation cause heart failure in mice von Wai, Timothy, García-Prieto, Jaime, Baker, Michael J, Merkwirth, Carsten, Benit, Paule, Rustin, Pierre, Rupérez, Francisco Javier, Barbas, Coral, Ibañez, Borja, Langer, Thomas

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Invasive Haemaphysalis longicornis (Acari: Ixodidae) investigation in South Carolina: new records of establishment, pathogen prevalence, and blood meal analyses von Dye-Braumuller, Kyndall C., Gual-Gonzalez, Lídia, Abiodun, Titi, Rustin, Lauren P., Evans, Chris L., Meyer, Madeleine M., Zellars, Kia, Neault, Mike J., Nolan, Melissa S.

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Biochemical and molecular investigations in respiratory chain deficiencies von Rustin, P., Chretien, D., Bourgeron, T., Gérard, B., Rötig, A., Saudubray, J.M., Munnich, A.

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Succinate dehydrogenase deficiency in human von Brière, J-J, Favier, J, El Ghouzzi, V, Djouadi, F, Bénit, P, Gimenez, A-P, Rustin, P

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Long-term Follow-up of Neonatal Mitochondrial Cytopathies: A Study of 57 Patients von Garcia-Cazorla, A, De Lonlay, P, Nassogne, M.C, Rustin, P, Touati, G, Saudubray, J.M

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Recurrent de novo mitochondrial DNA mutations in respiratory chain deficiency von Lebon, S, Chol, M, Benit, P, Mugnier, C, Chretien, D, Giurgea, I, Kern, I, Girardin, E, Hertz-Pannier, L, de Lonlay, P, Rötig, A, Rustin, P, Munnich, A

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Coenzyme Q(10) and idebenone in the therapy of respiratory chain diseases: rationale and comparative benefits von Geromel, Vanna, Darin, Niklas, Chrétien, Dominique, Bénit, Paule, DeLonlay, Pascale, Rötig, Agnès, Munnich, Arnold, Rustin, Pierre

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The mitochondrial DNA G13513A MELAS mutation in the NADH dehydrogenase 5 gene is a frequent cause of Leigh-like syndrome with isolated complex I deficiency von Chol, M, Lebon, S, Bénit, P, Chretien, D, de Lonlay, P, Goldenberg, A, Odent, S, Hertz-Pannier, L, Vincent-Delorme, C, Cormier-Daire, V, Rustin, P, Rötig, A, Munnich, A

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The molecular archaeology of a mitochondrial death effector: AIF in Drosophila von Joza, N, Galindo, K, Pospisilik, J A, Benit, P, Rangachari, M, Kanitz, E E, Nakashima, Y, Neely, G G, Rustin, P, Abrams, J M, Kroemer, G, Penninger, J M

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