Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly von Rackham, Oliver, Busch, Jakob D., Matic, Stanka, Siira, Stefan J., Kuznetsova, Irina, Atanassov, Ilian, Ermer, Judith A., Shearwood, Anne-Marie J., Richman, Tara R., Stewart, James B., Mourier, Arnaud, Milenkovic, Dusanka, Larsson, Nils-Göran, Filipovska, Aleksandra

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Biallelic Mutations in MRPS34 Lead to Instability of the Small Mitoribosomal Subunit and Leigh Syndrome von Lake, Nicole J., Webb, Bryn D., Stroud, David A., Richman, Tara R., Ruzzenente, Benedetta, Compton, Alison G., Mountford, Hayley S., Pulman, Juliette, Zangarelli, Coralie, Rio, Marlene, Boddaert, Nathalie, Assouline, Zahra, Sherpa, Mingma D., Schadt, Eric E., Houten, Sander M., Byrnes, James, McCormick, Elizabeth M., Zolkipli-Cunningham, Zarazuela, Haude, Katrina, Zhang, Zhancheng, Retterer, Kyle, Bai, Renkui, Calvo, Sarah E., Mootha, Vamsi K., Christodoulou, John, Rötig, Agnes, Filipovska, Aleksandra, Cristian, Ingrid, Falk, Marni J., Metodiev, Metodi D., Thorburn, David R.

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Loss of the RNA-binding protein TACO1 causes late-onset mitochondrial dysfunction in mice von Richman, Tara R., Spåhr, Henrik, Ermer, Judith A., Davies, Stefan M. K., Viola, Helena M., Bates, Kristyn A., Papadimitriou, John, Hool, Livia C., Rodger, Jennifer, Larsson, Nils-Göran, Rackham, Oliver, Filipovska, Aleksandra

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Mitochondrial gene expression is required for platelet function and blood clotting von Richman, Tara R., Ermer, Judith A., Baker, Jessica, Siira, Stefan J., Kile, Benjamin T., Linden, Matthew D., Rackham, Oliver, Filipovska, Aleksandra

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RNA processing in human mitochondria von Lopez Sanchez, Maria I.G., Mercer, Tim R., Davies, Stefan M.K., Shearwood, Anne-Marie J., Nygård, Karoline K.A., Richman, Tara R., Mattick, John S., Rackham, Oliver, Filipovska, Aleksandra

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Tighter Ligand Binding Can Compensate for Impaired Stability of an RNA-Binding Protein von Wallis, Christopher P, Richman, Tara R, Filipovska, Aleksandra, Rackham, Oliver

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Evidence for age-related and individual-specific changes in DNA methylation profile of mononuclear cells during early immune development in humans von Martino, David J., Tulic, Meri K., Gordon, Lavinia, Hodder, Megan, Richman, Tara R., Metcalfe, Jessica, Prescott, Susan L., Saffery, Richard

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Mutation in MRPS34 compromises protein synthesis and causes mitochondrial dysfunction von Richman, Tara R, Ermer, Judith A, Davies, Stefan M K, Perks, Kara L, Viola, Helena M, Shearwood, Anne-Marie J, Hool, Livia C, Rackham, Oliver, Filipovska, Aleksandra

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Concerted regulation of mitochondrial and nuclear non‐coding RNAs by a dual‐targeted RNase Z von Siira, Stefan J, Rossetti, Giulia, Richman, Tara R, Perks, Kara, Ermer, Judith A, Kuznetsova, Irina, Hughes, Laetitia, Shearwood, Anne‐Marie J, Viola, Helena M, Hool, Livia C, Rackham, Oliver, Filipovska, Aleksandra

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Mitochondria: Unusual features of the mammalian mitoribosome von Richman, Tara R., Rackham, Oliver, Filipovska, Aleksandra

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Mitochondrial mistranslation modulated by metabolic stress causes cardiovascular disease and reduced lifespan von Richman, Tara R., Ermer, Judith A., Siira, Stefan J., Kuznetsova, Irina, Brosnan, Christopher A., Rossetti, Giulia, Baker, Jessica, Perks, Kara L., Cserne Szappanos, Henrietta, Viola, Helena M., Gray, Nicola, Larance, Mark, Hool, Livia C., Zuryn, Steven, Rackham, Oliver, Filipovska, Aleksandra

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Stress signaling and cellular proliferation reverse the effects of mitochondrial mistranslation von Ferreira, Nicola, Perks, Kara L, Rossetti, Giulia, Rudler, Danielle L, Hughes, Laetitia A, Ermer, Judith A, Scott, Louis H, Kuznetsova, Irina, Richman, Tara R, Narayana, Vinod K, Abudulai, Laila N, Shearwood, Anne‐Marie J, Cserne Szappanos, Henrietta, Tull, Dedreia, Yeoh, George C, Hool, Livia C, Filipovska, Aleksandra, Rackham, Oliver

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Fidelity of translation initiation is required for coordinated respiratory complex assembly von Rudler, Danielle L, Hughes, Laetitia A, Perks, Kara L, Richman, Tara R, Kuznetsova, Irina, Ermer, Judith A, Abudulai, Laila N, Shearwood, Anne-Marie J, Viola, Helena M, Hool, Livia C, Siira, Stefan J, Rackham, Oliver, Filipovska, Aleksandra

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Reduced mitochondrial translation prevents diet-induced metabolic dysfunction but not inflammation von Perks, Kara L., Ferreira, Nicola, Ermer, Judith A., Rudler, Danielle L., Richman, Tara R., Rossetti, Giulia, Matthews, Vance B., Ward, Natalie C., Rackham, Oliver, Filipovska, Aleksandra

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The Role of the L-Type Ca2+ Channel in Altered Metabolic Activity in a Murine Model of Hypertrophic Cardiomyopathy von Viola, Helena M., PhD, Johnstone, Victoria P.A., PhD, Cserne Szappanos, Henrietta, PhD, Richman, Tara R., PhD, Tsoutsman, Tatiana, PhD, Filipovska, Aleksandra, PhD, Semsarian, Christopher, MD, PhD, Seidman, Jonathan G., PhD, Seidman, Christine E., MD, PhD, Hool, Livia C., PhD

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Biallelic Mutations in MRPS34 Lead to Instability of the Small Mitoribosomal Subunit and Leigh Syndrome von Lake, Nicole J., Webb, Bryn D., Stroud, David A., Richman, Tara R., Ruzzenente, Benedetta, Compton, Alison G., Mountford, Hayley S., Pulman, Juliette, Zangarelli, Coralie, Rio, Marlene, Boddaert, Nathalie, Assouline, Zahra, Sherpa, Mingma D., Schadt, Eric E., Houten, Sander M., Byrnes, James, McCormick, Elizabeth M., Zolkipli-Cunningham, Zarazuela, Haude, Katrina, Zhang, Zhancheng, Retterer, Kyle, Bai, Renkui, Calvo, Sarah E., Mootha, Vamsi K., Christodoulou, John, Rötig, Agnes, Filipovska, Aleksandra, Cristian, Ingrid, Falk, Marni J., Metodiev, Metodi D., Thorburn, David R.

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A bifunctional protein regulates mitochondrial protein synthesis von Richman, Tara R., Davies, Stefan M.K., Shearwood, Anne-Marie J., Ermer, Judith A., Scott, Louis H., Hibbs, Moira E., Rackham, Oliver, Filipovska, Aleksandra

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A common genetic variant of a mitochondrial RNA processing enzyme predisposes to insulin resistance von Rossetti, Giulia, Ermer, Judith A., Stentenbach, Maike, Siira, Stefan J., Richman, Tara R., Milenkovic, Dusanka, Perks, Kara L., Hughes, Laetitia A., Jamieson, Emma, Xiafukaiti, Gulibaikelamu, Ward, Natalie C., Takahashi, Satoru, Gray, Nicola, Viola, Helena M., Hool, Livia C., Rackham, Oliver, Filipovska, Aleksandra

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Adult-onset obesity is triggered by impaired mitochondrial gene expression von Perks, Kara L, Ferreira, Nicola, Richman, Tara R, Ermer, Judith A, Kuznetsova, Irina, Shearwood, Anne-Marie J, Lee, Richard G, Viola, Helena M, Johnstone, Victoria P A, Matthews, Vance, Hool, Livia C, Rackham, Oliver, Filipovska, Aleksandra

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A mutation in MT-TW causes a tRNA processing defect and reduced mitochondrial function in a family with Leigh syndrome von Duff, Rachael M, Shearwood, Anne-Marie J, Ermer, Judith, Rossetti, Giulia, Gooding, Rebecca, Richman, Tara R, Balasubramaniam, Shanti, Thorburn, David R, Rackham, Oliver, Lamont, Phillipa J, Filipovska, Aleksandra

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