Pharmacological correction of long QT-linked mutations in KCNH2 (hERG) increases the trafficking of Kv11.1 channels stored in the transitional endoplasmic reticulum von Smith, Jennifer L, Reloj, Allison R, Nataraj, Parvathi S, Bartos, Daniel C, Schroder, Elizabeth A, Moss, Arthur J, Ohno, Seiko, Horie, Minoru, Anderson, Corey L, January, Craig T, Delisle, Brian P

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High-Risk Long QT Syndrome Mutations in the Kv7.1 (KCNQ1) Pore Disrupt the Molecular Basis for Rapid K+ Permeation von Burgess, Don E, Bartos, Daniel C, Reloj, Allison R, Campbell, Kenneth S, Johnson, Jonathan N, Tester, David J, Ackerman, Michael J, Fressart, Véronique, Denjoy, Isabelle, Guicheney, Pascale, Moss, Arthur J, Ohno, Seiko, Horie, Minoru, Delisle, Brian P

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Mechanistic Basis for Type 2 Long QT Syndrome Caused by KCNH2 Mutations that Disrupt Conserved Arginine Residues in the Voltage Sensor von McBride, Christie M., Smith, Ashley M., Smith, Jennifer L., Reloj, Allison R., Velasco, Ellyn J., Powell, Jonathan, Elayi, Claude S., Bartos, Daniel C., Burgess, Don E., Delisle, Brian P.

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Abstract 394: Multiple Cellular Mechanisms Underlie the Trafficking-deficient Phenotype for Kv11.1 (hERG) Mutations Linked to Long QT Syndrome von Smith, Jennifer L, Reloj, Allison R, Anderson, Corey L, January, Craig T, Delisle, Brian T

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Cellular Mechanism for the Pharmacological Correction of hERG Mutations Linked to the Long QT Syndrome von Smith, Jennifer L., Reloj, Allison R., Nataraj, Parvathi S., Bartos, Daniel C., January, Craig T., Delisle, Brian P.

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A Mutation in the Voltage-Sensor of Kv7.1 Prevents PKA Activation of IKs to Elicit Concealed Type 1 Long QT Syndrome during Stress von Bartos, Daniel C., Burgess, Don E., Reloj, Allison R., Giudicessi, John, Tester, David J., Ackerman, Michael J., Delisle, Brian P.

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Abstract 18298: Trafficking-Deficient hERG K+ Channels Linked to Long QT Syndrome are Regulated by a Quality Control Compartment in the ER von Smith, Jennifer L, Reloj, Allison R, Nataraj, Parvathi, Anderson, Corey L, January, Craig T, Delisle, Brian P

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Malignant Long QT Syndrome KCNQ1 Mutations in the Pore Disrupt the Molecular Basis for Rapid K+ Permeation von Burgess, Don E., Bartos, Daniel C., Reloj, Allison R., Campbell, Kenneth S., Johnson, Jonathan N., Tester, David J., Ackerman, Michael J., Fressart, Véronique, Denjoy, Isabelle, Guicheney, Pascale, Moss, Arthur J., Ohno, Seiko, Horie, Minoru, Delisle, Brian

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Mechanistic Basis for Type 2 Long QT Syndrome Caused by KCNH2 Mutations that Disrupt Conserved Arginine Residue in the Voltage Sensor von McBride, Christie M., Smith, Ashley M., Smith, Jennifer L., Reloj, Allison R., Velasco, Ellyn J., Powell, Jonathan, Elayi, Claude S., Bartos, Daniel C., Burgess, Don E., Delisle, Brian P.

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