The Ever-Increasing Array of Novel Inborn Errors of Immunity: an Interim Update by the IUIS Committee von Tangye, Stuart G., Al-Herz, Waleed, Bousfiha, Aziz, Cunningham-Rundles, Charlotte, Franco, Jose Luis, Holland, Steven M, Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Picard, Capucine, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C, Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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Survival of the fetus: fetal B and T cell receptor repertoire development von Rechavi, Erez, Somech, Raz

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Human Inborn Errors of Immunity: 2022 Update on the Classification from the International Union of Immunological Societies Expert Committee von Tangye, Stuart G., Al-Herz, Waleed, Bousfiha, Aziz, Cunningham-Rundles, Charlotte, Franco, Jose Luis, Holland, Steven M., Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Picard, Capucine, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C., Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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The 2022 Update of IUIS Phenotypical Classification for Human Inborn Errors of Immunity von Bousfiha, Aziz, Moundir, Abderrahmane, Tangye, Stuart G., Picard, Capucine, Jeddane, Leïla, Al-Herz, Waleed, Rundles, Charlotte C., Franco, Jose Luis, Holland, Steven M., Klein, Christoph, Morio, Tomohiro, Oksenhendler, Eric, Puel, Anne, Puck, Jennifer, Seppänen, Mikko R. J., Somech, Raz, Su, Helen C., Sullivan, Kathleen E., Torgerson, Troy R., Meyts, Isabelle

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Prodromes as predictors of hereditary angioedema attacks von Leibovich‐Nassi, Iris, Reshef, Avner, Somech, Raz, Golander, Hava

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Deficiency of caspase recruitment domain family, member 11 (CARD11), causes profound combined immunodeficiency in human subjects von Stepensky, Polina, MD, Keller, Baerbel, MSc, Buchta, Mary, Kienzler, Anne-Kathrin, MSc, Elpeleg, Orly, MD, Somech, Raz, MD, PhD, Cohen, Sivan, MSc, Shachar, Idit, PhD, Miosge, Lisa A., PhD, Schlesier, Michael, PhD, Fuchs, Ilka, MSc, Enders, Anselm, MD, Eibel, Hermann, PhD, Grimbacher, Bodo, MD, Warnatz, Klaus, MD

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Genotype and functional correlates of disease phenotype in deficiency of adenosine deaminase 2 (DADA2) von Lee, Pui Y., Kellner, Erinn S., Huang, Yuelong, Furutani, Elissa, Huang, Zhengping, Bainter, Wayne, Alosaimi, Mohammed F., Stafstrom, Kelsey, Platt, Craig D., Stauber, Tali, Raz, Somech, Tirosh, Irit, Weiss, Aaron, Jordan, Michael B., Krupski, Christa, Eleftheriou, Despina, Brogan, Paul, Sobh, Ali, Baz, Zeina, Lefranc, Gerard, Irani, Carla, Kilic, Sara S., El-Owaidy, Rasha, Lokeshwar, M.R., Pimpale, Pallavi, Khubchandani, Raju, Chambers, Eugene P., Chou, Janet, Geha, Raif S., Nigrovic, Peter A., Zhou, Qing

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Minor Clinical Impact of COVID-19 Pandemic on Patients With Primary Immunodeficiency in Israel von Marcus, Nufar, Frizinsky, Shirly, Hagin, David, Ovadia, Adi, Hanna, Suhair, Farkash, Michael, Maoz-Segal, Ramit, Agmon-Levin, Nancy, Broides, Arnon, Nahum, Amit, Rosenberg, Elli, Kuperman, Amir Asher, Dinur-Schejter, Yael, Berkun, Yackov, Toker, Ori, Goldberg, Shmuel, Confino-Cohen, Ronit, Scheuerman, Oded, Badarneh, Basel, Epstein-Rigbi, Na'ama, Etzioni, Amos, Dalal, Ilan, Somech, Raz

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Treatment options for DOCK8 deficiency‐related severe dermatitis von Ollech, Ayelet, Mashiah, Jacob, Lev, Atar, Simon, Amos J., Somech, Raz, Adam, Etai, Barzilai, Aviv, Hagin, David, Greenberger, Shoshana

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New Instrument for the Evaluation of Prodromes and Attacks of Hereditary Angioedema (HAE-EPA) von Leibovich-Nassi, Iris, Golander, Hava, Somech, Raz, Har-Even, Dov, Reshef, Avner

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Human FCHO1 deficiency reveals role for clathrin-mediated endocytosis in development and function of T cells von Łyszkiewicz, Marcin, Ziętara, Natalia, Frey, Laura, Pannicke, Ulrich, Stern, Marcel, Liu, Yanshan, Fan, Yanxin, Puchałka, Jacek, Hollizeck, Sebastian, Somekh, Ido, Rohlfs, Meino, Yilmaz, Tuğba, Ünal, Ekrem, Karakukcu, Musa, Patiroğlu, Türkan, Kellerer, Christina, Karasu, Ebru, Sykora, Karl-Walter, Lev, Atar, Simon, Amos, Somech, Raz, Roesler, Joachim, Hoenig, Manfred, Keppler, Oliver T., Schwarz, Klaus, Klein, Christoph

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Leucocyte adhesion deficiency—A multicentre national experience von Wolach, Baruch, Gavrieli, Ronit, Wolach, Ofir, Stauber, Tal, Abuzaitoun, Omar, Kuperman, Amir, Amir, Yaakov, Stepensky, Polina, Somech, Raz, Etzioni, Amos

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Disruption of Thrombocyte and T Lymphocyte Development by a Mutation in ARPC1B von Somech, Raz, Lev, Atar, Lee, Yu Nee, Simon, Amos J, Barel, Ortal, Schiby, Ginette, Avivi, Camila, Barshack, Iris, Rhodes, Michele, Yin, Jiejing, Wang, Minshi, Yang, Yibin, Rhodes, Jennifer, Marcus, Nufar, Garty, Ben-Zion, Stein, Jerry, Amariglio, Ninette, Rechavi, Gideon, Wiest, David L, Zhang, Yong

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Perspective - Was it All for Nothing? von Somech, Raz

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Pediatric literature trends: high-level analysis using text-mining von Levy-Mendelovich, Sarina, Barbash, Yiftach, Budnik, Ivan, Levy-Erez, Daniella, Somech, Raz, Soffer, Shelly, Furth, Susan, Klang, Eyal

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Correction: Pediatric literature trends: high-level analysis using text-mining von Levy-Mendelovich, Sarina, Barbash, Yiftach, Budnik, Ivan, Levy-Erez, Daniella, Somech, Raz, Soffer, Shelly, Furth, Susan, Klang, Eyal

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CRISPR-Cas9 engineering of the RAG2 locus via complete coding sequence replacement for therapeutic applications von Allen, Daniel, Knop, Orli, Itkowitz, Bryan, Kalter, Nechama, Rosenberg, Michael, Iancu, Ortal, Beider, Katia, Lee, Yu Nee, Nagler, Arnon, Somech, Raz, Hendel, Ayal

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Mammalian VPS45 orchestrates trafficking through the endosomal system von Frey, Laura, Ziętara, Natalia, Łyszkiewicz, Marcin, Marquardt, Benjamin, Mizoguchi, Yoko, Linder, Monika I., Liu, Yanshan, Giesert, Florian, Wurst, Wolfgang, Dahlhoff, Maik, Schneider, Marlon R., Wolf, Eckhard, Somech, Raz, Klein, Christoph

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Kidney and urinary tract findings among patients with Kabuki (make-up) syndrome von Merdler-Rabinowicz, Rona, Pode-Shakked, Ben, Vivante, Asaf, Lahav, Einat, Kagan, Maayan, Chorin, Odelia, Somech, Raz, Raas-Rothschild, Annick

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Novel MALT1 Mutation Linked to Immunodeficiency, Immune Dysregulation, and an Abnormal T Cell Receptor Repertoire von Frizinsky, Shirly, Rechavi, Erez, Barel, Ortal, Najeeb, Rose H., Greenberger, Shoshana, Lee, Yu Nee, Simon, Amos J., Lev, Atar, Ma, Chi A., Sun, Guangping, Blackstone, Sarah A., Milner, Joshua D., Somech, Raz, Stauber, Tali

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