Biglycan Is Required for Adaptive Remodeling After Myocardial Infarction von WESTERMANN, D, MERSMANN, J, BRAND-HERRMANN, S.-M, YOUNG, M. F, SCHULTHEISS, H. P, LEVKAU, B, BABA, H. A, UNGER, T, ZACHAROWSKI, K, TSCHÖPE, C, FISCHER, J. W, MELCHIOR, A, FREUDENBERGER, T, PETRIK, C, SCHAEFER, L, LÜLLMANN-RAUCH, R, LETTAU, O, JACOBY, C, SCHRADER, J

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Overlapping functions of lysosomal acid phosphatase (LAP) and tartrate-resistant acid phosphatase (Acp5) revealed by doubly deficient mice von Suter, A, Everts, V, Boyde, A, Jones, S J, Lüllmann-Rauch, R, Hartmann, D, Hayman, A R, Cox, T M, Evans, M J, Meister, T, von Figura, K, Saftig, P

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Bone marrow stem cell-based gene transfer in a mouse model for metachromatic leukodystrophy: effects on visceral and nervous system disease manifestations von MATZNER, U, HARTMANN, D, LÜLLMANN-RAUCH, R, COENEN, R, ROTHERT, F, MANSSON, J.-E, FREDMAN, P, D'HOOGE, R, DE DEYN, P. P, GIESELMANN, V

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Metachromatic leukodystrophy: Molecular genetics and an animal model von Gieselmann, V., Matzner, U., Hess, B., Lüllmann‐Rauch, R., Coenen, R., Hartmann, D., D'Hooge, R., Dedeyn, P., Nagels, G.

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Lysosomal sulfoglycolipid storage in the kidneys of mice deficient for arylsulfatase A (ASA) and of double-knockout mice deficient for ASA and galactosylceramide synthase von Lüllmann-Rauch, R, Matzner, U, Franken, S, Hartmann, D, Gieselmann, V

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Metachromatic leukodystrophy: consequences of sulphatide accumulation von Gieselmann, V, Franken, S, Klein, D, Mansson, JE, Sandhoff, R, Rauch, R Lüllmann, Hartmann, D, Saravanan, VPM, De Deyn, PP, D'Hooge, R, Van Der Linden, AM, Schaeren-Wiemers, N

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Bone marrow stem cell gene therapy of arylsulfatase a-deficient mice, using an arylsulfatase A mutant that is hypersecreted from retrovirally transduced donor-type cells von MATZNER, Ulrich, SCHESTAG, Frank, HARTMANN, Dieter, LÜLLMANN-RAUCH, Renate, D'HOOGE, Rudi, DE DEYN, Peter P, GIESELMANN, Volkmar

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Lysosomal sulfatide storage in the brain of arylsulfatase A-deficient mice: cellular alterations and topographic distribution von Wittke, D, Hartmann, D, Gieselmann, V, Lüllmann-Rauch, R

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Accumulation of autophagic vacuoles and cardiomyopathy in LAMP-2-deficient mice von Saftig, Paul, Tanaka, Yoshitaka, Guhde, Gundula, Suter, Anke, Eskelinen, Eeva-Liisa, Hartmann, Dieter, Lüllmann-Rauch, Renate, Janssen, Paul M. L, Blanz, Judith, von Figura, Kurt

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Modest phenotypic improvements in ASA-deficient mice with only one UDP-galactose:ceramide-galactosyltransferase gene von Franken, S, Wittke, D, Mansson, J E, D'Hooge, R, De Deyn, P P, Lüllmann-Rauch, R, Matzner, U, Gieselmann, V

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Targeted Disruption of the Lysosomal α-Mannosidase Gene Results in Mice Resembling a Mild form of Human α-Mannosidosis von Stinchi, Sofia, Lüllmann-Rauch, Renate, Hartmann, Dieter, Coenen, Ruth, Beccari, Tommaso, Orlacchio, Aldo, von Figura, Kurt, Saftig, Paul

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Response to Letter Regarding Article, “Biglycan Is Required for Adaptive Remodeling After Myocardial Infarction” von Westermann, D., Lettau, O., Schultheiss, H.P., Tschöpe, C., Mersmann, J., Melchior, A., Freudenberger, T., Fischer, J.W., Petrik, C., Unger, T., Schaefer, L., Lüllmann-Rauch, R., Jacoby, C., Schrader, J., Brand-Herrman, S.M., Young, M.F., Levkau, B., Baba, H.A., Zacharowski, K.

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Normal Lysosomal Morphology and Function in LAMP-1-deficient Mice von Andrejewski, N, Punnonen, E L, Guhde, G, Tanaka, Y, Lüllmann-Rauch, R, Hartmann, D, von Figura, K, Saftig, P

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Disease model: LAMP-2 enlightens Danon disease von Saftig, Paul, von Figura, Kurt, Tanaka, Yshitaka, Lüllmann-Rauch, Renate

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Morphological alterations in the inner ear of the arylsulfatase A-deficient mouse von COENEN, R, GIESELMANN, V, LÜLLMANN-RAUCH, R

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Sulfatide storage in visceral organs of arylsulfatase A-deficient mice von SCHOTT, I, HARTMANN, D, GIESELMANN, V, LÜLLMANN-RAUCH, R

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LIMP-2/LGP85 deficiency causes ureteric pelvic junction obstruction, deafness and peripheral neuropathy in mice von Gamp, Alexander-Christian, Tanaka, Yoshitaka, Lüllmann-Rauch, Renate, Wittke, Dorothee, D'Hooge, Rudi, De Deyn, Peter P., Moser, Tobias, Maier, Hannes, Hartmann, Dieter, Reiss, Karina, Illert, Anna-Lena, von Figura, Kurt, Saftig, Paul

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Phenotype of Arylsulfatase A-Deficient Mice: Relationship to Human Metachromatic Leukodystrophy von Hess, Barbara, Saftig, Paul, Hartmann, Dieter, Coenen, Ruth, Lullmann-Rauch, Renate, Goebel, Hans H., Evers, Meike, Von Figura, Kurt, D'Hooge, Rudi, Nagels, Guy, De Deyn, Peter, Peters, Christoph, Gieselmann, Volkmar

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Disturbed cholesterol traffic but normal proteolytic function in LAMP-1/LAMP-2 double-deficient fibroblasts von Eskelinen, Eeva-Liisa, Schmidt, Christine Katrin, Neu, Silja, Willenborg, Marion, Fuertes, Graciela, Salvador, Natalia, Tanaka, Yoshitaka, Lüllmann-Rauch, Renate, Hartmann, Dieter, Heeren, Jörg, von Figura, Kurt, Knecht, Erwin, Saftig, Paul

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Enzyme replacement improves nervous system pathology and function in a mouse model for metachromatic leukodystrophy von Matzner, Ulrich, Herbst, Eva, Hedayati, Kerstin Khalaj, Lüllmann-Rauch, Renate, Wessig, Carsten, Schröder, Stephan, Eistrup, Carl, Möller, Christer, Fogh, Jens, Gieselmann, Volkmar

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